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Abnormal pulmonary artery physiology

MedGen UID:
1383991
•Concept ID:
C4476882
•
Finding
HPO: HP:0030967

Definition

An abnormality of the function of the pulmonary artery. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal pulmonary artery physiology

Professional guidelines

PubMed

Pulmonary arterial hypertension: pathogenesis and clinical management.
Thenappan T, Ormiston ML, Ryan JJ, Archer SL
BMJ 2018 Mar 14;360:j5492. doi: 10.1136/bmj.j5492. PMID: 29540357Free PMC Article
Epidemiology, pathogenesis, and management of takotsubo syndrome.
Y-Hassan S, Tornvall P
Clin Auton Res 2018 Feb;28(1):53-65. Epub 2017 Sep 15 doi: 10.1007/s10286-017-0465-z. PMID: 28917022Free PMC Article
Alagille syndrome: pathogenesis, diagnosis and management.
Turnpenny PD, Ellard S
Eur J Hum Genet 2012 Mar;20(3):251-7. Epub 2011 Sep 21 doi: 10.1038/ejhg.2011.181. PMID: 21934706Free PMC Article

Recent clinical studies

Etiology

Peripheral Pulmonary Artery Stenosis Is Not a Contraindication to a Single-ventricle Pathway.
Al-Khaldi A, Alsahari A, Alotay A, Momenah T, Alfonso JJ
Ann Thorac Surg 2022 May;113(5):1563-1568. Epub 2021 Apr 1 doi: 10.1016/j.athoracsur.2021.03.059. PMID: 33811885
Predictive Models for Pulmonary Artery Size in Fontan Patients.
Gupta A, Gillett C, Gerard P, Cheung MMH, Mynard JP, Kung E
J Cardiovasc Transl Res 2021 Aug;14(4):782-789. Epub 2020 Apr 4 doi: 10.1007/s12265-020-09993-4. PMID: 32248348
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954

Diagnosis

Congenital diaphragmatic hernia-associated pulmonary hypertension.
Gupta VS, Harting MT
Semin Perinatol 2020 Feb;44(1):151167. Epub 2019 Jul 30 doi: 10.1053/j.semperi.2019.07.006. PMID: 31519366
Cross-sectional imaging of congenital pulmonary artery anomalies.
Zucker EJ
Int J Cardiovasc Imaging 2019 Aug;35(8):1535-1548. Epub 2019 Jun 7 doi: 10.1007/s10554-019-01643-4. PMID: 31175525
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954
Pulmonary arteriovenous malformation.
Khurshid I, Downie GH
Postgrad Med J 2002 Apr;78(918):191-7. doi: 10.1136/pmj.78.918.191. PMID: 11930021Free PMC Article

Therapy

Predictive Models for Pulmonary Artery Size in Fontan Patients.
Gupta A, Gillett C, Gerard P, Cheung MMH, Mynard JP, Kung E
J Cardiovasc Transl Res 2021 Aug;14(4):782-789. Epub 2020 Apr 4 doi: 10.1007/s12265-020-09993-4. PMID: 32248348
Pulmonary arteriovenous malformations.
Tellapuri S, Park HS, Kalva SP
Int J Cardiovasc Imaging 2019 Aug;35(8):1421-1428. Epub 2018 Nov 1 doi: 10.1007/s10554-018-1479-x. PMID: 30386957
Transcatheter Pulmonary Valve Replacement: Current State of Art.
Alkashkari W, Alsubei A, Hijazi ZM
Curr Cardiol Rep 2018 Mar 15;20(4):27. doi: 10.1007/s11886-018-0966-y. PMID: 29546472
Pulmonary Artery Abnormalities in Ex-smokers with and without Airflow Obstruction.
Lindenmaier TJ, Kirby M, Paulin G, Mielniczuk L, Cunningham IA, Mura M, Licskai C, Parraga G
COPD 2016;13(2):224-34. Epub 2015 Nov 25 doi: 10.3109/15412555.2015.1074666. PMID: 26606693
Transcatheter Fontan takedown.
Hallbergson A, Mascio CE, Rome JJ
Catheter Cardiovasc Interv 2015 Nov;86(5):849-54. Epub 2015 May 6 doi: 10.1002/ccd.25963. PMID: 25945427

