U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Abnormal pulmonary artery morphology

MedGen UID:
1379288
•Concept ID:
C4476881
•
Anatomical Abnormality
HPO: HP:0030966

Definition

An abnormality of the structure of the pulmonary artery. [from HPO]

Professional guidelines

PubMed

Diagnosis and endovascular management of pulmonary arteriovenous malformations.
Kramdhari H, Valakkada J, Ayyappan A
Br J Radiol 2021 Jul 1;94(1123):20200695. Epub 2021 May 26 doi: 10.1259/bjr.20200695. PMID: 34038182Free PMC Article
Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment.
Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G
Arch Cardiovasc Dis 2013 Aug-Sep;106(8-9):448-54. Epub 2013 Aug 9 doi: 10.1016/j.acvd.2013.05.004. PMID: 23938302
Primary pulmonary hypertension.
Gaine SP, Rubin LJ
Lancet 1998 Aug 29;352(9129):719-25. doi: 10.1016/S0140-6736(98)02111-4. PMID: 9729004

Recent clinical studies

Etiology

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
Staged unifocalization revisited.
Nakamura Y, Burkhart HM
J Card Surg 2022 Apr;37(4):967-968. Epub 2022 Feb 9 doi: 10.1111/jocs.16296. PMID: 35137983
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757

Diagnosis

Pulmonary artery sling: An overview.
K Rahmath MR, Durward A
Pediatr Pulmonol 2023 May;58(5):1299-1309. Epub 2023 Feb 24 doi: 10.1002/ppul.26345. PMID: 36790334
Pulmonary Arteriovenous Malformation and Its Vascular Mimickers.
Lee HN, Hyun D
Korean J Radiol 2022 Feb;23(2):202-217. Epub 2022 Jan 4 doi: 10.3348/kjr.2021.0417. PMID: 35029077Free PMC Article
Discontinuous Pulmonary Artery.
Eltayeb O, Mongé MC, Popescu AR, Sarwark AE, Harris T, Backer CL
World J Pediatr Congenit Heart Surg 2017 Jan;8(1):106-110. Epub 2016 Jun 22 doi: 10.1177/2150135115618871. PMID: 26993757
Coronary-Pulmonary Artery Fistulas: A Systematic Review.
Verdini D, Vargas D, Kuo A, Ghoshhajra B, Kim P, Murillo H, Kirsch J, Lane M, Restrepo C
J Thorac Imaging 2016 Nov;31(6):380-390. doi: 10.1097/RTI.0000000000000232. PMID: 27768631
Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment.
Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G
Arch Cardiovasc Dis 2013 Aug-Sep;106(8-9):448-54. Epub 2013 Aug 9 doi: 10.1016/j.acvd.2013.05.004. PMID: 23938302

Therapy

The Secrets of the Frogs Heart.
Corno AF, Zhou Z, Uppu SC, Huang S, Marino B, Milewicz DM, Salazar JD
Pediatr Cardiol 2022 Oct;43(7):1471-1480. Epub 2022 Mar 15 doi: 10.1007/s00246-022-02870-8. PMID: 35290490
Transthoracic Pulmonary Artery Denervation for Pulmonary Arterial Hypertension.
Huang Y, Liu YW, Pan HZ, Zhang XL, Li J, Xiang L, Meng J, Wang PH, Yang J, Jing ZC, Zhang H
Arterioscler Thromb Vasc Biol 2019 Apr;39(4):704-718. doi: 10.1161/ATVBAHA.118.311992. PMID: 30816802
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560

Prognosis

Congenital central pulmonary artery anomalies: Part 2.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1030-1040. Epub 2020 Jun 4 doi: 10.1007/s00247-020-04703-3. PMID: 32500159
Congenital central pulmonary artery anomalies: Part 1.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1022-1029. Epub 2020 May 30 doi: 10.1007/s00247-020-04690-5. PMID: 32474775
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment.
Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G
Arch Cardiovasc Dis 2013 Aug-Sep;106(8-9):448-54. Epub 2013 Aug 9 doi: 10.1016/j.acvd.2013.05.004. PMID: 23938302
Coronary artery fistulae.
Luo L, Kebede S, Wu S, Stouffer GA
Am J Med Sci 2006 Aug;332(2):79-84. doi: 10.1097/00000441-200608000-00005. PMID: 16909054

Clinical prediction guides

State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560
Pathophysiology and clinical implications of pulmonary arterial enlargement in COPD.
Wells JM, Dransfield MT
Int J Chron Obstruct Pulmon Dis 2013;8:509-21. Epub 2013 Oct 29 doi: 10.2147/COPD.S52204. PMID: 24235822Free PMC Article
Unilateral absence of pulmonary artery: pathophysiology, symptoms, diagnosis and current treatment.
Kruzliak P, Syamasundar RP, Novak M, Pechanova O, Kovacova G
Arch Cardiovasc Dis 2013 Aug-Sep;106(8-9):448-54. Epub 2013 Aug 9 doi: 10.1016/j.acvd.2013.05.004. PMID: 23938302

Recent systematic reviews

Partial Anomalous Left Pulmonary Artery Anterior Versus Posterior Types: A Systematic Review.
Restrepo CS, Gonzalez TV, Baxi AJ, Saboo SS
Tomography 2022 Jul 27;8(4):1947-1958. doi: 10.3390/tomography8040163. PMID: 36006061Free PMC Article
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2018 Jan 4;1(1):CD008017. doi: 10.1002/14651858.CD008017.pub5. PMID: 29298459Free PMC Article
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Coronary-Pulmonary Artery Fistulas: A Systematic Review.
Verdini D, Vargas D, Kuo A, Ghoshhajra B, Kim P, Murillo H, Kirsch J, Lane M, Restrepo C
J Thorac Imaging 2016 Nov;31(6):380-390. doi: 10.1097/RTI.0000000000000232. PMID: 27768631
Embolisation for pulmonary arteriovenous malformation.
Hsu CC, Kwan GN, Thompson SA, Evans-Barns H, van Driel ML
Cochrane Database Syst Rev 2015 Jan 29;1:CD008017. doi: 10.1002/14651858.CD008017.pub4. PMID: 25634560

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Consumer resources

    Reviews

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...