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Orbit embryonal rhabdomyosarcoma

MedGen UID:
233267
Concept ID:
C1335127
Neoplastic Process
Synonyms: Embryonal Rhabdomyosarcoma of Orbit; embryonal rhabdomyosarcoma of orbit; Embryonal Rhabdomyosarcoma of the Orbit; embryonal rhabdomyosarcoma of the orbit; Orbit Embryonal Rhabdomyosarcoma; orbit embryonal rhabdomyosarcoma
 
Monarch Initiative: MONDO:0002579

Definition

A malignant mesenchymal neoplasm that arises from the orbit. It is characterized by the presence of skeletal muscle tissue exhibiting embryonic features. [from NCI]

Professional guidelines

PubMed

Sobel RK, Ford JR, Dong W, Shriver E, Griepentrog GJ, Debnam JM, Esmaeli B
Am J Ophthalmol 2022 Feb;234:28-36. Epub 2021 Jul 17 doi: 10.1016/j.ajo.2021.06.035. PMID: 34280364
Darwish C, Shim T, Sparks AD, Chillakuru Y, Strum D, Benito DA, Monfared A
Int J Pediatr Otorhinolaryngol 2020 Dec;139:110403. Epub 2020 Sep 25 doi: 10.1016/j.ijporl.2020.110403. PMID: 33049553
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

Recent clinical studies

Etiology

Pontes FS, de Oliveira JI, de Souza LL, de Almeida OP, Fregnani ER, Vilela RS, Silva WM, Fonseca FP, Pontes HA
Med Oral Patol Oral Cir Bucal 2018 Mar 1;23(2):e188-e197. doi: 10.4317/medoral.22106. PMID: 29476676Free PMC Article
Reilly BK, Kim A, Peña MT, Dong TA, Rossi C, Murnick JG, Choi SS
Int J Pediatr Otorhinolaryngol 2015 Sep;79(9):1477-83. Epub 2015 Jul 3 doi: 10.1016/j.ijporl.2015.06.032. PMID: 26231745
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992
Crist WM, Anderson JR, Meza JL, Fryer C, Raney RB, Ruymann FB, Breneman J, Qualman SJ, Wiener E, Wharam M, Lobe T, Webber B, Maurer HM, Donaldson SS
J Clin Oncol 2001 Jun 15;19(12):3091-102. doi: 10.1200/JCO.2001.19.12.3091. PMID: 11408506
Ashton N, Morgan G
J Clin Pathol 1965 Nov;18(6):699-714. doi: 10.1136/jcp.18.6.699. PMID: 4284785Free PMC Article

Diagnosis

Barh A, Mukherjee B, Koka K, Krishnakumar S
Orbit 2020 Dec;39(6):418-421. Epub 2019 Nov 20 doi: 10.1080/01676830.2019.1692873. PMID: 31746248
Cortes Barrantes P, Jakobiec FA, Dryja TP
Semin Ophthalmol 2019;34(4):243-251. Epub 2019 May 30 doi: 10.1080/08820538.2019.1620802. PMID: 31146616
Pontes FS, de Oliveira JI, de Souza LL, de Almeida OP, Fregnani ER, Vilela RS, Silva WM, Fonseca FP, Pontes HA
Med Oral Patol Oral Cir Bucal 2018 Mar 1;23(2):e188-e197. doi: 10.4317/medoral.22106. PMID: 29476676Free PMC Article
Lee YC, Hsu YH, Yang SH, Huang TL
Ophthalmic Plast Reconstr Surg 2016 Sep-Oct;32(5):e104-6. doi: 10.1097/IOP.0000000000000290. PMID: 25216197
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992

Therapy

Indelicato DJ, Rotondo RL, Mailhot Vega RB, Uezono H, Bradfield S, Agarwal V, Hol ML, Bradley JA
Acta Oncol 2019 Oct;58(10):1404-1409. Epub 2019 Sep 18 doi: 10.1080/0284186X.2019.1627412. PMID: 31530120
Casey DL, Wexler LH, Wolden SL
Int J Radiat Oncol Biol Phys 2019 Apr 1;103(5):1151-1157. Epub 2018 Nov 30 doi: 10.1016/j.ijrobp.2018.11.049. PMID: 30508617Free PMC Article
Reilly BK, Kim A, Peña MT, Dong TA, Rossi C, Murnick JG, Choi SS
Int J Pediatr Otorhinolaryngol 2015 Sep;79(9):1477-83. Epub 2015 Jul 3 doi: 10.1016/j.ijporl.2015.06.032. PMID: 26231745
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992
Crist WM, Anderson JR, Meza JL, Fryer C, Raney RB, Ruymann FB, Breneman J, Qualman SJ, Wiener E, Wharam M, Lobe T, Webber B, Maurer HM, Donaldson SS
J Clin Oncol 2001 Jun 15;19(12):3091-102. doi: 10.1200/JCO.2001.19.12.3091. PMID: 11408506

Prognosis

Barh A, Mukherjee B, Koka K, Krishnakumar S
Orbit 2020 Dec;39(6):418-421. Epub 2019 Nov 20 doi: 10.1080/01676830.2019.1692873. PMID: 31746248
Cortes Barrantes P, Jakobiec FA, Dryja TP
Semin Ophthalmol 2019;34(4):243-251. Epub 2019 May 30 doi: 10.1080/08820538.2019.1620802. PMID: 31146616
Reilly BK, Kim A, Peña MT, Dong TA, Rossi C, Murnick JG, Choi SS
Int J Pediatr Otorhinolaryngol 2015 Sep;79(9):1477-83. Epub 2015 Jul 3 doi: 10.1016/j.ijporl.2015.06.032. PMID: 26231745
Karcioglu ZA, Hadjistilianou D, Rozans M, DeFrancesco S
Cancer Control 2004 Sep-Oct;11(5):328-33. doi: 10.1177/107327480401100507. PMID: 15377992
Crist WM, Anderson JR, Meza JL, Fryer C, Raney RB, Ruymann FB, Breneman J, Qualman SJ, Wiener E, Wharam M, Lobe T, Webber B, Maurer HM, Donaldson SS
J Clin Oncol 2001 Jun 15;19(12):3091-102. doi: 10.1200/JCO.2001.19.12.3091. PMID: 11408506

Clinical prediction guides

Zhao D, Zhou F, Liu W, Huang Z, Xu X, Zheng B, Liu C, Bai C, Liu J, Sun Y, Wang W, Xiao S
BMC Cancer 2024 Mar 14;24(1):340. doi: 10.1186/s12885-024-12079-y. PMID: 38486204Free PMC Article
Zeng J, Liu L, Li J, Huang Q, Pi L, Jin K
Dentomaxillofac Radiol 2021 Dec 1;50(8):20210030. Epub 2021 Apr 9 doi: 10.1259/dmfr.20210030. PMID: 33835837Free PMC Article
Indelicato DJ, Rotondo RL, Mailhot Vega RB, Uezono H, Bradfield S, Agarwal V, Hol ML, Bradley JA
Acta Oncol 2019 Oct;58(10):1404-1409. Epub 2019 Sep 18 doi: 10.1080/0284186X.2019.1627412. PMID: 31530120
Hicks J, Flaitz C
Oral Oncol 2002 Jul;38(5):450-9. doi: 10.1016/s1368-8375(01)00105-1. PMID: 12110339
Grosfeld JL
J Am Coll Surg 1999 Oct;189(4):407-25. doi: 10.1016/s1072-7515(99)00167-2. PMID: 10509467

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