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Kidney Epithelioid Angiomyolipoma

MedGen UID:
1677196
Concept ID:
C4763994
Neoplastic Process
Synonyms: Epithelioid Angiomyolipoma/Epithelioid PEComa of the Kidney; Kidney EAML; Kidney Epithelioid Type Angiomyolipoma; Perivascular Epithelioid Cell Tumor of the Kidney; Renal Epithelioid Angiomyolipoma

Definition

An angiomyolipoma that arises from the kidney and is composed exclusively or predominantly of epithelioid cells. It is often associated with cytologic atypia and may recur or metastasize. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVKidney Epithelioid Angiomyolipoma

Professional guidelines

PubMed

Yang JW, Liang C, Yang L
Kaohsiung J Med Sci 2022 Oct;38(10):925-932. Epub 2022 Sep 3 doi: 10.1002/kjm2.12586. PMID: 36056704
Lee KH, Tsai HY, Kao YT, Lin HC, Chou YC, Su SH, Chuang CK
J Formos Med Assoc 2019 Jan;118(1 Pt 1):162-169. Epub 2018 Mar 15 doi: 10.1016/j.jfma.2018.02.012. PMID: 29549981
Nelson CP, Sanda MG
J Urol 2002 Oct;168(4 Pt 1):1315-25. doi: 10.1016/S0022-5347(05)64440-0. PMID: 12352384

Recent clinical studies

Etiology

Wang MX, Segaran N, Bhalla S, Pickhardt PJ, Lubner MG, Katabathina VS, Ganeshan D
Radiographics 2021 Nov-Dec;41(7):1992-2010. Epub 2021 Sep 17 doi: 10.1148/rg.2021210103. PMID: 34534018
Çalışkan S, Gümrükçü G, Özsoy E, Topaktas R, Öztürk Mİ
Rev Assoc Med Bras (1992) 2019 Aug 5;65(7):977-981. doi: 10.1590/1806-9282.65.7.977. PMID: 31389508
Cong X, Zhang J, Xu X, Zhang M, Chen Y
Abdom Radiol (NY) 2018 Oct;43(10):2756-2763. doi: 10.1007/s00261-018-1548-6. PMID: 29525877
Martignoni G, Pea M, Zampini C, Brunelli M, Segala D, Zamboni G, Bonetti F
Semin Diagn Pathol 2015 Mar;32(2):140-59. Epub 2015 Feb 24 doi: 10.1053/j.semdp.2015.02.006. PMID: 25804448
Haas NB, Nathanson KL
Adv Chronic Kidney Dis 2014 Jan;21(1):81-90. doi: 10.1053/j.ackd.2013.10.001. PMID: 24359990Free PMC Article

Diagnosis

Yang JW, Liang C, Yang L
Kaohsiung J Med Sci 2022 Oct;38(10):925-932. Epub 2022 Sep 3 doi: 10.1002/kjm2.12586. PMID: 36056704
Salles DC, Asrani K, Woo J, Vidotto T, Liu HB, Vidal I, Matoso A, Netto GJ, Argani P, Lotan TL
J Pathol 2022 Jun;257(2):158-171. Epub 2022 Mar 29 doi: 10.1002/path.5875. PMID: 35072947Free PMC Article
Çalışkan S, Gümrükçü G, Özsoy E, Topaktas R, Öztürk Mİ
Rev Assoc Med Bras (1992) 2019 Aug 5;65(7):977-981. doi: 10.1590/1806-9282.65.7.977. PMID: 31389508
Jinzaki M, Silverman SG, Akita H, Mikami S, Oya M
Semin Ultrasound CT MR 2017 Feb;38(1):37-46. Epub 2016 Nov 5 doi: 10.1053/j.sult.2016.11.001. PMID: 28237279
Eble JN
Semin Diagn Pathol 1998 Feb;15(1):21-40. PMID: 9503504

