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Abnormal extrahepatic bile duct morphology

MedGen UID:
1842019
•Concept ID:
C5826835
•
Anatomical Abnormality
HPO: HP:0035013

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal extrahepatic bile duct morphology

Professional guidelines

PubMed

Diagnostic criteria for congenital biliary dilatation 2015.
Hamada Y, Ando H, Kamisawa T, Itoi T, Urushihara N, Koshinaga T, Saito T, Fujii H, Morotomi Y
J Hepatobiliary Pancreat Sci 2016 Jun;23(6):342-6. Epub 2016 May 3 doi: 10.1002/jhbp.346. PMID: 26996969
Diagnosis and treatment of pancreaticobiliary maljunction in children.
Ono S, Fumino S, Iwai N
Surg Today 2011 May;41(5):601-5. Epub 2011 May 1 doi: 10.1007/s00595-010-4492-9. PMID: 21533929
Biliary atresia: pathogenesis and treatment.
Bates MD, Bucuvalas JC, Alonso MH, Ryckman FC
Semin Liver Dis 1998;18(3):281-93. doi: 10.1055/s-2007-1007164. PMID: 9773428

Recent clinical studies

Etiology

Biliary carcinogenesis in pancreaticobiliary maljunction.
Kamisawa T, Kuruma S, Chiba K, Tabata T, Koizumi S, Kikuyama M
J Gastroenterol 2017 Feb;52(2):158-163. Epub 2016 Oct 4 doi: 10.1007/s00535-016-1268-z. PMID: 27704265
Imaging of choledochal cysts.
Lewis VA, Adam SZ, Nikolaidis P, Wood C, Wu JG, Yaghmai V, Miller FH
Abdom Imaging 2015 Aug;40(6):1567-80. doi: 10.1007/s00261-015-0381-4. PMID: 25682292
Choledochal cyst.
Gafur MA, Rahman MZ
Mymensingh Med J 2007 Jan;16(1):113-6. doi: 10.3329/mmj.v16i1.264. PMID: 17344793
Biliary atresia.
Chardot C
Orphanet J Rare Dis 2006 Jul 26;1:28. doi: 10.1186/1750-1172-1-28. PMID: 16872500Free PMC Article
Biliary atresia revisited.
Kahn E
Pediatr Dev Pathol 2004 Mar-Apr;7(2):109-24. Epub 2004 Mar 4 doi: 10.1007/s10024-003-0307-y. PMID: 14994122

Diagnosis

Pancreaticobiliary maljunction and congenital biliary dilatation.
Kamisawa T, Kaneko K, Itoi T, Ando H
Lancet Gastroenterol Hepatol 2017 Aug;2(8):610-618. doi: 10.1016/S2468-1253(17)30002-X. PMID: 28691687
Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Pancreaticobiliary maljunction.
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Congenital biliary dilatation.
Miyano T, Yamataka A, Li L
Semin Pediatr Surg 2000 Nov;9(4):187-95. doi: 10.1053/spsu.2000.18843. PMID: 11112836

Therapy

Advances in understanding of biliary atresia pathogenesis and progression - a riddle wrapped in a mystery inside an enigma.
Davenport M, Kronfli R, Makin E
Expert Rev Gastroenterol Hepatol 2023 Apr;17(4):343-352. Epub 2023 Mar 15 doi: 10.1080/17474124.2023.2191188. PMID: 36908275
Perioperative Complications in Neonatal Surgery: Biliary Atresia and Choledochal Malformations.
Wilde JCH, Calinescu AM, Wildhaber BE
Eur J Pediatr Surg 2018 Apr;28(2):156-162. Epub 2018 Mar 6 doi: 10.1055/s-0038-1636929. PMID: 29510428
Portal biliopathy.
Khuroo MS, Rather AA, Khuroo NS, Khuroo MS
World J Gastroenterol 2016 Sep 21;22(35):7973-82. doi: 10.3748/wjg.v22.i35.7973. PMID: 27672292Free PMC Article
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article
Pancreaticobiliary maljunction.
Kamisawa T, Takuma K, Anjiki H, Egawa N, Kurata M, Honda G, Tsuruta K, Sasaki T
Clin Gastroenterol Hepatol 2009 Nov;7(11 Suppl):S84-8. doi: 10.1016/j.cgh.2009.08.024. PMID: 19896105

