U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Refractory Alveolar Rhabdomyosarcoma

MedGen UID:
1640719
Concept ID:
C4684888
Neoplastic Process

Definition

Alveolar rhabdomyosarcoma that does not respond to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Alveolar Rhabdomyosarcoma

Professional guidelines

PubMed

Barnbrock AE, Luckowitsch M, Schmidt S, Buus-Gehrig C, Koscher L, Becker M, Vokuhl C, Klingebiel T, Lehrnbecher T, Bochennek K
Klin Padiatr 2023 Nov;235(6):360-365. Epub 2023 Jul 11 doi: 10.1055/a-2103-2781. PMID: 37494132
Casanova M, Ferrari A, Bisogno G, Merks JH, De Salvo GL, Meazza C, Tettoni K, Provenzi M, Mazzarino I, Carli M
Cancer 2004 Oct 1;101(7):1664-71. doi: 10.1002/cncr.20544. PMID: 15378498

Recent clinical studies

Etiology

Allen-Rhoades W, Lupo PJ, Scheurer ME, Chi YY, Kuttesch JF, Venkatramani R, Meyer WH, Mascarenhas L
Cancer Med 2023 May;12(9):10222-10229. Epub 2023 Apr 4 doi: 10.1002/cam4.5749. PMID: 37016270Free PMC Article
Endo M, Kataoka T, Fujiwara T, Tsukushi S, Takahashi M, Kobayashi E, Yamada Y, Tanaka T, Nezu Y, Hiraga H, Wasa J, Nagano A, Nakano K, Nakayama R, Hamada T, Kawano M, Torigoe T, Sakamoto A, Asanuma K, Morii T, Machida R, Sekino Y, Fukuda H, Oda Y, Ozaki T, Tanaka K
BMC Cancer 2023 Mar 8;23(1):219. doi: 10.1186/s12885-023-10693-w. PMID: 36890471Free PMC Article
Poli E, Barbon V, Lucchetta S, Cattelan M, Santoro L, Zin A, Milano GM, Zanetti I, Bisogno G, Bonvini P
Oncoimmunology 2022;11(1):2096349. Epub 2022 Jul 6 doi: 10.1080/2162402X.2022.2096349. PMID: 35813575Free PMC Article
Butel T, Karanian M, Pierron G, Orbach D, Ranchere D, Cozic N, Galmiche L, Coulomb A, Corradini N, Lacour B, Proust S, Guerin F, Boutroux H, Rome A, Mansuy L, Vérité C, Defachelles AS, Tirode F, Minard-Colin V
Cancer Med 2020 Apr;9(8):2698-2709. Epub 2020 Feb 22 doi: 10.1002/cam4.2713. PMID: 32087612Free PMC Article
Harel M, Ferrer FA, Shapiro LH, Makari JH
Urol Oncol 2016 Feb;34(2):103-15. Epub 2015 Oct 28 doi: 10.1016/j.urolonc.2015.09.013. PMID: 26519985

Diagnosis

Allen-Rhoades W, Lupo PJ, Scheurer ME, Chi YY, Kuttesch JF, Venkatramani R, Meyer WH, Mascarenhas L
Cancer Med 2023 May;12(9):10222-10229. Epub 2023 Apr 4 doi: 10.1002/cam4.5749. PMID: 37016270Free PMC Article
Metts JL, Trucco M, Weiser DA, Thompson P, Sandler E, Smith T, Crimella J, Sansil S, Thapa R, Fridley BL, Llosa N, Badgett T, Gorlick R, Reed D, Gill J
Cancer Med 2023 Feb;12(4):4270-4281. Epub 2022 Sep 23 doi: 10.1002/cam4.5297. PMID: 36151773Free PMC Article
Poli E, Barbon V, Lucchetta S, Cattelan M, Santoro L, Zin A, Milano GM, Zanetti I, Bisogno G, Bonvini P
Oncoimmunology 2022;11(1):2096349. Epub 2022 Jul 6 doi: 10.1080/2162402X.2022.2096349. PMID: 35813575Free PMC Article
Ricker CA, Woods AD, Simonson W, Lathara M, Srinivasa G, Rudzinski ER, Mansoor A, Irwin RG, Keller C, Berlow NE
Cold Spring Harb Mol Case Stud 2021 Feb;7(1) Epub 2021 Feb 19 doi: 10.1101/mcs.a005983. PMID: 33436392Free PMC Article
Katoh M, Nakagama H
Med Res Rev 2014 Mar;34(2):280-300. Epub 2013 May 21 doi: 10.1002/med.21288. PMID: 23696246