Prognosis

Congenital central pulmonary artery anomalies: Part 2.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1030-1040. Epub 2020 Jun 4 doi: 10.1007/s00247-020-04703-3. PMID: 32500159
Congenital central pulmonary artery anomalies: Part 1.
Newman B, Alkhori N
Pediatr Radiol 2020 Jul;50(8):1022-1029. Epub 2020 May 30 doi: 10.1007/s00247-020-04690-5. PMID: 32474775
Cross-sectional imaging of congenital pulmonary artery anomalies.
Zucker EJ
Int J Cardiovasc Imaging 2019 Aug;35(8):1535-1548. Epub 2019 Jun 7 doi: 10.1007/s10554-019-01643-4. PMID: 31175525
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
Pulmonary arteriovenous malformations.
Cartin-Ceba R, Swanson KL, Krowka MJ
Chest 2013 Sep;144(3):1033-1044. doi: 10.1378/chest.12-0924. PMID: 24008954

Clinical prediction guides

Cross-sectional imaging of congenital pulmonary artery anomalies.
Zucker EJ
Int J Cardiovasc Imaging 2019 Aug;35(8):1535-1548. Epub 2019 Jun 7 doi: 10.1007/s10554-019-01643-4. PMID: 31175525
Update on MR imaging of the pulmonary vasculature.
Aziz M, Krishnam M, Madhuranthakam AJ, Rajiah P
Int J Cardiovasc Imaging 2019 Aug;35(8):1483-1497. Epub 2019 Apr 27 doi: 10.1007/s10554-019-01603-y. PMID: 31030315
State-of-the-art pulmonary arterial imaging - Part 2.
Goerne H, Chaturvedi A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):361-375. Epub 2018 May 28 doi: 10.1024/0301-1526/a000709. PMID: 29806799
State-of-the-art pulmonary arterial imaging - Part 1.
Tanabe Y, Landeras L, Ghandour A, Partovi S, Rajiah P
Vasa 2018 Aug;47(5):345-359. Epub 2018 May 28 doi: 10.1024/0301-1526/a000708. PMID: 29806797
Pathophysiology and clinical implications of pulmonary arterial enlargement in COPD.
Wells JM, Dransfield MT
Int J Chron Obstruct Pulmon Dis 2013;8:509-21. Epub 2013 Oct 29 doi: 10.2147/COPD.S52204. PMID: 24235822Free PMC Article

Recent systematic reviews

Absent pulmonary valve with tricuspid atresia/stenosis: literature review with new three long-term cases.
Kawasaki Y, Murakami Y, Fujino M, Sasaki T, Nakamura K, Yoshida Y, Suzuki T, Nishigaki K, Ehara E
Heart Vessels 2022 Jan;37(1):142-151. Epub 2021 Jun 5 doi: 10.1007/s00380-021-01887-y. PMID: 34089363
Serum albumin and cardiovascular disease: State-of-the-art review.
Arques S
Ann Cardiol Angeiol (Paris) 2020 Oct;69(4):192-200. Epub 2020 Aug 11 doi: 10.1016/j.ancard.2020.07.012. PMID: 32797938
State-of-the-Art Review: Echocardiography in Pulmonary Hypertension.
Cordina RL, Playford D, Lang I, Celermajer DS
Heart Lung Circ 2019 Sep;28(9):1351-1364. Epub 2019 Apr 30 doi: 10.1016/j.hlc.2019.03.003. PMID: 31109891
Pulmonary hypertension secondary to congenital diaphragmatic hernia: factors and pathways involved in pulmonary vascular remodeling.
Montalva L, Antounians L, Zani A
Pediatr Res 2019 May;85(6):754-768. Epub 2019 Feb 19 doi: 10.1038/s41390-019-0345-4. PMID: 30780153
Limitations and strengths of doppler/echo pulmonary artery systolic pressure-right heart catheterization correlations: a systematic literature review.
Finkelhor RS, Lewis SA, Pillai D
Echocardiography 2015 Jan;32(1):10-8. Epub 2014 Mar 25 doi: 10.1111/echo.12594. PMID: 24661140

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