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Neonatal hearing loss

MedGen UID:
105487
Concept ID:
C0521786
Disease or Syndrome
Synonym: Neonatal Hearing Loss
SNOMED CT: Neonatal hearing loss (95821001)

Definition

Partial or complete loss of the ability to detect or understand sounds present in an infant within its first month after birth. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVNeonatal hearing loss

Professional guidelines

PubMed

Ferlito S, Maniaci A, Cocuzza S, La Mantia I, Di Mauro P, Poli G, Maiolino L, Coco S, Merlino F, Maltese M, Ragliani M, Russo M, Gulino A, Azieli C, Martines F, Galletti F, Bubbico L
Acta Otorhinolaryngol Ital 2021 Aug;41(4):356-363. doi: 10.14639/0392-100X-N1162. PMID: 34533539Free PMC Article
Pesch MH, Saunders NA, Abdelnabi S
J Midwifery Womens Health 2021 May;66(3):397-402. Epub 2021 May 24 doi: 10.1111/jmwh.13228. PMID: 34031974
Ezzeldin ZM, Sharaf E, Hamdy HS, Abdelwahab Selim YA
Int J Pediatr Otorhinolaryngol 2021 Mar;142:110591. Epub 2020 Dec 23 doi: 10.1016/j.ijporl.2020.110591. PMID: 33360868

Recent clinical studies

Etiology

Mostafa BE, Mostafa A, Fiky LME, Omara A, Teaima A
Eur Arch Otorhinolaryngol 2022 Jul;279(7):3435-3438. Epub 2021 Oct 2 doi: 10.1007/s00405-021-07098-5. PMID: 34599653Free PMC Article
Pesch MH, Saunders NA, Abdelnabi S
J Midwifery Womens Health 2021 May;66(3):397-402. Epub 2021 May 24 doi: 10.1111/jmwh.13228. PMID: 34031974
Gupta S, Wang M, Hong B, Curhan SG, Curhan GC
Ear Hear 2020 Sep/Oct;41(5):1208-1214. doi: 10.1097/AUD.0000000000000838. PMID: 31996588Free PMC Article
Corujo-Santana C, Falcón-González JC, Borkoski-Barreiro SA, Pérez-Plasencia D, Ramos-Macías Á
Acta Otorrinolaringol Esp 2015 Nov-Dec;66(6):326-31. Epub 2015 Jan 29 doi: 10.1016/j.otorri.2014.10.001. PMID: 25638013
Borg E
Scand Audiol 1997;26(2):77-91. doi: 10.3109/01050399709074979. PMID: 9187000

Diagnosis

Mostafa BE, Mostafa A, Fiky LME, Omara A, Teaima A
Eur Arch Otorhinolaryngol 2022 Jul;279(7):3435-3438. Epub 2021 Oct 2 doi: 10.1007/s00405-021-07098-5. PMID: 34599653Free PMC Article
Pesch MH, Saunders NA, Abdelnabi S
J Midwifery Womens Health 2021 May;66(3):397-402. Epub 2021 May 24 doi: 10.1111/jmwh.13228. PMID: 34031974
Ezzeldin ZM, Sharaf E, Hamdy HS, Abdelwahab Selim YA
Int J Pediatr Otorhinolaryngol 2021 Mar;142:110591. Epub 2020 Dec 23 doi: 10.1016/j.ijporl.2020.110591. PMID: 33360868
Corujo-Santana C, Falcón-González JC, Borkoski-Barreiro SA, Pérez-Plasencia D, Ramos-Macías Á
Acta Otorrinolaringol Esp 2015 Nov-Dec;66(6):326-31. Epub 2015 Jan 29 doi: 10.1016/j.otorri.2014.10.001. PMID: 25638013
Borg E
Scand Audiol 1997;26(2):77-91. doi: 10.3109/01050399709074979. PMID: 9187000

Therapy

Overcash RT, Marc-Aurele KL, Hull AD, Ramos GA
Pediatrics 2016 Apr;137(4) Epub 2016 Mar 22 doi: 10.1542/peds.2015-3722. PMID: 27006474
Yoshikawa S, Ikeda K, Kudo T, Kobayashi T
Auris Nasus Larynx 2004 Dec;31(4):361-8. doi: 10.1016/j.anl.2004.07.007. PMID: 15571908
Kountakis SE, Skoulas I, Phillips D, Chang CY
Am J Otolaryngol 2002 May-Jun;23(3):133-7. doi: 10.1053/ajot.2002.123453. PMID: 12019480
Dort JC, Tobolski C, Brown D
J Otolaryngol 2000 Aug;29(4):206-10. PMID: 11003070

Prognosis

van Dommelen P, Verkerk PH, de Graaff-Korf K, van Straaten HLM
Early Hum Dev 2023 Dec;187:105899. Epub 2023 Nov 6 doi: 10.1016/j.earlhumdev.2023.105899. PMID: 37948978
Ferlito S, Maniaci A, Cocuzza S, La Mantia I, Di Mauro P, Poli G, Maiolino L, Coco S, Merlino F, Maltese M, Ragliani M, Russo M, Gulino A, Azieli C, Martines F, Galletti F, Bubbico L
Acta Otorhinolaryngol Ital 2021 Aug;41(4):356-363. doi: 10.14639/0392-100X-N1162. PMID: 34533539Free PMC Article
van Dommelen P, Verkerk PH, van Straaten HL; Dutch Neonatal Intensive Care Unit Neonatal Hearing Screening Working Group
J Pediatr 2015 Apr;166(4):840-3.e1. Epub 2015 Feb 4 doi: 10.1016/j.jpeds.2014.12.041. PMID: 25661409
Mehra S, Eavey RD, Keamy DG Jr
Otolaryngol Head Neck Surg 2009 Apr;140(4):461-72. doi: 10.1016/j.otohns.2008.12.022. PMID: 19328331
Borg E
Scand Audiol 1997;26(2):77-91. doi: 10.3109/01050399709074979. PMID: 9187000

Clinical prediction guides

Doncarli A, Tillaut H, Akkari M, Baladi B, Creutz-Leroy M, Parodi M, Beltzer N, Goulet V, Regnault N
Acta Paediatr 2022 Oct;111(10):1907-1913. Epub 2022 Jun 21 doi: 10.1111/apa.16438. PMID: 35642710
Yu Y, Shi K, Nielson C, Graham EM, Price MS, Haller TJ, Carraro M, Firpo MA, Park AH, Harrison RV
Hear Res 2022 Apr;417:108454. Epub 2022 Jan 31 doi: 10.1016/j.heares.2022.108454. PMID: 35131579
Ferlito S, Maniaci A, Cocuzza S, La Mantia I, Di Mauro P, Poli G, Maiolino L, Coco S, Merlino F, Maltese M, Ragliani M, Russo M, Gulino A, Azieli C, Martines F, Galletti F, Bubbico L
Acta Otorhinolaryngol Ital 2021 Aug;41(4):356-363. doi: 10.14639/0392-100X-N1162. PMID: 34533539Free PMC Article
Anastasio ART, Yamamoto AY, Massuda ET, Manfredi AKS, Cavalcante JMS, Lopes BCP, Aragon DC, Boppana S, Fowler KB, Britt WJ, Mussi-Pinhata MM
J Perinatol 2021 Feb;41(2):315-323. Epub 2020 Sep 3 doi: 10.1038/s41372-020-00807-8. PMID: 32884104
Borg E
Scand Audiol 1997;26(2):77-91. doi: 10.3109/01050399709074979. PMID: 9187000

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