Therapy

Allen-Rhoades W, Lupo PJ, Scheurer ME, Chi YY, Kuttesch JF, Venkatramani R, Meyer WH, Mascarenhas L
Cancer Med 2023 May;12(9):10222-10229. Epub 2023 Apr 4 doi: 10.1002/cam4.5749. PMID: 37016270Free PMC Article
Metts JL, Trucco M, Weiser DA, Thompson P, Sandler E, Smith T, Crimella J, Sansil S, Thapa R, Fridley BL, Llosa N, Badgett T, Gorlick R, Reed D, Gill J
Cancer Med 2023 Feb;12(4):4270-4281. Epub 2022 Sep 23 doi: 10.1002/cam4.5297. PMID: 36151773Free PMC Article
Saulnier-Sholler G, Duda DG, Bergendahl G, Ebb D, Snuderl M, Laetsch TW, Michlitsch J, Hanson D, Isakoff MS, Bielamowicz K, Kraveka JM, Ferguson W, Carmeliet P, De Deene A, Gijsen L, Jain RK
Clin Cancer Res 2022 Sep 15;28(18):3950-3957. doi: 10.1158/1078-0432.CCR-22-1169. PMID: 35833850Free PMC Article
Ricker CA, Woods AD, Simonson W, Lathara M, Srinivasa G, Rudzinski ER, Mansoor A, Irwin RG, Keller C, Berlow NE
Cold Spring Harb Mol Case Stud 2021 Feb;7(1) Epub 2021 Feb 19 doi: 10.1101/mcs.a005983. PMID: 33436392Free PMC Article
Katoh M, Nakagama H
Med Res Rev 2014 Mar;34(2):280-300. Epub 2013 May 21 doi: 10.1002/med.21288. PMID: 23696246

Prognosis

Poli E, Barbon V, Lucchetta S, Cattelan M, Santoro L, Zin A, Milano GM, Zanetti I, Bisogno G, Bonvini P
Oncoimmunology 2022;11(1):2096349. Epub 2022 Jul 6 doi: 10.1080/2162402X.2022.2096349. PMID: 35813575Free PMC Article
Compostella A, Affinita MC, Casanova M, Milano GM, Scagnellato A, Dall'Igna P, Chiaravalli S, Pierobon M, Manzitti C, Zanetti I, Schiavetti A, Sorbara S, Mura RM, Ruggiero A, Ferrari A, Bisogno G
Tumori 2019 Apr;105(2):138-143. Epub 2018 Aug 22 doi: 10.1177/0300891618792479. PMID: 30131003
Gallego S, Zanetti I, Orbach D, Ranchère D, Shipley J, Zin A, Bergeron C, de Salvo GL, Chisholm J, Ferrari A, Jenney M, Mandeville HC, Rogers T, Merks JHM, Mudry P, Glosli H, Milano GM, Ferman S, Bisogno G; European Paediatric Soft Tissue Sarcoma Study Group (EpSSG)
Cancer 2018 Aug 1;124(15):3201-3209. Epub 2018 May 24 doi: 10.1002/cncr.31553. PMID: 29797665
Schmid E, Stagno MJ, Yan J, Schleicher S, Yu W, Honisch S, Lang F, Fuchs J, Seitz G
Cell Physiol Biochem 2017;43(3):1301-1308. Epub 2017 Oct 9 doi: 10.1159/000481842. PMID: 28992614
Harel M, Ferrer FA, Shapiro LH, Makari JH
Urol Oncol 2016 Feb;34(2):103-15. Epub 2015 Oct 28 doi: 10.1016/j.urolonc.2015.09.013. PMID: 26519985

Clinical prediction guides

Allen-Rhoades W, Lupo PJ, Scheurer ME, Chi YY, Kuttesch JF, Venkatramani R, Meyer WH, Mascarenhas L
Cancer Med 2023 May;12(9):10222-10229. Epub 2023 Apr 4 doi: 10.1002/cam4.5749. PMID: 37016270Free PMC Article
Metts JL, Trucco M, Weiser DA, Thompson P, Sandler E, Smith T, Crimella J, Sansil S, Thapa R, Fridley BL, Llosa N, Badgett T, Gorlick R, Reed D, Gill J
Cancer Med 2023 Feb;12(4):4270-4281. Epub 2022 Sep 23 doi: 10.1002/cam4.5297. PMID: 36151773Free PMC Article
Saulnier-Sholler G, Duda DG, Bergendahl G, Ebb D, Snuderl M, Laetsch TW, Michlitsch J, Hanson D, Isakoff MS, Bielamowicz K, Kraveka JM, Ferguson W, Carmeliet P, De Deene A, Gijsen L, Jain RK
Clin Cancer Res 2022 Sep 15;28(18):3950-3957. doi: 10.1158/1078-0432.CCR-22-1169. PMID: 35833850Free PMC Article
Schöffski P, Wozniak A, Leahy MG, Aamdal S, Rutkowski P, Bauer S, Richter S, Grünwald V, Debiec-Rychter M, Sciot R, Geoerger B, Marréaud S, Collette S, Nzokirantevye A, Strauss SJ
Eur J Cancer 2018 May;94:156-167. Epub 2018 Mar 20 doi: 10.1016/j.ejca.2018.02.011. PMID: 29567632
Pappo AS, Vassal G, Crowley JJ, Bolejack V, Hogendoorn PC, Chugh R, Ladanyi M, Grippo JF, Dall G, Staddon AP, Chawla SP, Maki RG, Araujo DM, Geoerger B, Ganjoo K, Marina N, Blay JY, Schuetze SM, Chow WA, Helman LJ
Cancer 2014 Aug 15;120(16):2448-56. Epub 2014 May 2 doi: 10.1002/cncr.28728. PMID: 24797726Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...