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Adult central nervous system mixed germ cell tumor

MedGen UID:
231038
Concept ID:
C1332195
Neoplastic Process
Synonyms: Adult Central Nervous System Mixed Germ Cell Tumor; adult central nervous system mixed germ cell tumor; adult mixed germ cell tumor of central nervous system; adult mixed germ cell tumour of central nervous system; mixed germ cell tumor of central nervous system of adults; mixed germ cell tumour of central nervous system of adults
 
Monarch Initiative: MONDO:0004406

Definition

A mixed germ cell tumor of central nervous system that occurs in an adult. [from MONDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdult central nervous system mixed germ cell tumor

Professional guidelines

PubMed

Hundsberger T, Tonder M, Hottinger A, Brügge D, Roelcke U, Putora PM, Stupp R, Weller M
J Neurooncol 2014 Jun;118(2):321-328. Epub 2014 Apr 16 doi: 10.1007/s11060-014-1434-1. PMID: 24736829
Krieger MD, McComb JG
Childs Nerv Syst 2009 Oct;25(10):1269-73. Epub 2009 Apr 9 doi: 10.1007/s00381-009-0879-6. PMID: 19357854
Friedman JA, Lynch JJ, Buckner JC, Scheithauer BW, Raffel C
Neurosurgery 2001 Mar;48(3):518-22; discussion 522-3. doi: 10.1097/00006123-200103000-00011. PMID: 11270541

Recent clinical studies

Etiology

Wu PB, Filley AC, Miller ML, Bruce JN
Adv Exp Med Biol 2023;1405:31-71. doi: 10.1007/978-3-031-23705-8_2. PMID: 37452934
Abdel Razek AAK, Elsebaie NA, Zamora C, Castillo M
J Comput Assist Tomogr 2020 May/Jun;44(3):356-369. doi: 10.1097/RCT.0000000000001010. PMID: 32217897
Yu X, Liu R, Wang Y, Wang H, Zhao H, Wu Z
Clin Neurol Neurosurg 2012 Feb;114(2):112-9. Epub 2011 Oct 21 doi: 10.1016/j.clineuro.2011.09.010. PMID: 22018920
van den Bent MJ, Afra D, de Witte O, Ben Hassel M, Schraub S, Hoang-Xuan K, Malmström PO, Collette L, Piérart M, Mirimanoff R, Karim AB; EORTC Radiotherapy and Brain Tumor Groups and the UK Medical Research Council
Lancet 2005 Sep 17-23;366(9490):985-90. doi: 10.1016/S0140-6736(05)67070-5. PMID: 16168780
Burton EC, Prados MD
Curr Treat Options Oncol 2000 Dec;1(5):459-68. doi: 10.1007/s11864-000-0073-2. PMID: 12057153

Diagnosis

Wu PB, Filley AC, Miller ML, Bruce JN
Adv Exp Med Biol 2023;1405:31-71. doi: 10.1007/978-3-031-23705-8_2. PMID: 37452934
Viaene AN, Santi M, Hawkins C
Pediatr Dev Pathol 2022 Jan-Feb;25(1):46-58. Epub 2021 Apr 19 doi: 10.1177/10935266211009101. PMID: 33872106
Slegers RJ, Blumcke I
Acta Neuropathol Commun 2020 Mar 9;8(1):27. doi: 10.1186/s40478-020-00904-x. PMID: 32151273Free PMC Article
Chiaramonte C, Rabaste S, Jacquesson T, Meyronet D, Cotton F, Jouanneau E, Berhouma M
World Neurosurg 2018 Apr;112:18-24. Epub 2018 Jan 8 doi: 10.1016/j.wneu.2018.01.012. PMID: 29325939
Burton EC, Prados MD
Curr Treat Options Oncol 2000 Dec;1(5):459-68. doi: 10.1007/s11864-000-0073-2. PMID: 12057153

Therapy

Robertson PL, Jakacki R, Hukin J, Siffert J, Allen JC
J Neurooncol 2014 May;118(1):93-100. Epub 2014 Apr 4 doi: 10.1007/s11060-013-1306-0. PMID: 24700239
Legault G, Allen JC
Pediatr Blood Cancer 2013 Oct;60(10):1647-50. Epub 2013 Jun 20 doi: 10.1002/pbc.24620. PMID: 23788492
Krieger MD, McComb JG
Childs Nerv Syst 2009 Oct;25(10):1269-73. Epub 2009 Apr 9 doi: 10.1007/s00381-009-0879-6. PMID: 19357854
van den Bent MJ, Afra D, de Witte O, Ben Hassel M, Schraub S, Hoang-Xuan K, Malmström PO, Collette L, Piérart M, Mirimanoff R, Karim AB; EORTC Radiotherapy and Brain Tumor Groups and the UK Medical Research Council
Lancet 2005 Sep 17-23;366(9490):985-90. doi: 10.1016/S0140-6736(05)67070-5. PMID: 16168780
Burton EC, Prados MD
Curr Treat Options Oncol 2000 Dec;1(5):459-68. doi: 10.1007/s11864-000-0073-2. PMID: 12057153

