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Aortic arch syndrome

MedGen UID:
1616
Concept ID:
C0003490
Disease or Syndrome
Synonyms: Aortic Arch Syndrome; Aortic Arch Syndromes; Syndrome, Aortic Arch; Syndromes, Aortic Arch
SNOMED CT: Aortic arch syndrome (359789008)

Definition

A syndrome resulting from structural defects of the arteries that arise from the aortic arch. Signs and symptoms include weakness, dizziness, arm numbness, blurred vision and transient ischemic attacks. [from NCI]

Term Hierarchy

Professional guidelines

PubMed

EDLING NP, NYSTROM B, SELDINGER SI
Acta Radiol (Stockh) 1961 Jun;55:417-32. doi: 10.3109/00016926109175138. PMID: 13725722

Recent clinical studies

Etiology

Lemmens CC, Konings TJAJ, Dean A, Wanhainen A, Mani K, Gormley S, Khashram M, Mees BME, Schurink GWH
Eur J Vasc Endovasc Surg 2025 Jan;69(1):38-45. Epub 2024 Jul 23 doi: 10.1016/j.ejvs.2024.07.023. PMID: 39053643
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269
Muratore F, Pazzola G, Pipitone N, Boiardi L, Salvarani C
Clin Exp Rheumatol 2014 May-Jun;32(3 Suppl 82):S106-11. Epub 2014 May 15 PMID: 24854380
Miyagi K, Mukawa J, Kinjo N, Horikawa K, Mekaru S, Nakasone S, Koga H, Higa Y, Naito M
Acta Neurochir (Wien) 1995;135(1-2):87-92. doi: 10.1007/BF02307420. PMID: 8748798
Criado FJ
Br J Surg 1982 Jun;69 Suppl:S45-51. doi: 10.1002/bjs.1800691316. PMID: 7044468

Diagnosis

Gerber NJ
Eur Neurol 1984;23(6):410-20. doi: 10.1159/000115723. PMID: 6510442
Thompson BW, Read RC, Campbell GS
Arch Surg 1969 May;98(5):607-11. doi: 10.1001/archsurg.1969.01340110099010. PMID: 5778697
Bettelheim H
Bibl Ophthalmol 1968;76:204-14. PMID: 5674844
Shah HS, Shah RM
J Assoc Physicians India 1968 Dec;16(12):949-54. PMID: 4889946
EDLING NP, NYSTROM B, SELDINGER SI
Acta Radiol (Stockh) 1961 Jun;55:417-32. doi: 10.3109/00016926109175138. PMID: 13725722

Therapy

Salvarani C, Cantini F, Hunder GG
Lancet 2008 Jul 19;372(9634):234-45. doi: 10.1016/S0140-6736(08)61077-6. PMID: 18640460
Nuenninghoff DM, Warrington KJ, Matteson EL
Arthritis Rheum 2003 Dec 15;49(6):858-61. doi: 10.1002/art.11453. PMID: 14673975
Gerber NJ
Eur Neurol 1984;23(6):410-20. doi: 10.1159/000115723. PMID: 6510442
Rotman M, Seidenberg B, Rubin I, Botstein C, Bosniak M
Arch Intern Med 1969 Jul;124(1):87-90. PMID: 5791490
Hunder GG, Ward LE, Burbank MK
Ann Intern Med 1967 Mar;66(3):578-82. doi: 10.7326/0003-4819-66-3-578. PMID: 6019233

Prognosis

Lensen KD, Voskuyl AE, Comans EF, van der Laken CJ, Smulders YM
Neth J Med 2016 Jun;74(5):182-92. PMID: 27323671
Muratore F, Pazzola G, Pipitone N, Boiardi L, Salvarani C
Clin Exp Rheumatol 2014 May-Jun;32(3 Suppl 82):S106-11. Epub 2014 May 15 PMID: 24854380
Salvarani C, Cantini F, Hunder GG
Lancet 2008 Jul 19;372(9634):234-45. doi: 10.1016/S0140-6736(08)61077-6. PMID: 18640460
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Gerber NJ
Eur Neurol 1984;23(6):410-20. doi: 10.1159/000115723. PMID: 6510442

Clinical prediction guides

Lemmens CC, Konings TJAJ, Dean A, Wanhainen A, Mani K, Gormley S, Khashram M, Mees BME, Schurink GWH
Eur J Vasc Endovasc Surg 2025 Jan;69(1):38-45. Epub 2024 Jul 23 doi: 10.1016/j.ejvs.2024.07.023. PMID: 39053643
Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269
Both M, Ahmadi-Simab K, Reuter M, Dourvos O, Fritzer E, Ullrich S, Gross WL, Heller M, Bähre M
Ann Rheum Dis 2008 Jul;67(7):1030-3. Epub 2008 Jan 26 doi: 10.1136/ard.2007.082123. PMID: 18223265
Jorens PG, Williame LM, Tombeur JP, Kockx MM, Parizel GA, Zeyen TG
J Cardiovasc Surg (Torino) 1991 May-Jun;32(3):373-5. PMID: 1676030
MYERS JD, MURDAUGH HV, MCINTOSH HD, BLAISDELL RK
AMA Arch Intern Med 1956 Jun;97(6):726-37. doi: 10.1001/archinte.1956.00250240078007. PMID: 13312714

Recent systematic reviews

Duarte MM, Geraldes R, Sousa R, Alarcão J, Costa J
J Stroke Cerebrovasc Dis 2016 Apr;25(4):781-91. Epub 2016 Jan 13 doi: 10.1016/j.jstrokecerebrovasdis.2015.12.005. PMID: 26775269

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