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Abnormality of the pulmonary vasculature

MedGen UID:
870814
•Concept ID:
C4025271
•
Anatomical Abnormality
Synonym: Abnormality of the lung blood vessels
 
HPO: HP:0004930

Professional guidelines

PubMed

Pathophysiology and Management of Persistent Pulmonary Hypertension of the Newborn.
Singh Y, Lakshminrusimha S
Clin Perinatol 2021 Aug;48(3):595-618. doi: 10.1016/j.clp.2021.05.009. PMID: 34353582Free PMC Article
Pulmonary arterial hypertension: pathogenesis and clinical management.
Thenappan T, Ormiston ML, Ryan JJ, Archer SL
BMJ 2018 Mar 14;360:j5492. doi: 10.1136/bmj.j5492. PMID: 29540357Free PMC Article
Epidemiology, pathogenesis, and management of takotsubo syndrome.
Y-Hassan S, Tornvall P
Clin Auton Res 2018 Feb;28(1):53-65. Epub 2017 Sep 15 doi: 10.1007/s10286-017-0465-z. PMID: 28917022Free PMC Article

Recent clinical studies

Etiology

Lung growth and pulmonary function after prematurity and bronchopulmonary dysplasia.
Moschino L, Bonadies L, Baraldi E
Pediatr Pulmonol 2021 Nov;56(11):3499-3508. Epub 2021 Mar 26 doi: 10.1002/ppul.25380. PMID: 33729686Free PMC Article
Oxygen and pulmonary vasodilation: The role of oxidative and nitrosative stress.
Steinhorn RH, Lakshminrusimha S
Semin Fetal Neonatal Med 2020 Apr;25(2):101083. Epub 2020 Jan 16 doi: 10.1016/j.siny.2020.101083. PMID: 31983672
The eye in CHD.
Nasir-Ahmad S, Cordina R, Liew G, McCluskey P, Celermajer D
Cardiol Young 2018 Aug;28(8):981-985. doi: 10.1017/S1047951118000859. PMID: 30043722
Fontan physiology revisited.
Jolley M, Colan SD, Rhodes J, DiNardo J
Anesth Analg 2015 Jul;121(1):172-182. doi: 10.1213/ANE.0000000000000717. PMID: 26086514
Congenital lung malformations.
Andrade CF, Ferreira HP, Fischer GB
J Bras Pneumol 2011 Mar-Apr;37(2):259-71. doi: 10.1590/s1806-37132011000200017. PMID: 21537663

Diagnosis

Intrapulmonary Lung Sequestration.
A Cunha S, Klepetko W
Port J Card Thorac Vasc Surg 2022 Oct 5;29(3):85. doi: 10.48729/pjctvs.282. PMID: 36197824
Congenital diaphragmatic hernia-associated pulmonary hypertension.
Gupta VS, Harting MT
Semin Perinatol 2020 Feb;44(1):151167. Epub 2019 Jul 30 doi: 10.1053/j.semperi.2019.07.006. PMID: 31519366
The multiple dimensions of Platypnea-Orthodeoxia syndrome: A review.
Agrawal A, Palkar A, Talwar A
Respir Med 2017 Aug;129:31-38. Epub 2017 May 31 doi: 10.1016/j.rmed.2017.05.016. PMID: 28732833
Hepatopulmonary syndrome.
Müller C, Schenk P
Wien Klin Wochenschr 1999 May 7;111(9):339-47. PMID: 10407994
Pulmonary edema.
Colice GL
Clin Geriatr Med 1986 May;2(2):411-32. PMID: 3516371

Therapy

Issues in Medicine.
Shaw JA, John TJ, Koegelenberg CFN, Da Silva M, Allwood BW, Weich H
S Afr Med J 2023 Feb 1;113(2):65-68. doi: 10.7196/SAMJ.2022.v113i2.16758. PMID: 36757074
The eye in CHD.
Nasir-Ahmad S, Cordina R, Liew G, McCluskey P, Celermajer D
Cardiol Young 2018 Aug;28(8):981-985. doi: 10.1017/S1047951118000859. PMID: 30043722
Fontan physiology revisited.
Jolley M, Colan SD, Rhodes J, DiNardo J
Anesth Analg 2015 Jul;121(1):172-182. doi: 10.1213/ANE.0000000000000717. PMID: 26086514
Update on PPHN: mechanisms and treatment.
Nair J, Lakshminrusimha S
Semin Perinatol 2014 Mar;38(2):78-91. doi: 10.1053/j.semperi.2013.11.004. PMID: 24580763Free PMC Article
Exercise limitation, exercise testing and exercise recommendations in sickle cell anemia.
Connes P, Machado R, Hue O, Reid H
Clin Hemorheol Microcirc 2011;49(1-4):151-63. doi: 10.3233/CH-2011-1465. PMID: 22214686