Prognosis

Wu PB, Filley AC, Miller ML, Bruce JN
Adv Exp Med Biol 2023;1405:31-71. doi: 10.1007/978-3-031-23705-8_2. PMID: 37452934
Viaene AN, Santi M, Hawkins C
Pediatr Dev Pathol 2022 Jan-Feb;25(1):46-58. Epub 2021 Apr 19 doi: 10.1177/10935266211009101. PMID: 33872106
Zeiner PS, Preusse C, Golebiewska A, Zinke J, Iriondo A, Muller A, Kaoma T, Filipski K, Müller-Eschner M, Bernatz S, Blank AE, Baumgarten P, Ilina E, Grote A, Hansmann ML, Verhoff MA, Franz K, Feuerhake F, Steinbach JP, Wischhusen J, Stenzel W, Niclou SP, Harter PN, Mittelbronn M
Brain Pathol 2019 Jul;29(4):513-529. Epub 2019 Jan 15 doi: 10.1111/bpa.12690. PMID: 30506802Free PMC Article
Yu X, Liu R, Wang Y, Wang H, Zhao H, Wu Z
Clin Neurol Neurosurg 2012 Feb;114(2):112-9. Epub 2011 Oct 21 doi: 10.1016/j.clineuro.2011.09.010. PMID: 22018920
Burton EC, Prados MD
Curr Treat Options Oncol 2000 Dec;1(5):459-68. doi: 10.1007/s11864-000-0073-2. PMID: 12057153

Clinical prediction guides

Lampros MG, Vlachos N, Voulgaris S, Alexiou GA
Childs Nerv Syst 2021 Aug;37(8):2465-2474. Epub 2021 Jun 17 doi: 10.1007/s00381-021-05257-x. PMID: 34137942
Ho CY, Bornhorst M, Almira-Suarez MI, Donev K, Grafe M, Gordish-Dressman H, Rodriguez FJ
J Neuropathol Exp Neurol 2020 Jan 1;79(1):67-73. doi: 10.1093/jnen/nlz115. PMID: 31793986Free PMC Article
Graffeo CS, Perry A, Copeland WR 3rd, Giannini C, Neff BA, Driscoll CL, Link MJ
World Neurosurg 2017 Feb;98:632-643. Epub 2016 Nov 12 doi: 10.1016/j.wneu.2016.11.002. PMID: 27836701
Yu X, Liu R, Wang Y, Wang H, Zhao H, Wu Z
Clin Neurol Neurosurg 2012 Feb;114(2):112-9. Epub 2011 Oct 21 doi: 10.1016/j.clineuro.2011.09.010. PMID: 22018920
Thom M, Toma A, An S, Martinian L, Hadjivassiliou G, Ratilal B, Dean A, McEvoy A, Sisodiya SM, Brandner S
J Neuropathol Exp Neurol 2011 Oct;70(10):859-78. doi: 10.1097/NEN.0b013e3182302475. PMID: 21937911

Recent systematic reviews

Pascual JSG, Khu KJO, Starreveld YP
Neuropsychologia 2023 Jan 28;179:108450. Epub 2022 Dec 16 doi: 10.1016/j.neuropsychologia.2022.108450. PMID: 36529263
Lampros MG, Vlachos N, Voulgaris S, Alexiou GA
Childs Nerv Syst 2021 Aug;37(8):2465-2474. Epub 2021 Jun 17 doi: 10.1007/s00381-021-05257-x. PMID: 34137942
Graffeo CS, Perry A, Copeland WR 3rd, Giannini C, Neff BA, Driscoll CL, Link MJ
World Neurosurg 2017 Feb;98:632-643. Epub 2016 Nov 12 doi: 10.1016/j.wneu.2016.11.002. PMID: 27836701
Fouke SJ, Benzinger T, Gibson D, Ryken TC, Kalkanis SN, Olson JJ
J Neurooncol 2015 Dec;125(3):457-79. Epub 2015 Nov 3 doi: 10.1007/s11060-015-1908-9. PMID: 26530262
Englot DJ, Berger MS, Barbaro NM, Chang EF
J Neurosurg 2011 Aug;115(2):240-4. Epub 2011 Apr 29 doi: 10.3171/2011.3.JNS1153. PMID: 21529134

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