U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Junctional ectopic tachycardia

MedGen UID:
21066
Concept ID:
C0039235
Disease or Syndrome
Synonym: His bundle tachycardia
SNOMED CT: His bundle tachycardia (233901002); Junctional ectopic tachycardia (251155001); His bundle (junctional ectopic) tachycardia (251155001)
Modes of inheritance:
Unknown inheritance
MedGen UID:
989040
Concept ID:
CN307042
Finding
Source: Orphanet
Hereditary clinical entity whose mode of inheritance is unknown.
 
HPO: HP:0011716
Monarch Initiative: MONDO:0017989
Orphanet: ORPHA3283

Definition

Junctional ectopic tachycardia (JET) is a unique type of supraventricular arrhythmia defined by narrow QRS complex and atrioventricular (AV) dissociation or retrograde atrial conduction in a 1:1 pattern. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVJunctional ectopic tachycardia

Conditions with this feature

Linear skin defects with multiple congenital anomalies 1
MedGen UID:
163210
Concept ID:
C0796070
Disease or Syndrome
Microphthalmia with linear skin defects (MLS) syndrome is characterized by unilateral or bilateral microphthalmia and/or anophthalmia and linear skin defects, usually involving the face and neck, which are present at birth and heal with age, leaving minimal residual scarring. Other findings can include a wide variety of other ocular abnormalities (e.g., corneal anomalies, orbital cysts, cataracts), central nervous system involvement (e.g., structural anomalies, developmental delay, infantile seizures), cardiac concerns (e.g., hypertrophic or oncocytic cardiomyopathy, atrial or ventricular septal defects, arrhythmias), short stature, diaphragmatic hernia, nail dystrophy, hearing impairment, and genitourinary malformations. Inter- and intrafamilial variability is described.

Professional guidelines

PubMed

Catton KG, Peterson JK
Crit Care Nurse 2020 Feb 1;40(1):46-55. doi: 10.4037/ccn2020793. PMID: 32006036
Page RL, Joglar JA, Caldwell MA, Calkins H, Conti JB, Deal BJ, Estes NA 3rd, Field ME, Goldberger ZD, Hammill SC, Indik JH, Lindsay BD, Olshansky B, Russo AM, Shen WK, Tracy CM, Al-Khatib SM; Evidence Review Committee Chair‡
Circulation 2016 Apr 5;133(14):e506-74. Epub 2015 Sep 23 doi: 10.1161/CIR.0000000000000311. PMID: 26399663
Page RL, Joglar JA, Caldwell MA, Calkins H, Conti JB, Deal BJ, Estes NA 3rd, Field ME, Goldberger ZD, Hammill SC, Indik JH, Lindsay BD, Olshansky B, Russo AM, Shen WK, Tracy CM, Al-Khatib SM; Evidence Review Committee Chair‡
Circulation 2016 Apr 5;133(14):e471-505. Epub 2015 Sep 23 doi: 10.1161/CIR.0000000000000310. PMID: 26399662

Recent clinical studies

Etiology

Izumi G, Takeda A, Yamazawa H, Kato N, Kato H, Tachibana T, Sagae O, Yahagi R, Maeno M, Hoshino K, Saito H
Heart Vessels 2022 Oct;37(10):1792-1800. Epub 2022 Apr 25 doi: 10.1007/s00380-022-02074-3. PMID: 35469049
Dumeny L, Chantra M, Langaee T, Duong BQ, Zambrano DH, Han F, Lopez-Colon D, Humma JF, Dacosta J, Lovato T, Mei C, Duarte JD, Johnson JA, Peek GJ, Jacobs JP, Bleiweis MS, Cavallari LH
Clin Transl Sci 2022 Mar;15(3):619-625. Epub 2021 Nov 5 doi: 10.1111/cts.13178. PMID: 34713976Free PMC Article
Catton KG, Peterson JK
Crit Care Nurse 2020 Feb 1;40(1):46-55. doi: 10.4037/ccn2020793. PMID: 32006036
Pierick AR, Law IH, Muldonado JR, VON Bergen NH
Pacing Clin Electrophysiol 2017 Jun;40(6):655-660. Epub 2017 Feb 14 doi: 10.1111/pace.13022. PMID: 28097671
Cools E, Missant C
Acta Anaesthesiol Belg 2014;65(1):1-8. PMID: 24988822

Diagnosis

Overman DM, Gram KL
Ann Thorac Surg 2024 Jun;117(6):1185-1186. Epub 2024 Apr 24 doi: 10.1016/j.athoracsur.2024.04.005. PMID: 38663659
Izumi G, Takeda A, Yamazawa H, Kato N, Kato H, Tachibana T, Sagae O, Yahagi R, Maeno M, Hoshino K, Saito H
Heart Vessels 2022 Oct;37(10):1792-1800. Epub 2022 Apr 25 doi: 10.1007/s00380-022-02074-3. PMID: 35469049
Demirci O, Tosun Ö, Bolat G
J Gynecol Obstet Hum Reprod 2022 Mar;51(3):102323. Epub 2022 Jan 19 doi: 10.1016/j.jogoh.2022.102323. PMID: 35063720
Catton KG, Peterson JK
Crit Care Nurse 2020 Feb 1;40(1):46-55. doi: 10.4037/ccn2020793. PMID: 32006036
Cools E, Missant C
Acta Anaesthesiol Belg 2014;65(1):1-8. PMID: 24988822

