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Adult kidney Wilms tumor

MedGen UID:
231045
Concept ID:
C1332219
Neoplastic Process
Synonyms: Adenosarcoma of Adult Kidney; adenosarcoma of adult kidney; Adenosarcoma of the Adult Kidney; adenosarcoma of the adult kidney; Adult Kidney Adenosarcoma; adult kidney adenosarcoma; Adult Kidney Nephroblastoma; Adult Kidney Wilms Tumor; adult kidney Wilms tumor; adult nephroblastoma; Adult Renal Adenosarcoma; adult renal adenosarcoma; Adult Renal Wilms Tumor; adult renal Wilms tumor; Adult Renal Wilms' Tumor; adult renal Wilms' tumor; kidney Wilms tumor of adults
 
Monarch Initiative: MONDO:0024675

Definition

Wilms tumor of the kidney which occurs in adults. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAdult kidney Wilms tumor

Professional guidelines

PubMed

Segers H, van den Heuvel-Eibrink MM, Pritchard-Jones K, Coppes MJ, Aitchison M, Bergeron C, de Camargo B, Dome JS, Grundy P, Gatta G, Graf N, Grundy P, Kalapurakal JA, de Kraker J, Perlman EJ, Reinhard H, Spreafico F, Vujanic G, Warwick AB; SIOP-RTSG and the COG-Renal Tumour Committee
Expert Rev Anticancer Ther 2011 Jul;11(7):1105-13. doi: 10.1586/era.11.76. PMID: 21806333
Rao A, Rothman J, Nichols KE
Curr Opin Pediatr 2008 Feb;20(1):1-7. doi: 10.1097/MOP.0b013e3282f4249a. PMID: 18197032
Firoozi F, Kogan BA
Urol Clin North Am 2003 Nov;30(4):869-79. doi: 10.1016/s0094-0143(03)00052-1. PMID: 14680321

Recent clinical studies

Etiology

Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
González-Arboleda AA, Fernandez N, García-Perdomo HA
Curr Pediatr Rev 2022;18(3):166-178. doi: 10.2174/1573396318666220111143902. PMID: 35021978
Heck JE, He D, Janzen C, Federman N, Olsen J, Ritz B, Hansen J
Pediatr Blood Cancer 2019 Jan;66(1):e27461. Epub 2018 Sep 25 doi: 10.1002/pbc.27461. PMID: 30255546Free PMC Article
Sadowski CE, Lovric S, Ashraf S, Pabst WL, Gee HY, Kohl S, Engelmann S, Vega-Warner V, Fang H, Halbritter J, Somers MJ, Tan W, Shril S, Fessi I, Lifton RP, Bockenhauer D, El-Desoky S, Kari JA, Zenker M, Kemper MJ, Mueller D, Fathy HM, Soliman NA; SRNS Study Group, Hildebrandt F
J Am Soc Nephrol 2015 Jun;26(6):1279-89. Epub 2014 Oct 27 doi: 10.1681/ASN.2014050489. PMID: 25349199Free PMC Article
Castellino SM, Martinez-Borges AR, McLean TW
Curr Opin Oncol 2009 May;21(3):278-83. doi: 10.1097/CCO.0b013e328329f201. PMID: 19295433Free PMC Article

Diagnosis

Hol JA, Kuiper RP, van Dijk F, Waanders E, van Peer SE, Koudijs MJ, Bladergroen R, van Reijmersdal SV, Morgado LM, Bliek J, Lombardi MP, Hopman S, Drost J, de Krijger RR, van den Heuvel-Eibrink MM, Jongmans MCJ
J Clin Oncol 2022 Jun 10;40(17):1892-1902. Epub 2022 Mar 1 doi: 10.1200/JCO.21.02510. PMID: 35230882Free PMC Article
González-Arboleda AA, Fernandez N, García-Perdomo HA
Curr Pediatr Rev 2022;18(3):166-178. doi: 10.2174/1573396318666220111143902. PMID: 35021978
Calandrini C, Schutgens F, Oka R, Margaritis T, Candelli T, Mathijsen L, Ammerlaan C, van Ineveld RL, Derakhshan S, de Haan S, Dolman E, Lijnzaad P, Custers L, Begthel H, Kerstens HHD, Visser LL, Rookmaaker M, Verhaar M, Tytgat GAM, Kemmeren P, de Krijger RR, Al-Saadi R, Pritchard-Jones K, Kool M, Rios AC, van den Heuvel-Eibrink MM, Molenaar JJ, van Boxtel R, Holstege FCP, Clevers H, Drost J
Nat Commun 2020 Mar 11;11(1):1310. doi: 10.1038/s41467-020-15155-6. PMID: 32161258Free PMC Article
Spreafico F, Ferrari A, Mascarin M, Collini P, Morosi C, Biasoni D, Biassoni V, Schiavello E, Gandola L, Gattuso G, Chiaravalli S, Massimino M
Cancer Metastasis Rev 2019 Dec;38(4):683-694. doi: 10.1007/s10555-019-09831-3. PMID: 31797181
Castellino SM, Martinez-Borges AR, McLean TW
Curr Opin Oncol 2009 May;21(3):278-83. doi: 10.1097/CCO.0b013e328329f201. PMID: 19295433Free PMC Article

