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Distal aortic arch hypoplasia

MedGen UID:: 1814379
•Concept ID:: C5676815
•: Congenital Abnormality

HPO:	HP:0034229

Definition

A type of aortic arch hypoplasia whereby the distal aortic arch (arch distal to the ductus arteriosus) has a diameter of less than 60% of the diameter of the ascending aorta. [from HPO]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVDistal aortic arch hypoplasia

Abnormal vascular morphology
- Abnormal blood vessel morphology
  - Abnormal morphology of the great vessels
    - Abnormal aortic morphology
      - Abnormal aortic arch morphology
        Hypoplastic aortic arch
        Distal aortic arch hypoplasia

Professional guidelines

PubMed

Surgical treatment for right-side aortic arch concomitant with Kommerell's diverticulum: techniques selection and follow-up results.

Wang Y, Li S, Jin M, Xue Y, Wang D, Zhou Q
Eur J Med Res 2024 Jan 3;29(1):10. doi: 10.1186/s40001-023-01595-5. PMID: 38172972 Free PMC Article

Contemporary Management of Type B Aortic Dissection in the Endovascular Era.

Bannazadeh M, Tadros RO, McKinsey J, Chander R, Marin ML, Faries PL
Surg Technol Int 2016 Apr;28:214-21. PMID: 27175814

Diagnosing Neonatal Aortic Coarctation in the Setting of Patent Ductus Arteriosus.

Peng DM, Punn R, Maeda K, Selamet Tierney ES
Ann Thorac Surg 2016 Mar;101(3):1005-10. Epub 2015 Dec 1 doi: 10.1016/j.athoracsur.2015.09.050. PMID: 26652138

See all (3)

Recent clinical studies

Etiology

Equal cerebral perfusion during extended aortic coarctation repair.

Rüffer A, Knieling F, Cesnjevar R, Regensburger A, Purbojo A, Dittrich S, Münch F, Wölfle J, Jüngert J
Eur J Cardiothorac Surg 2022 Jan 24;61(2):299-306. doi: 10.1093/ejcts/ezab415. PMID: 34718510

Modified technique for coarctation of aorta with hypoplastic distal aortic arch.

Kozyrev IA, Kotin NA, Averkin II, Ivanov AA, Latypov AA, Gordeev ML, Vasichkina ES, Pervunina TM, Grekhov EV
J Card Surg 2021 Jun;36(6):2063-2069. Epub 2021 Mar 19 doi: 10.1111/jocs.15492. PMID: 33738821

Distal Aortic Arch Hypoplasia and Coarctation Repair: A Tailored Enlargement Technique.

Poncelet AJ, Henkens A, Sluysmans T, Moniotte S, de Beco G, Momeni M, Detaille T, Rubay JE
World J Pediatr Congenit Heart Surg 2018 Sep;9(5):496-503. doi: 10.1177/2150135118780611. PMID: 30157733

Modified reverse aortoplasty versus extended anastomosis in patients with coarctation of the aorta and distal arch hypoplasia.

Soynov I, Sinelnikov Y, Gorbatykh Y, Omelchenko A, Kornilov I, Nichay N, Bogachev-Prokophiev A, Karaskov A
Eur J Cardiothorac Surg 2018 Jan 1;53(1):254-261. doi: 10.1093/ejcts/ezx249. PMID: 28977406

Impact of Coronary Artery Anatomy in Arterial Switch Procedure on Early Mortality and Morbidity.

Altin FH, Sengul FS, Yildiz O, Tosun O, Ozturk E, Kyaruzi M, Cine N, Guzeltas A, Yeniterzi M, Bakir İ
Congenit Heart Dis 2016 Mar-Apr;11(2):115-21. Epub 2015 Aug 24 doi: 10.1111/chd.12295. PMID: 26303170

See all (5)

Diagnosis

Distal Aortic Arch Hypoplasia and Coarctation Repair: A Tailored Enlargement Technique.

Poncelet AJ, Henkens A, Sluysmans T, Moniotte S, de Beco G, Momeni M, Detaille T, Rubay JE
World J Pediatr Congenit Heart Surg 2018 Sep;9(5):496-503. doi: 10.1177/2150135118780611. PMID: 30157733

Impact of Coronary Artery Anatomy in Arterial Switch Procedure on Early Mortality and Morbidity.

See all (2)

Therapy

Equal cerebral perfusion during extended aortic coarctation repair.

Modified reverse aortoplasty versus extended anastomosis in patients with coarctation of the aorta and distal arch hypoplasia.

Soynov I, Sinelnikov Y, Gorbatykh Y, Omelchenko A, Kornilov I, Nichay N, Bogachev-Prokophiev A, Karaskov A
Eur J Cardiothorac Surg 2018 Jan 1;53(1):254-261. doi: 10.1093/ejcts/ezx249. PMID: 28977406

See all (2)

Prognosis

Distal Aortic Arch Hypoplasia and Coarctation Repair: A Tailored Enlargement Technique.

Poncelet AJ, Henkens A, Sluysmans T, Moniotte S, de Beco G, Momeni M, Detaille T, Rubay JE
World J Pediatr Congenit Heart Surg 2018 Sep;9(5):496-503. doi: 10.1177/2150135118780611. PMID: 30157733

Modified reverse aortoplasty versus extended anastomosis in patients with coarctation of the aorta and distal arch hypoplasia.

Soynov I, Sinelnikov Y, Gorbatykh Y, Omelchenko A, Kornilov I, Nichay N, Bogachev-Prokophiev A, Karaskov A
Eur J Cardiothorac Surg 2018 Jan 1;53(1):254-261. doi: 10.1093/ejcts/ezx249. PMID: 28977406

Impact of Coronary Artery Anatomy in Arterial Switch Procedure on Early Mortality and Morbidity.

See all (3)

Clinical prediction guides

Modified technique for coarctation of aorta with hypoplastic distal aortic arch.

Modified reverse aortoplasty versus extended anastomosis in patients with coarctation of the aorta and distal arch hypoplasia.

Soynov I, Sinelnikov Y, Gorbatykh Y, Omelchenko A, Kornilov I, Nichay N, Bogachev-Prokophiev A, Karaskov A
Eur J Cardiothorac Surg 2018 Jan 1;53(1):254-261. doi: 10.1093/ejcts/ezx249. PMID: 28977406

Impact of Coronary Artery Anatomy in Arterial Switch Procedure on Early Mortality and Morbidity.

See all (3)

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Distal aortic arch hypoplasia

Definition

Term Hierarchy

Professional guidelines

PubMed

Recent clinical studies

Etiology

Diagnosis

Therapy

Prognosis

Clinical prediction guides

Supplemental Content

Table of contents

Clinical resources

Practice guidelines

Consumer resources

Reviews

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