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Vulvar Distal-Type Epithelioid Sarcoma

MedGen UID:
1793841
•Concept ID:
C5557400
•
Neoplastic Process

Definition

A rare epithelioid sarcoma of the distal type that arises from the vulva. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar Distal-Type Epithelioid Sarcoma

Recent clinical studies

Etiology

"Proximal-type" epithelioid sarcoma, a distinctive aggressive neoplasm showing rhabdoid features. Clinicopathologic, immunohistochemical, and ultrastructural study of a series.
Guillou L, Wadden C, Coindre JM, Krausz T, Fletcher CD
Am J Surg Pathol 1997 Feb;21(2):130-46. doi: 10.1097/00000478-199702000-00002. PMID: 9042279

Diagnosis

Immunoreactivity for Ca 125 and INI 1 loss of expression are useful markers in the diagnosis of vulvar proximal-type epithelioid sarcomas: report of two cases.
Cossu A, Paliogiannis P, Capobianco G, Sini MC, Dessole M, Dessole S, Palmieri G
Eur J Gynaecol Oncol 2013;34(5):469-72. PMID: 24475586
"Proximal-type" epithelioid sarcoma, a distinctive aggressive neoplasm showing rhabdoid features. Clinicopathologic, immunohistochemical, and ultrastructural study of a series.
Guillou L, Wadden C, Coindre JM, Krausz T, Fletcher CD
Am J Surg Pathol 1997 Feb;21(2):130-46. doi: 10.1097/00000478-199702000-00002. PMID: 9042279

Clinical prediction guides

Immunoreactivity for Ca 125 and INI 1 loss of expression are useful markers in the diagnosis of vulvar proximal-type epithelioid sarcomas: report of two cases.
Cossu A, Paliogiannis P, Capobianco G, Sini MC, Dessole M, Dessole S, Palmieri G
Eur J Gynaecol Oncol 2013;34(5):469-72. PMID: 24475586
"Proximal-type" epithelioid sarcoma, a distinctive aggressive neoplasm showing rhabdoid features. Clinicopathologic, immunohistochemical, and ultrastructural study of a series.
Guillou L, Wadden C, Coindre JM, Krausz T, Fletcher CD
Am J Surg Pathol 1997 Feb;21(2):130-46. doi: 10.1097/00000478-199702000-00002. PMID: 9042279

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