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Childhood mediastinal neurogenic neoplasm

MedGen UID:
234134
Concept ID:
C1332981
Neoplastic Process
Synonyms: Childhood Mediastinal Neurogenic Neoplasm; childhood mediastinal neurogenic neoplasm; Childhood Mediastinal Neurogenic Tumor; childhood mediastinal neurogenic tumor; childhood mediastinal neurogenic tumour; Childhood Neurogenic Neoplasm of Mediastinum; childhood neurogenic neoplasm of mediastinum; Childhood Neurogenic Neoplasm of the Mediastinum; childhood neurogenic neoplasm of the mediastinum; Childhood Neurogenic Tumor of Mediastinum; childhood neurogenic tumor of mediastinum; Childhood Neurogenic Tumor of the Mediastinum; childhood neurogenic tumor of the mediastinum; childhood neurogenic tumour of mediastinum; childhood neurogenic tumour of the mediastinum; paediatric mediastinal neurogenic neoplasm; paediatric mediastinal neurogenic tumour; paediatric neurogenic neoplasm of mediastinum; paediatric neurogenic neoplasm of the mediastinum; paediatric neurogenic tumour of mediastinum; paediatric neurogenic tumour of the mediastinum; Pediatric Mediastinal Neurogenic Neoplasm; pediatric mediastinal neurogenic neoplasm; Pediatric Mediastinal Neurogenic Tumor; pediatric mediastinal neurogenic tumor; Pediatric Neurogenic Neoplasm of Mediastinum; pediatric neurogenic neoplasm of mediastinum; Pediatric Neurogenic Neoplasm of the Mediastinum; pediatric neurogenic neoplasm of the mediastinum; Pediatric Neurogenic Tumor of Mediastinum; pediatric neurogenic tumor of mediastinum; Pediatric Neurogenic Tumor of the Mediastinum; pediatric neurogenic tumor of the mediastinum
 
Monarch Initiative: MONDO:0003097

Definition

A peripheral nervous system neoplasm that arises in the mediastinum during childhood. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVChildhood mediastinal neurogenic neoplasm

Recent clinical studies

Etiology

Tansel T, Onursal E, Dayloğlu E, Başaran M, Sungur Z, Qamci E, Yilmazbayhan D, Eker R, Ertuğrul T
Turk J Pediatr 2006 Jan-Mar;48(1):8-12. PMID: 16562779
Lam JC, Chui CH, Jacobsen AS, Tan AM, Joseph VT
Pediatr Surg Int 2004 Mar;20(3):180-4. Epub 2004 Apr 3 doi: 10.1007/s00383-004-1142-6. PMID: 15064964
Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Bar-Ziv J, Nogrady MB
Am J Roentgenol Radium Ther Nucl Med 1975 Oct;125(2):380-90. doi: 10.2214/ajr.125.2.380. PMID: 1200237

Diagnosis

Lin PC, Lin SH, Chou SH, Chen YW, Chang TT, Wu JR, Jaw TS, Dai ZK, Chao MC
Kaohsiung J Med Sci 2010 Sep;26(9):496-501. doi: 10.1016/S1607-551X(10)70078-4. PMID: 20837347
Tansel T, Onursal E, Dayloğlu E, Başaran M, Sungur Z, Qamci E, Yilmazbayhan D, Eker R, Ertuğrul T
Turk J Pediatr 2006 Jan-Mar;48(1):8-12. PMID: 16562779
Lam JC, Chui CH, Jacobsen AS, Tan AM, Joseph VT
Pediatr Surg Int 2004 Mar;20(3):180-4. Epub 2004 Apr 3 doi: 10.1007/s00383-004-1142-6. PMID: 15064964
Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Bar-Ziv J, Nogrady MB
Am J Roentgenol Radium Ther Nucl Med 1975 Oct;125(2):380-90. doi: 10.2214/ajr.125.2.380. PMID: 1200237

Therapy

Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074

Prognosis

Saenz NC, Schnitzer JJ, Eraklis AE, Hendren WH, Grier HE, Macklis RM, Shamberger RC
J Pediatr Surg 1993 Feb;28(2):172-6. doi: 10.1016/s0022-3468(05)80268-4. PMID: 8437074
Bar-Ziv J, Nogrady MB
Am J Roentgenol Radium Ther Nucl Med 1975 Oct;125(2):380-90. doi: 10.2214/ajr.125.2.380. PMID: 1200237

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