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Abnormal pulmonary artery morphology

MedGen UID:
1379288
•Concept ID:
C4476881
•
Anatomical Abnormality
HPO: HP:0030966

Definition

An abnormality of the structure of the pulmonary artery. [from HPO]

Professional guidelines

PubMed

Diagnosis and Management of Persistent Pulmonary Arterio-venous Malformations following Embolotherapy.
Kulkarni CB, Sutphin P, Iqbal S, Kalva SP
Acad Radiol 2023 Mar;30(3):441-452. Epub 2022 Sep 9 doi: 10.1016/j.acra.2022.08.012. PMID: 36089478
Diagnosis and endovascular management of pulmonary arteriovenous malformations.
Kramdhari H, Valakkada J, Ayyappan A
Br J Radiol 2021 Jul 1;94(1123):20200695. Epub 2021 May 26 doi: 10.1259/bjr.20200695. PMID: 34038182Free PMC Article
Calcium-sensing receptor in the development and treatment of pulmonary hypertension.
Zhou MY, Cheng L, Chen L, Gu YJ, Wang Y
Mol Biol Rep 2021 Jan;48(1):975-981. Epub 2021 Jan 4 doi: 10.1007/s11033-020-06065-3. PMID: 33394231

Recent clinical studies

Etiology

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
Staged unifocalization revisited.
Nakamura Y, Burkhart HM
J Card Surg 2022 Apr;37(4):967-968. Epub 2022 Feb 9 doi: 10.1111/jocs.16296. PMID: 35137983
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757

Diagnosis

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
Pulmonary Arteriovenous Malformation and Its Vascular Mimickers.
Lee HN, Hyun D
Korean J Radiol 2022 Feb;23(2):202-217. Epub 2022 Jan 4 doi: 10.3348/kjr.2021.0417. PMID: 35029077Free PMC Article
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757
Rings and slings revisited.
Smith BM, Lu JC, Dorfman AL, Mahani MG, Agarwal PP
Magn Reson Imaging Clin N Am 2015 Feb;23(1):127-35. Epub 2014 Oct 3 doi: 10.1016/j.mric.2014.09.011. PMID: 25476681

Therapy

The Secrets of the Frogs Heart.
Corno AF, Zhou Z, Uppu SC, Huang S, Marino B, Milewicz DM, Salazar JD
Pediatr Cardiol 2022 Oct;43(7):1471-1480. Epub 2022 Mar 15 doi: 10.1007/s00246-022-02870-8. PMID: 35290490
Transthoracic Pulmonary Artery Denervation for Pulmonary Arterial Hypertension.
Huang Y, Liu YW, Pan HZ, Zhang XL, Li J, Xiang L, Meng J, Wang PH, Yang J, Jing ZC, Zhang H
Arterioscler Thromb Vasc Biol 2019 Apr;39(4):704-718. doi: 10.1161/ATVBAHA.118.311992. PMID: 30816802
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560

Prognosis

Congenital central pulmonary artery anomalies: Part 2.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1030-1040. Epub 2020 Jun 4 doi: 10.1007/s00247-020-04703-3. PMID: 32500159
Congenital central pulmonary artery anomalies: Part 1.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1022-1029. Epub 2020 May 30 doi: 10.1007/s00247-020-04690-5. PMID: 32474775
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Coronary artery fistulae.
Luo L, Kebede S, Wu S, Stouffer GA
Am J Med Sci 2006 Aug;332(2):79-84. doi: 10.1097/00000441-200608000-00005. PMID: 16909054

Clinical prediction guides

State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Right heart and pulmonary vessels structure and function.
D'Alto M, Scognamiglio G, Dimopoulos K, Bossone E, Vizza D, Romeo E, Vonk-Noordergraaf A, Gaine S, Peacock A, Naeije R
Echocardiography 2015 Jan;32 Suppl 1:S3-10. Epub 2014 Sep 19 doi: 10.1111/echo.12227. PMID: 25244348
Pathophysiology and clinical implications of pulmonary arterial enlargement in COPD.
Wells JM, Dransfield MT
Int J Chron Obstruct Pulmon Dis 2013;8:509-21. Epub 2013 Oct 29 doi: 10.2147/COPD.S52204. PMID: 24235822Free PMC Article
Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment.
Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G
Arch Cardiovasc Dis 2013 Aug-Sep;106(8-9):448-54. Epub 2013 Aug 9 doi: 10.1016/j.acvd.2013.05.004. PMID: 23938302

Recent systematic reviews

Partial Anomalous Left Pulmonary Artery Anterior Versus Posterior Types: A Systematic Review.
Restrepo CS, Gonzalez TV, Baxi AJ, Saboo SS
Tomography 2022 Jul 27;8(4):1947-1958. doi: 10.3390/tomography8040163. PMID: 36006061Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Paediatric haemoptysis and the otorhinolaryngologist: Systematic review.
Bannister M
Int J Pediatr Otorhinolaryngol 2017 Jan;92:99-102. Epub 2016 Oct 24 doi: 10.1016/j.ijporl.2016.10.021. PMID: 28012543
Coronary-Pulmonary Artery Fistulas: A Systematic Review.
Verdini D, Vargas D, Kuo A, Ghoshhajra B, Kim P, Murillo H, Kirsch J, Lane M, Restrepo C
J Thorac Imaging 2016 Nov;31(6):380-390. doi: 10.1097/RTI.0000000000000232. PMID: 27768631

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