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Pediatric fibrosarcoma

MedGen UID:
124685
•Concept ID:
C0279981
•
Neoplastic Process
Synonyms: Childhood Fibrosarcoma; childhood fibrosarcoma; Pediatric Fibrosarcoma; pediatric fibrosarcoma
 
Monarch Initiative: MONDO:0002678

Definition

A malignant neoplasm arising from the deep soft tissues in children. It is characterized by the presence of spindle-shaped fibroblasts and collagenous stroma formation in a herringbone growth pattern. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPediatric fibrosarcoma

Professional guidelines

PubMed

DICER1-associated Tumors in the Female Genital Tract: Molecular Basis, Clinicopathologic Features, and Differential Diagnosis.
Han LM, Weiel JJ, Longacre TA, Folkins AK
Adv Anat Pathol 2022 Sep 1;29(5):297-308. Epub 2022 Jul 1 doi: 10.1097/PAP.0000000000000351. PMID: 35778792
Advances in the Diagnosis and Management of Neonatal Sarcomas.
Rashid T, Noyd DH, Iranzad N, Davis JT, Deel MD
Clin Perinatol 2021 Mar;48(1):117-145. doi: 10.1016/j.clp.2020.11.007. PMID: 33583500
The Evolving Diagnostic and Treatment Landscape of NTRK-Fusion-Driven Pediatric Cancers.
Shulman DS, DuBois SG
Paediatr Drugs 2020 Apr;22(2):189-197. doi: 10.1007/s40272-020-00380-9. PMID: 31965543

Recent clinical studies

Diagnosis

Radical Resection of Pediatric Fibrosarcoma Is Not Associated With Survival Benefit: A Nationwide Database Analysis.
Huerta CT, Quinn K, Saberi RA, Rao KA, Quiroz HJ, Brady AC, Thorson CM, Sola JE, Perez EA
J Surg Res 2022 Nov;279:639-647. Epub 2022 Aug 2 doi: 10.1016/j.jss.2022.06.030. PMID: 35930817

Prognosis

Radical Resection of Pediatric Fibrosarcoma Is Not Associated With Survival Benefit: A Nationwide Database Analysis.
Huerta CT, Quinn K, Saberi RA, Rao KA, Quiroz HJ, Brady AC, Thorson CM, Sola JE, Perez EA
J Surg Res 2022 Nov;279:639-647. Epub 2022 Aug 2 doi: 10.1016/j.jss.2022.06.030. PMID: 35930817

Clinical prediction guides

Radical Resection of Pediatric Fibrosarcoma Is Not Associated With Survival Benefit: A Nationwide Database Analysis.
Huerta CT, Quinn K, Saberi RA, Rao KA, Quiroz HJ, Brady AC, Thorson CM, Sola JE, Perez EA
J Surg Res 2022 Nov;279:639-647. Epub 2022 Aug 2 doi: 10.1016/j.jss.2022.06.030. PMID: 35930817

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

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    Consumer resources

    Reviews

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    • PMC Articles
      Related information in PubMed Central Links
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