U.S. flag

An official website of the United States government

Format

Send to:

Choose Destination

Cerebellar liponeurocytoma

MedGen UID:
237160
Concept ID:
C1370507
Neoplastic Process
Synonym: Lipomatous medulloblastoma (formerly)
SNOMED CT: Cerebellar liponeurocytoma (716592003); Liponeurocytoma of cerebellum (716592003); Cerebellar liponeurocytoma (734134003)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0006131
Orphanet: ORPHA251931

Definition

A rare slow growing neuronal tumor seen more frequently in females than males, occurring most commonly in the cerebellum but occasionally in the supratentorial compartment or the fourth ventricle and presenting in the 4th to 6th decade of life with symptoms of dizziness, headache and gait instability. It often has a high rate of local recurrence. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCerebellar liponeurocytoma
Follow this link to review classifications for Cerebellar liponeurocytoma in Orphanet.

Recent clinical studies

Etiology

Anghileri E, Eoli M, Paterra R, Ferroli P, Pollo B, Cuccarini V, Maderna E, Tringali G, Saini M, Salsano E, Finocchiaro G
J Neurooncol 2012 Jul;108(3):513-9. Epub 2012 Apr 3 doi: 10.1007/s11060-012-0853-0. PMID: 22476608
Pasquale G, Maria BA, Vania P, Gastone P, Nicola DL
Neurol India 2009 Mar-Apr;57(2):194-6. doi: 10.4103/0028-3886.51294. PMID: 19439854
Horstmann S, Perry A, Reifenberger G, Giangaspero F, Huang H, Hara A, Masuoka J, Rainov NG, Bergmann M, Heppner FL, Brandner S, Chimelli L, Montagna N, Jackson T, Davis DG, Markesbery WR, Ellison DW, Weller RO, Taddei GL, Conti R, Del Bigio MR, González-Cámpora R, Radhakrishnan VV, Söylemezoglu F, Uro-Coste E, Qian J, Kleihues P, Ohgaki H
Brain Pathol 2004 Jul;14(3):281-9. doi: 10.1111/j.1750-3639.2004.tb00065.x. PMID: 15446583Free PMC Article
Montagna N, Moreira D, Vaz LC, Reis M
Arq Neuropsiquiatr 2002 Sep;60(3-B):725-9. doi: 10.1590/s0004-282x2002000500008. PMID: 12364938
Jackson TR, Regine WF, Wilson D, Davis DG
J Neurosurg 2001 Oct;95(4):700-3. doi: 10.3171/jns.2001.95.4.0700. PMID: 11596966

Diagnosis

Hirono S, Gao Y, Matsutani T, Ikeda JI, Yokoo H, Iwadate Y
Brain Tumor Pathol 2021 Jul;38(3):257-262. Epub 2021 Jun 17 doi: 10.1007/s10014-021-00405-2. PMID: 34138409
Cai J, Li W, Du J, Xu N, Gao P, Zhou J, Li X
Medicine (Baltimore) 2018 Jan;97(2):e9556. doi: 10.1097/MD.0000000000009556. PMID: 29480846Free PMC Article
Xu L, Du J, Wang J, Fang J, Liu Z, He Y, Li G
Brain Tumor Pathol 2017 Jan;34(1):28-35. Epub 2017 Feb 24 doi: 10.1007/s10014-017-0279-7. PMID: 28236115
Nishimoto T, Kaya B
Arch Pathol Lab Med 2012 Aug;136(8):965-9. doi: 10.5858/arpa.2011-0337-RS. PMID: 22849747
Owler BK, Makeham JM, Shingde M, Besser M
J Clin Neurosci 2005 Apr;12(3):326-9. doi: 10.1016/j.jocn.2004.05.017. PMID: 15851097

Prognosis

Xu L, Du J, Wang J, Fang J, Liu Z, He Y, Li G
Brain Tumor Pathol 2017 Jan;34(1):28-35. Epub 2017 Feb 24 doi: 10.1007/s10014-017-0279-7. PMID: 28236115
Nishimoto T, Kaya B
Arch Pathol Lab Med 2012 Aug;136(8):965-9. doi: 10.5858/arpa.2011-0337-RS. PMID: 22849747
Owler BK, Makeham JM, Shingde M, Besser M
J Clin Neurosci 2005 Apr;12(3):326-9. doi: 10.1016/j.jocn.2004.05.017. PMID: 15851097
Aker FV, Ozkara S, Eren P, Peker O, Armağan S, Hakan T
J Neurooncol 2005 Jan;71(1):53-9. doi: 10.1007/s11060-004-9172-4. PMID: 15719276
George DH, Scheithauer BW
Am J Surg Pathol 2001 Dec;25(12):1551-5. doi: 10.1097/00000478-200112000-00013. PMID: 11717547

Clinical prediction guides

Alzoubi H, Gianno F, Abuelhaija Y, Najadat AA, Mustafa A, Al-Arman AY, Al-Arman LY, Banihani D, Mustafa A, Abualdahab N, Broggi G, Gaggero G, Piol N, Fiaschi P, Miele E, Giangaspero F
Clin Neuropathol 2022 Jan-Feb;41(1):12-17. doi: 10.5414/NP301415. PMID: 34672257
Horstmann S, Perry A, Reifenberger G, Giangaspero F, Huang H, Hara A, Masuoka J, Rainov NG, Bergmann M, Heppner FL, Brandner S, Chimelli L, Montagna N, Jackson T, Davis DG, Markesbery WR, Ellison DW, Weller RO, Taddei GL, Conti R, Del Bigio MR, González-Cámpora R, Radhakrishnan VV, Söylemezoglu F, Uro-Coste E, Qian J, Kleihues P, Ohgaki H
Brain Pathol 2004 Jul;14(3):281-9. doi: 10.1111/j.1750-3639.2004.tb00065.x. PMID: 15446583Free PMC Article
Cacciola F, Conti R, Taddei GL, Buccoliero AM, Di Lorenzo N
Acta Neurochir (Wien) 2002 Aug;144(8):829-33. doi: 10.1007/s007010200082. PMID: 12181694
Kleihues P, Louis DN, Scheithauer BW, Rorke LB, Reifenberger G, Burger PC, Cavenee WK
J Neuropathol Exp Neurol 2002 Mar;61(3):215-25; discussion 226-9. doi: 10.1093/jnen/61.3.215. PMID: 11895036
Taddei GL, Buccoliero AM, Caldarella A, Conti R, Di Lorenzo N, Cacciola F, Franchi A
Ultrastruct Pathol 2001 Jan-Feb;25(1):59-63. doi: 10.1080/019131201300004690. PMID: 11297321

Supplemental Content

Table of contents

    Clinical resources

    Practice guidelines

    • Bookshelf
      See practice and clinical guidelines in NCBI Bookshelf. The search results may include broader topics and may not capture all published guidelines. See the FAQ for details.

    Recent activity

    Your browsing activity is empty.

    Activity recording is turned off.

    Turn recording back on

    See more...