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Extralobar congenital pulmonary sequestration

MedGen UID:
1843113
•Concept ID:
C5679951
•
Congenital Abnormality
Synonyms: Congenital extrapulmonary sequestration; congenital extrapulmonary sequestration; Extralobar congenital bronchopulmonary sequestration; extralobar congenital bronchopulmonary sequestration; extralobar congenital pulmonary sequestration
 
Monarch Initiative: MONDO:0017246
Orphanet: ORPHA280811

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVExtralobar congenital pulmonary sequestration

Professional guidelines

PubMed

Imaging and differential diagnosis of suprarenal masses in the fetus.
Maki E, Oh K, Rogers S, Sohaey R
J Ultrasound Med 2014 May;33(5):895-904. doi: 10.7863/ultra.33.5.895. PMID: 24764345

Recent clinical studies

Etiology

Revising the classification of lung sequestrations.
Alamo L, Saltiel S, Tenisch E
Clin Imaging 2021 Sep;77:92-97. Epub 2021 Feb 23 doi: 10.1016/j.clinimag.2021.02.024. PMID: 33662713
Surgical treatment of pulmonary sequestration in adults and children: long-term results.
Trabalza Marinucci B, Maurizi G, Vanni C, Cardillo G, Poggi C, Pardi V, Inserra A, Rendina EA
Interact Cardiovasc Thorac Surg 2020 Jul 1;31(1):71-77. doi: 10.1093/icvts/ivaa054. PMID: 32300793
The pathology of congenital lung lesions.
Fowler DJ, Gould SJ
Semin Pediatr Surg 2015 Aug;24(4):176-82. Epub 2015 Feb 27 doi: 10.1053/j.sempedsurg.2015.02.002. PMID: 26051050
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Sequestrations of the lung.
Stocker JT
Semin Diagn Pathol 1986 May;3(2):106-21. PMID: 3303232

Diagnosis

Pulmonary sequestration: What the radiologist should know.
Gabelloni M, Faggioni L, Accogli S, Aringhieri G, Neri E
Clin Imaging 2021 May;73:61-72. Epub 2020 Dec 3 doi: 10.1016/j.clinimag.2020.11.040. PMID: 33310586
Anomalous Systemic Arterial Supply to the Lung: To Which Category Should This Belong?
Sha JM, Zhao H, Lin ZB
Heart Lung Circ 2020 Sep;29(9):1292-1300. Epub 2019 Aug 31 doi: 10.1016/j.hlc.2019.08.009. PMID: 32349946
MR imaging of thoracic abnormalities in the fetus.
Recio Rodríguez M, Martínez de Vega V, Cano Alonso R, Carrascoso Arranz J, Martínez Ten P, Pérez Pedregosa J
Radiographics 2012 Nov-Dec;32(7):E305-21. doi: 10.1148/rg.327125053. PMID: 23150864
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956
Pulmonary sequestration.
O'Mara CS, Baker RR, Jeyasingham K
Surg Gynecol Obstet 1978 Oct;147(4):609-16. PMID: 360452

Therapy

Clinical analysis of extralobar pulmonary sequestration with torsion in children: report of 6 cases.
Ti Y, Wang Y, Huang J, Zheng F, Zhang Q
J Cardiothorac Surg 2022 Jun 29;17(1):168. doi: 10.1186/s13019-022-01921-8. PMID: 35768850Free PMC Article
Hybrid minimally invasive treatment of intralobar pulmonary sequestration: a single-centre experience.
Grossi W, Londero F, Vit A, De Franceschi E, Masullo G, Sponza M, Morelli A
Interact Cardiovasc Thorac Surg 2022 Jan 18;34(2):255-257. doi: 10.1093/icvts/ivab245. PMID: 34480559Free PMC Article
Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration: a 12-year 3-center experience in China.
Xu G, Zhou J, Zeng S, Zhang M, Ouyang Z, Zhao Y, Yuan H, Tong L, Yin C, Zhou Q
Sci Rep 2019 Jan 30;9(1):943. doi: 10.1038/s41598-018-37268-1. PMID: 30700771Free PMC Article
Pulmonary sequestration in adults: a retrospective review of resected and unresected cases.
Alsumrain M, Ryu JH
BMC Pulm Med 2018 Jun 5;18(1):97. doi: 10.1186/s12890-018-0663-z. PMID: 29871620Free PMC Article
Extralobar sequestration with congenital diaphragmatic hernia: a complicated case study.
Harris K
Neonatal Netw 2004 Nov-Dec;23(6):7-24. doi: 10.1891/0730-0832.23.6.7. PMID: 15612417

Prognosis

Clinical analysis of extralobar pulmonary sequestration with torsion in children: report of 6 cases.
Ti Y, Wang Y, Huang J, Zheng F, Zhang Q
J Cardiothorac Surg 2022 Jun 29;17(1):168. doi: 10.1186/s13019-022-01921-8. PMID: 35768850Free PMC Article
Surgical treatment of pulmonary sequestration in adults and children: long-term results.
Trabalza Marinucci B, Maurizi G, Vanni C, Cardillo G, Poggi C, Pardi V, Inserra A, Rendina EA
Interact Cardiovasc Thorac Surg 2020 Jul 1;31(1):71-77. doi: 10.1093/icvts/ivaa054. PMID: 32300793
MR imaging of thoracic abnormalities in the fetus.
Recio Rodríguez M, Martínez de Vega V, Cano Alonso R, Carrascoso Arranz J, Martínez Ten P, Pérez Pedregosa J
Radiographics 2012 Nov-Dec;32(7):E305-21. doi: 10.1148/rg.327125053. PMID: 23150864
Asymptomatic congenital lung malformations.
Laberge JM, Puligandla P, Flageole H
Semin Pediatr Surg 2005 Feb;14(1):16-33. doi: 10.1053/j.sempedsurg.2004.10.022. PMID: 15770585
Pulmonary sequestration.
Corbett HJ, Humphrey GM
Paediatr Respir Rev 2004 Mar;5(1):59-68. doi: 10.1016/j.prrv.2003.09.009. PMID: 15222956

Clinical prediction guides

Hybrid minimally invasive treatment of intralobar pulmonary sequestration: a single-centre experience.
Grossi W, Londero F, Vit A, De Franceschi E, Masullo G, Sponza M, Morelli A
Interact Cardiovasc Thorac Surg 2022 Jan 18;34(2):255-257. doi: 10.1093/icvts/ivab245. PMID: 34480559Free PMC Article
Prenatal diagnosis of fetal intraabdominal extralobar pulmonary sequestration: a 12-year 3-center experience in China.
Xu G, Zhou J, Zeng S, Zhang M, Ouyang Z, Zhao Y, Yuan H, Tong L, Yin C, Zhou Q
Sci Rep 2019 Jan 30;9(1):943. doi: 10.1038/s41598-018-37268-1. PMID: 30700771Free PMC Article
Imaging findings in fetal diaphragmatic abnormalities.
Alamo L, Gudinchet F, Meuli R
Pediatr Radiol 2015 Dec;45(13):1887-900. Epub 2015 Aug 9 doi: 10.1007/s00247-015-3418-5. PMID: 26255159
Asymptomatic congenital lung malformations.
Laberge JM, Puligandla P, Flageole H
Semin Pediatr Surg 2005 Feb;14(1):16-33. doi: 10.1053/j.sempedsurg.2004.10.022. PMID: 15770585
The management of asymptomatic congenital lung malformations.
Laberge JM, Bratu I, Flageole H
Paediatr Respir Rev 2004;5 Suppl A:S305-12. doi: 10.1016/s1526-0542(04)90055-3. PMID: 14980288

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