Prognosis

Pulmonary Hypertension in Heart Failure: Pathophysiology, Pathobiology, and Emerging Clinical Perspectives.
Guazzi M, Naeije R
J Am Coll Cardiol 2017 Apr 4;69(13):1718-1734. doi: 10.1016/j.jacc.2017.01.051. PMID: 28359519
Congenital lung malformations.
Andrade CF, Ferreira HP, Fischer GB
J Bras Pneumol 2011 Mar-Apr;37(2):259-71. doi: 10.1590/s1806-37132011000200017. PMID: 21537663
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Hepatopulmonary syndrome.
Müller C, Schenk P
Wien Klin Wochenschr 1999 May 7;111(9):339-47. PMID: 10407994
Pulmonary edema.
Colice GL
Clin Geriatr Med 1986 May;2(2):411-32. PMID: 3516371

Clinical prediction guides

Effect of Telmisartan on Walking Performance in Patients With Lower Extremity Peripheral Artery Disease: The TELEX Randomized Clinical Trial.
McDermott MM, Bazzano L, Peterson CA, Sufit R, Ferrucci L, Domanchuk K, Zhao L, Polonsky TS, Zhang D, Lloyd-Jones D, Leeuwenburgh C, Guralnik JM, Kibbe MR, Kosmac K, Criqui MH, Tian L
JAMA 2022 Oct 4;328(13):1315-1325. doi: 10.1001/jama.2022.16797. PMID: 36194220Free PMC Article
Update on MR imaging of the pulmonary vasculature.
Aziz M, Krishnam M, Madhuranthakam AJ, Rajiah P
Int J Cardiovasc Imaging 2019 Aug;35(8):1483-1497. Epub 2019 Apr 27 doi: 10.1007/s10554-019-01603-y. PMID: 31030315
The eye in CHD.
Nasir-Ahmad S, Cordina R, Liew G, McCluskey P, Celermajer D
Cardiol Young 2018 Aug;28(8):981-985. doi: 10.1017/S1047951118000859. PMID: 30043722
The pathophysiology of chronic thromboembolic pulmonary hypertension.
Simonneau G, Torbicki A, Dorfmüller P, Kim N
Eur Respir Rev 2017 Mar 31;26(143) Epub 2017 Mar 29 doi: 10.1183/16000617.0112-2016. PMID: 28356405Free PMC Article
Hepatopulmonary Syndrome.
Lv Y, Fan D
Dig Dis Sci 2015 Jul;60(7):1914-23. Epub 2015 Mar 3 doi: 10.1007/s10620-015-3593-0. PMID: 25732713

Recent systematic reviews

Clinical outcomes of pulmonary agenesis: A systematic review of the literature.
Fukuoka S, Yamamura K, Nagata H, Toyomura D, Nagatomo Y, Eguchi Y, Uike K, Hirata Y, Inoue H, Ochiai M, Ohga S
Pediatr Pulmonol 2022 Dec;57(12):3060-3068. Epub 2022 Sep 16 doi: 10.1002/ppul.26135. PMID: 36069476
Internal mammary artery-to-pulmonary vasculature fistula: Systematic review of case reports.
Abdul Jabbar A, Patel A, Marzlin N, Altabaqchali S, Hasan M, Al-Zubaidi M, Agarwal A
Vasc Med 2017 Oct;22(5):426-431. doi: 10.1177/1358863X17724262. PMID: 28990495
Paediatric haemoptysis and the otorhinolaryngologist: Systematic review.
Bannister M
Int J Pediatr Otorhinolaryngol 2017 Jan;92:99-102. Epub 2016 Oct 24 doi: 10.1016/j.ijporl.2016.10.021. PMID: 28012543
Intravenous bevacizumab for complications of hereditary hemorrhagic telangiectasia: a review of the literature.
Arizmendez NP, Rudmik L, Poetker DM
Int Forum Allergy Rhinol 2015 Nov;5(11):1042-7. Epub 2015 Jul 22 doi: 10.1002/alr.21587. PMID: 26202958
Automated segmentation of pulmonary structures in thoracic computed tomography scans: a review.
van Rikxoort EM, van Ginneken B
Phys Med Biol 2013 Sep 7;58(17):R187-220. doi: 10.1088/0031-9155/58/17/R187. PMID: 23956328

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