Therapy

González-Arboleda AA, Fernandez N, García-Perdomo HA
Curr Pediatr Rev 2022;18(3):166-178. doi: 10.2174/1573396318666220111143902. PMID: 35021978
Awal HB, Nandula SR, Domingues CC, Dore FJ, Kundu N, Brichacek B, Fakhri M, Elzarki A, Ahmadi N, Safai S, Fosso M, Amdur RL, Sen S
Cardiovasc Diabetol 2020 Jun 3;19(1):72. doi: 10.1186/s12933-020-01046-z. PMID: 32493344Free PMC Article
Spreafico F, Ferrari A, Mascarin M, Collini P, Morosi C, Biasoni D, Biassoni V, Schiavello E, Gandola L, Gattuso G, Chiaravalli S, Massimino M
Cancer Metastasis Rev 2019 Dec;38(4):683-694. doi: 10.1007/s10555-019-09831-3. PMID: 31797181
Chapuis AG, Egan DN, Bar M, Schmitt TM, McAfee MS, Paulson KG, Voillet V, Gottardo R, Ragnarsson GB, Bleakley M, Yeung CC, Muhlhauser P, Nguyen HN, Kropp LA, Castelli L, Wagener F, Hunter D, Lindberg M, Cohen K, Seese A, McElrath MJ, Duerkopp N, Gooley TA, Greenberg PD
Nat Med 2019 Jul;25(7):1064-1072. Epub 2019 Jun 24 doi: 10.1038/s41591-019-0472-9. PMID: 31235963Free PMC Article
Heck JE, He D, Janzen C, Federman N, Olsen J, Ritz B, Hansen J
Pediatr Blood Cancer 2019 Jan;66(1):e27461. Epub 2018 Sep 25 doi: 10.1002/pbc.27461. PMID: 30255546Free PMC Article

Prognosis

Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
Spreafico F, Ferrari A, Mascarin M, Collini P, Morosi C, Biasoni D, Biassoni V, Schiavello E, Gandola L, Gattuso G, Chiaravalli S, Massimino M
Cancer Metastasis Rev 2019 Dec;38(4):683-694. doi: 10.1007/s10555-019-09831-3. PMID: 31797181
Heck JE, He D, Janzen C, Federman N, Olsen J, Ritz B, Hansen J
Pediatr Blood Cancer 2019 Jan;66(1):e27461. Epub 2018 Sep 25 doi: 10.1002/pbc.27461. PMID: 30255546Free PMC Article
Sadowski CE, Lovric S, Ashraf S, Pabst WL, Gee HY, Kohl S, Engelmann S, Vega-Warner V, Fang H, Halbritter J, Somers MJ, Tan W, Shril S, Fessi I, Lifton RP, Bockenhauer D, El-Desoky S, Kari JA, Zenker M, Kemper MJ, Mueller D, Fathy HM, Soliman NA; SRNS Study Group, Hildebrandt F
J Am Soc Nephrol 2015 Jun;26(6):1279-89. Epub 2014 Oct 27 doi: 10.1681/ASN.2014050489. PMID: 25349199Free PMC Article
Ottaviani G, Jaffe N
Cancer Treat Res 2009;152:3-13. doi: 10.1007/978-1-4419-0284-9_1. PMID: 20213383

Clinical prediction guides

Foster KL, Salehabadi SM, Green DM, Xing M, Ness KK, Krull KR, Brinkman TM, Ehrhardt MJ, Chemaitilly W, Dixon SB, Bhakta N, Brennan RC, Krasin MJ, Davidoff AM, Robison LL, Hudson MM, Mulrooney DA
Pediatrics 2022 Nov 1;150(5) doi: 10.1542/peds.2022-056918. PMID: 36300342Free PMC Article
Higgs EF, Bao R, Hatogai K, Gajewski TF
J Immunother Cancer 2022 Jun;10(6) doi: 10.1136/jitc-2022-004797. PMID: 35705315Free PMC Article
Sherif S, Roelands J, Mifsud W, Ahmed EI, Raynaud CM, Rinchai D, Sathappan A, Maaz A, Saleh A, Ozer E, Fakhro KA, Mifsud B, Thorsson V, Bedognetti D, Hendrickx WRL
J Exp Clin Cancer Res 2022 Jun 11;41(1):199. doi: 10.1186/s13046-022-02397-z. PMID: 35690832Free PMC Article
Venkataramany AS, Schieffer KM, Lee K, Cottrell CE, Wang PY, Mardis ER, Cripe TP, Chandler DS
Ann Oncol 2022 Jun;33(6):578-592. Epub 2022 Mar 23 doi: 10.1016/j.annonc.2022.03.011. PMID: 35339647
Ying Y, Ma X, Fang J, Chen S, Wang W, Li J, Xie H, Wu J, Xie B, Liu B, Wang X, Zheng X, Xie L
Cell Death Dis 2021 Jul 29;12(8):750. doi: 10.1038/s41419-021-04038-3. PMID: 34326314Free PMC Article

Recent systematic reviews

Doganis D, Katsimpris A, Panagopoulou P, Bouka P, Bouka E, Moschovi M, Polychronopoulou S, Papakonstantinou E, Tragiannidis A, Katzilakis N, Dana H, Antoniadi K, Stefanaki K, Strantzia K, Dessypris N, Schüz J, Petridou ET
Cancer Epidemiol 2020 Aug;67:101769. Epub 2020 Jul 10 doi: 10.1016/j.canep.2020.101769. PMID: 32659726
Malek MM, Behr CA, Aldrink JH, Dasgupta R, Heaton TE, Gehred A, Lautz TB, Baertschiger RM, Christison-Lagay ER, Tracy ET, Rhee DS, Rodeberg D, Austin MT, Ehrlich PF
J Pediatr Surg 2020 Nov;55(11):2251-2259. Epub 2020 Mar 31 doi: 10.1016/j.jpedsurg.2020.03.019. PMID: 32386972
Gómez FM, Patel PA, Stuart S, Roebuck DJ
Pediatr Radiol 2014 Oct;44(10):1281-9. Epub 2014 May 13 doi: 10.1007/s00247-014-3001-5. PMID: 24821394

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