U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Sporadic Malignant Peripheral Nerve Sheath Tumor

MedGen UID:
1716654
•Concept ID:
C5236144
•
Neoplastic Process

Definition

A malignant peripheral nerve sheath tumor that is not caused by inherited genetic mutations. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSporadic Malignant Peripheral Nerve Sheath Tumor

Professional guidelines

PubMed

Malignant Peripheral Nerve Sheath Tumors of the Brachial Plexus: A Single-Center Experience on Diagnosis, Management, and Outcomes.
Donaldson EK, Winter JM, Chandler RM, Clark TA, Giuffre JL
Ann Plast Surg 2023 Apr 1;90(4):339-342. Epub 2023 Feb 4 doi: 10.1097/SAP.0000000000003462. PMID: 36752552
Experience of a single center in the treatment of rare malignant peripheral nerve sheath tumors during the years 1991-2021.
Ptchelintseva A, Nuutinen H, Salo J, Tukiainen E
J Plast Surg Hand Surg 2023 Feb-Dec;57(1-6):376-382. Epub 2022 Oct 16 doi: 10.1080/2000656X.2022.2131559. PMID: 36244030
Outcomes of Treatment for Malignant Peripheral Nerve Sheath Tumors: Different Clinical Features Associated with Neurofibromatosis Type 1.
Hwang IK, Hahn SM, Kim HS, Kim SK, Kim HS, Shin KH, Suh CO, Lyu CJ, Han JW
Cancer Res Treat 2017 Jul;49(3):717-726. Epub 2016 Dec 1 doi: 10.4143/crt.2016.271. PMID: 28052660Free PMC Article

Recent clinical studies

Diagnosis

Repetitive syncope caused by a rare massive sporadic malignant peripheral nerve sheath tumor involving carotid arteries: A case report.
Wang T, Wang J, Zhao J, Yuan D, Yao W
Medicine (Baltimore) 2021 Feb 5;100(5):e24386. doi: 10.1097/MD.0000000000024386. PMID: 33592886Free PMC Article
A case of a sporadic malignant peripheral nerve sheath tumor of the urinary bladder with concomitant in situ urothelial carcinoma treated by transuretheral resection.
Sari A, Bal K, Tunakan M, Ozturk C
Indian J Pathol Microbiol 2011 Jan-Mar;54(1):147-9. doi: 10.4103/0377-4929.77376. PMID: 21393901

Prognosis

The prognostic value of C-X-C motif chemokine receptor 4 in patients with sporadic malignant peripheral nerve sheath tumors.
Zhang C, Chang FY, Zhou WY, Yang JL
Chin J Cancer 2017 Oct 11;36(1):80. doi: 10.1186/s40880-017-0246-z. PMID: 29020982Free PMC Article
A case of a sporadic malignant peripheral nerve sheath tumor of the urinary bladder with concomitant in situ urothelial carcinoma treated by transuretheral resection.
Sari A, Bal K, Tunakan M, Ozturk C
Indian J Pathol Microbiol 2011 Jan-Mar;54(1):147-9. doi: 10.4103/0377-4929.77376. PMID: 21393901

Clinical prediction guides

The prognostic value of C-X-C motif chemokine receptor 4 in patients with sporadic malignant peripheral nerve sheath tumors.
Zhang C, Chang FY, Zhou WY, Yang JL
Chin J Cancer 2017 Oct 11;36(1):80. doi: 10.1186/s40880-017-0246-z. PMID: 29020982Free PMC Article

Supplemental Content

Table of contents

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Related information

    • PMC Articles
      Related information in PubMed Central Links
    • PubMed
      Related literature resources in PubMed

    Recent activity

    Clear Turn Off Turn On

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...