Table 1. Relative Proportions and Features of Pleuropulmonary Blastomaa

Type I Type IrType IIType II/III or III
Relative proportion of pleuropulmonary blastoma cases 33% 35% 32%
Presence of germline DICER1 variant75%83%63%75%
Median age at diagnosis (months)73135 41
5-year overall survival rate98% 100%71% 53%

aAdapted from Messinger et al.[2] and Nelson et al.[3]

From: Childhood Pleuropulmonary Blastoma Treatment (PDQ®)

Cover of PDQ Cancer Information Summaries
PDQ Cancer Information Summaries [Internet].
Bethesda (MD): National Cancer Institute (US); 2002-.

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