Prognosis

Choledochal malformations: global research, scientific advances and key controversies.
Friedmacher F, Ford KE, Davenport M
Pediatr Surg Int 2019 Mar;35(3):273-282. Epub 2018 Nov 7 doi: 10.1007/s00383-018-4392-4. PMID: 30406431
Biliary atresia.
Mieli-Vergani G, Vergani D
Semin Immunopathol 2009 Sep;31(3):371-81. Epub 2009 Jun 17 doi: 10.1007/s00281-009-0171-6. PMID: 19533128
Acute recurrent pancreatitis.
Lehman GA
Can J Gastroenterol 2003 Jun;17(6):381-3. doi: 10.1155/2003/781237. PMID: 12813605
Sclerosing cholangitis.
Lillemoe KD, Pitt HA, Cameron JL
Adv Surg 1988;21:65-92. PMID: 3318316
Neonatal cholestasis.
Balistreri WF
J Pediatr 1985 Feb;106(2):171-84. doi: 10.1016/s0022-3476(85)80282-1. PMID: 3881579

Clinical prediction guides

Association between anatomic variations of extrahepatic and intrahepatic bile ducts: Do look up!
Renzulli M, Brandi N, Brocchi S, Balacchi C, Lanza C, Pettinari I, Stefanini B, Carrafiello G, Piscaglia F, Golfieri R, Marasco G
J Anat 2023 Apr;242(4):683-694. Epub 2023 Jan 20 doi: 10.1111/joa.13808. PMID: 36670522Free PMC Article
Choledochal cysts: Similarities and differences between Asian and Western countries.
Baison GN, Bonds MM, Helton WS, Kozarek RA
World J Gastroenterol 2019 Jul 14;25(26):3334-3343. doi: 10.3748/wjg.v25.i26.3334. PMID: 31341359Free PMC Article
Normograms for the Extrahepatic Bile Duct Diameter in Children.
Feng A, O'hara SM, Gupta R, Fei L, Lin TK
J Pediatr Gastroenterol Nutr 2017 Mar;64(3):e61-e64. doi: 10.1097/MPG.0000000000001372. PMID: 27513696
"Biliary Diseases with Pancreatic Counterparts": Cross-sectional Imaging Findings.
Katabathina VS, Flaherty EM, Dasyam AK, Menias CO, Riddle ND, Lath N, Kozaka K, Matsui O, Nakanuma Y, Prasad SR
Radiographics 2016 Mar-Apr;36(2):374-92. Epub 2016 Feb 1 doi: 10.1148/rg.2016150071. PMID: 26824512
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article

Recent systematic reviews

Defining an optimal surveillance strategy for patients following choledochal cyst resection: results of a systematic review.
Koea J, O'Grady M, Agraval J, Srinivasa S
ANZ J Surg 2022 Jun;92(6):1356-1364. Epub 2022 May 17 doi: 10.1111/ans.17775. PMID: 35579057
Left-sided gallbladder: a systematic review of a rare biliary anomaly.
Pereira R, Singh T, Avramovic J, Baker S, Eslick GD, Cox MR
ANZ J Surg 2019 Nov;89(11):1392-1397. Epub 2019 Mar 5 doi: 10.1111/ans.15041. PMID: 30836441
A systematic review of the anatomical findings of multiple gallbladders.
Darnis B, Mohkam K, Cauchy F, Cazauran JB, Bancel B, Rode A, Ducerf C, Lesurtel M, Mabrut JY
HPB (Oxford) 2018 Nov;20(11):985-991. Epub 2018 Jun 7 doi: 10.1016/j.hpb.2018.04.002. PMID: 29887260
Therapeutic approaches for portal biliopathy: A systematic review.
Franceschet I, Zanetto A, Ferrarese A, Burra P, Senzolo M
World J Gastroenterol 2016 Dec 7;22(45):9909-9920. doi: 10.3748/wjg.v22.i45.9909. PMID: 28018098Free PMC Article
Utility of fluorescent cholangiography during laparoscopic cholecystectomy: A systematic review.
Pesce A, Piccolo G, La Greca G, Puleo S
World J Gastroenterol 2015 Jul 7;21(25):7877-83. doi: 10.3748/wjg.v21.i25.7877. PMID: 26167088Free PMC Article

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