Therapy

Izumi G, Takeda A, Yamazawa H, Kato N, Kato H, Tachibana T, Sagae O, Yahagi R, Maeno M, Hoshino K, Saito H
Heart Vessels 2022 Oct;37(10):1792-1800. Epub 2022 Apr 25 doi: 10.1007/s00380-022-02074-3. PMID: 35469049
Katsura D, Tsuji S, Tokoro S, Hoshiyama T, Hoshino S, Furukawa O, Murakami T
BMC Pregnancy Childbirth 2022 Apr 11;22(1):311. doi: 10.1186/s12884-022-04655-6. PMID: 35410180Free PMC Article
Dumeny L, Chantra M, Langaee T, Duong BQ, Zambrano DH, Han F, Lopez-Colon D, Humma JF, Dacosta J, Lovato T, Mei C, Duarte JD, Johnson JA, Peek GJ, Jacobs JP, Bleiweis MS, Cavallari LH
Clin Transl Sci 2022 Mar;15(3):619-625. Epub 2021 Nov 5 doi: 10.1111/cts.13178. PMID: 34713976Free PMC Article
Catton KG, Peterson JK
Crit Care Nurse 2020 Feb 1;40(1):46-55. doi: 10.4037/ccn2020793. PMID: 32006036
Cools E, Missant C
Acta Anaesthesiol Belg 2014;65(1):1-8. PMID: 24988822

Prognosis

Hassan PF, El Haddad AM
Paediatr Anaesth 2024 May;34(5):459-466. Epub 2024 Jan 25 doi: 10.1111/pan.14848. PMID: 38269418
Dumeny L, Chantra M, Langaee T, Duong BQ, Zambrano DH, Han F, Lopez-Colon D, Humma JF, Dacosta J, Lovato T, Mei C, Duarte JD, Johnson JA, Peek GJ, Jacobs JP, Bleiweis MS, Cavallari LH
Clin Transl Sci 2022 Mar;15(3):619-625. Epub 2021 Nov 5 doi: 10.1111/cts.13178. PMID: 34713976Free PMC Article
Paluszek C, Brenner P, Pichlmaier M, Haas NA, Dalla-Pozza R, Hagl C, Hakami L
World J Pediatr Congenit Heart Surg 2019 Jan;10(1):50-57. doi: 10.1177/2150135118813124. PMID: 30799715
Ismail MF, Arafat AA, Hamouda TE, El Tantawy AE, Edrees A, Bogis A, Badawy N, Mahmoud AB, Elmahrouk AF, Jamjoom AA
J Cardiothorac Surg 2018 Jun 5;13(1):60. doi: 10.1186/s13019-018-0749-y. PMID: 29871684Free PMC Article
Haas NA, Plumpton K, Justo R, Jalali H, Pohlner P
Z Kardiol 2004 May;93(5):371-80. doi: 10.1007/s00392-004-0067-3. PMID: 15160272

Clinical prediction guides

Dasgupta S, Shalhoub K, El-Assaad I, O'Leary E, Feins EN, Triedman JK, Walsh EP, Kheir JN, Dionne A
Heart Rhythm 2023 Jul;20(7):1011-1017. Epub 2023 Mar 8 doi: 10.1016/j.hrthm.2023.03.005. PMID: 36898471
Izumi G, Takeda A, Yamazawa H, Kato N, Kato H, Tachibana T, Sagae O, Yahagi R, Maeno M, Hoshino K, Saito H
Heart Vessels 2022 Oct;37(10):1792-1800. Epub 2022 Apr 25 doi: 10.1007/s00380-022-02074-3. PMID: 35469049
Dumeny L, Chantra M, Langaee T, Duong BQ, Zambrano DH, Han F, Lopez-Colon D, Humma JF, Dacosta J, Lovato T, Mei C, Duarte JD, Johnson JA, Peek GJ, Jacobs JP, Bleiweis MS, Cavallari LH
Clin Transl Sci 2022 Mar;15(3):619-625. Epub 2021 Nov 5 doi: 10.1111/cts.13178. PMID: 34713976Free PMC Article
Zampi JD, Hirsch JC, Gurney JG, Donohue JE, Yu S, LaPage MJ, Hanauer DA, Charpie JR
Pediatr Cardiol 2012 Dec;33(8):1362-9. Epub 2012 May 15 doi: 10.1007/s00246-012-0348-y. PMID: 22585344
Calabrò MP, Cerrito M, Luzza F, Oreto G
Curr Pharm Des 2008;14(8):723-8. doi: 10.2174/138161208784007761. PMID: 18393870

Recent systematic reviews

Wang Q, Chen C, Wang L
J Pediatr (Rio J) 2022 Jan-Feb;98(1):15-25. Epub 2021 Jul 9 doi: 10.1016/j.jped.2021.05.008. PMID: 34252370Free PMC Article
Mendel B, Christianto C, Setiawan M, Prakoso R, Siagian SN
Curr Cardiol Rev 2022;18(1):e030621193817. doi: 10.2174/1573403X17666210603113430. PMID: 34082685Free PMC Article
Li X, Zhang C, Dai D, Liu H, Ge S
Congenit Heart Dis 2018 Sep;13(5):799-807. Epub 2018 Sep 27 doi: 10.1111/chd.12674. PMID: 30260073
Ghimire LV, Chou FS
Paediatr Anaesth 2018 Jul;28(7):597-606. Epub 2018 Jun 7 doi: 10.1111/pan.13405. PMID: 29882346
Liu Y, Bian W, Liu P, Zang X, Gu X, Chen W
Interact Cardiovasc Thorac Surg 2018 May 1;26(5):852-858. doi: 10.1093/icvts/ivy043. PMID: 29522148

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • PubMed
      See practice and clinical guidelines in PubMed. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.
    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...