Vulvar Angiosarcoma

MedGen UID:: 1785656
•Concept ID:: C5447285
•: Neoplastic Process

Definition

A rare angiosarcoma that arises from the vulva. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVVulvar Angiosarcoma

Disorder by Site
- Connective and Soft Tissue Disorder
  - Connective and soft tissue neoplasm
    - Sarcoma
      - Angiosarcoma
        Soft Tissue Angiosarcoma
        Vulvar Angiosarcoma

Recent clinical studies

Etiology

Angiosarcomas of primary gynecologic origin: a clinicopathologic review and quantitative analysis of survival.

Kruse AJ, Sep S, Slangen BF, Vandevijver NM, Van Gorp T, Kruitwagen RF, Van de Vijver KK
Int J Gynecol Cancer 2014 Jan;24(1):4-12. doi: 10.1097/IGC.0000000000000020. PMID: 24257655

Postoperative radiotherapy for cervix cancer incidentally discovered after a simple hysterectomy for either benign conditions or noninvasive pathology.

Smith KB, Amdur RJ, Yeung AR, Morris CG, Kirwan J, Morgan LS
Am J Clin Oncol 2010 Jun;33(3):229-32. doi: 10.1097/COC.0b013e3181a6500d. PMID: 19806037

Epithelioid angiosarcoma of the mons after chemoradiation for vulvar cancer.

Guirguis A, Kanbour-Shakir A, Kelley J
Int J Gynecol Pathol 2007 Jul;26(3):265-8. doi: 10.1097/01.pgp.0000250145.67462.c9. PMID: 17581409

Vascular tumors of the female genital tract: a clinicopathological study of nine cases.

Kondi-Pafiti A, Kairi-Vassilatou E, Spanidou-Carvouni H, Kontogianni K, Dimopoulou K, Goula K
Eur J Gynaecol Oncol 2003;24(1):48-50. PMID: 12691317

Primary vulvar sarcomas.

Nirenberg A, Ostör AG, Slavin J, Riley CB, Rome RM
Int J Gynecol Pathol 1995 Jan;14(1):55-62. doi: 10.1097/00004347-199501000-00010. PMID: 7883427

See all (5)

Diagnosis

Acquired Elastotic Hemangioma-like Change of the Vulva Associated With Lichen Sclerosus.

Val-Bernal JF, Hermana S, Aller L
Int J Gynecol Pathol 2022 Nov 1;41(6):636-641. Epub 2021 Sep 29 doi: 10.1097/PGP.0000000000000829. PMID: 34593702

Primary angiosarcoma of the vulva: report of a case misdiagnosed as a benign tumor.

Stolnicu S, Podoleanu C, Orban I, Stan O, Szabo B
Pol J Pathol 2021;72(2):167-169. doi: 10.5114/pjp.2021.109519. PMID: 34706524

Intravascular papillary endothelial hyperplasia of the vulva: report of a patient with Masson tumor of the vulva and literature review.

Beutler BD, Cohen PR
Dermatol Online J 2016 May 15;22(5) PMID: 27617519

Angiosarcomas of primary gynecologic origin: a clinicopathologic review and quantitative analysis of survival.

Kruse AJ, Sep S, Slangen BF, Vandevijver NM, Van Gorp T, Kruitwagen RF, Van de Vijver KK
Int J Gynecol Cancer 2014 Jan;24(1):4-12. doi: 10.1097/IGC.0000000000000020. PMID: 24257655

Epithelioid angiosarcoma of the mons after chemoradiation for vulvar cancer.

Guirguis A, Kanbour-Shakir A, Kelley J
Int J Gynecol Pathol 2007 Jul;26(3):265-8. doi: 10.1097/01.pgp.0000250145.67462.c9. PMID: 17581409

See all (12)

Therapy

Postoperative radiotherapy for cervix cancer incidentally discovered after a simple hysterectomy for either benign conditions or noninvasive pathology.

Smith KB, Amdur RJ, Yeung AR, Morris CG, Kirwan J, Morgan LS
Am J Clin Oncol 2010 Jun;33(3):229-32. doi: 10.1097/COC.0b013e3181a6500d. PMID: 19806037

Groin angiosarcoma following radiotherapy for vulvar cancer.

Sanz C, Moreno F, Armas A, Casado A, Castillo MC
Gynecol Oncol 2005 May;97(2):677-80. doi: 10.1016/j.ygyno.2004.12.061. PMID: 15863181

Sarcoma in association with multimodality management of vulvar cancer: two case reports.

Hyde S, Uitterhoeve LJ, Schilthuis MS, ten Kate FJ, van der Velden J
Gynecol Oncol 2001 May;81(2):320-3. doi: 10.1006/gyno.2001.6139. PMID: 11330970

See all (3)

Prognosis

Primary angiosarcoma of the vulva: report of a case misdiagnosed as a benign tumor.

Stolnicu S, Podoleanu C, Orban I, Stan O, Szabo B
Pol J Pathol 2021;72(2):167-169. doi: 10.5114/pjp.2021.109519. PMID: 34706524

Angiosarcomas of primary gynecologic origin: a clinicopathologic review and quantitative analysis of survival.

Kruse AJ, Sep S, Slangen BF, Vandevijver NM, Van Gorp T, Kruitwagen RF, Van de Vijver KK
Int J Gynecol Cancer 2014 Jan;24(1):4-12. doi: 10.1097/IGC.0000000000000020. PMID: 24257655

Groin angiosarcoma following radiotherapy for vulvar cancer.

Sanz C, Moreno F, Armas A, Casado A, Castillo MC
Gynecol Oncol 2005 May;97(2):677-80. doi: 10.1016/j.ygyno.2004.12.061. PMID: 15863181

Primary vulvar sarcomas.

Nirenberg A, Ostör AG, Slavin J, Riley CB, Rome RM
Int J Gynecol Pathol 1995 Jan;14(1):55-62. doi: 10.1097/00004347-199501000-00010. PMID: 7883427

Soft tissue sarcomas of vulva.

Davos I, Abell MR
Gynecol Oncol 1976 Mar;4(1):70-86. doi: 10.1016/0090-8258(76)90009-3. PMID: 186362

See all (7)