Therapy

Anwaier A, Xu WH, Tian X, Ding T, Su JQ, Wang Y, Qu YY, Zhang HL, Ye DW
BMC Urol 2022 Sep 12;22(1):148. doi: 10.1186/s12894-022-01101-9. PMID: 36096809Free PMC Article
Hatano T, Egawa S
Asian J Surg 2020 Oct;43(10):967-972. Epub 2020 Jan 17 doi: 10.1016/j.asjsur.2019.12.008. PMID: 31959574
Chuang CK, Lin HCA, Tasi HY, Lee KH, Kao Y, Chuang FL, Chang YH, Lin PH, Liu CY, Pang ST
Int Urol Nephrol 2017 Sep;49(9):1527-1536. Epub 2017 May 25 doi: 10.1007/s11255-017-1629-4. PMID: 28547571
Wolff N, Kabbani W, Bradley T, Raj G, Watumull L, Brugarolas J
J Clin Oncol 2010 Feb 10;28(5):e65-8. Epub 2010 Jan 4 doi: 10.1200/JCO.2009.26.3061. PMID: 20048172
Higa F, Uchihara T, Haranaga S, Yara S, Tateyama M, Oshiro Y, Shiraishi M, Kumasaka T, Seyama K, Fujita J
Intern Med 2009;48(20):1821-5. Epub 2009 Oct 15 doi: 10.2169/internalmedicine.48.2411. PMID: 19834275

Prognosis

Luo C, Liu Z, Gao M, Hu Q, He X, Xi Y, Cai F, Zhang R, Zeng X, Xiao N
Abdom Radiol (NY) 2022 Jan;47(1):310-319. Epub 2021 Oct 19 doi: 10.1007/s00261-021-03313-3. PMID: 34664098
Lee W, Choi SY, Lee C, Yoo S, You D, Jeong IG, Song C, Kim KS, Hong B, Hong JH, Ahn H, Kim CS
Investig Clin Urol 2018 Nov;59(6):357-362. Epub 2018 Oct 4 doi: 10.4111/icu.2018.59.6.357. PMID: 30402567Free PMC Article
Varma S, Gupta S, Talwar J, Forte F, Dhar M
J Nephrol 2011 Jan-Feb;24(1):18-22. doi: 10.5301/jn.2010.5451. PMID: 20349413
Hornick JL, Fletcher CD
Histopathology 2006 Jan;48(1):75-82. doi: 10.1111/j.1365-2559.2005.02316.x. PMID: 16359539
Eble JN
Semin Diagn Pathol 1998 Feb;15(1):21-40. PMID: 9503504

Clinical prediction guides

Salles DC, Asrani K, Woo J, Vidotto T, Liu HB, Vidal I, Matoso A, Netto GJ, Argani P, Lotan TL
J Pathol 2022 Jun;257(2):158-171. Epub 2022 Mar 29 doi: 10.1002/path.5875. PMID: 35072947Free PMC Article
Luo C, Liu Z, Gao M, Hu Q, He X, Xi Y, Cai F, Zhang R, Zeng X, Xiao N
Abdom Radiol (NY) 2022 Jan;47(1):310-319. Epub 2021 Oct 19 doi: 10.1007/s00261-021-03313-3. PMID: 34664098
Lee W, Choi SY, Lee C, Yoo S, You D, Jeong IG, Song C, Kim KS, Hong B, Hong JH, Ahn H, Kim CS
Investig Clin Urol 2018 Nov;59(6):357-362. Epub 2018 Oct 4 doi: 10.4111/icu.2018.59.6.357. PMID: 30402567Free PMC Article
Varma S, Gupta S, Talwar J, Forte F, Dhar M
J Nephrol 2011 Jan-Feb;24(1):18-22. doi: 10.5301/jn.2010.5451. PMID: 20349413
Hornick JL, Fletcher CD
Histopathology 2006 Jan;48(1):75-82. doi: 10.1111/j.1365-2559.2005.02316.x. PMID: 16359539

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