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Synovial chondromatosis

MedGen UID:
40275
Concept ID:
C0008476
Neoplastic Process
Synonyms: Chondromatoses, Synovial; Chondromatosis, Synovial; Chondrometaplasia, Synovial; Chondrometaplasias, Synovial; Henderson Jones Syndrome; Henderson-Jones Syndrome; Reichel Syndrome; Reichel's Syndrome; Reichels Syndrome; Syndrome, Henderson-Jones; Syndrome, Reichel's; Synovial Chondromatoses; Synovial Chondromatosis; Synovial Chondrometaplasia; Synovial Chondrometaplasias
SNOMED CT: Synovial chondromatosis (240207006)
 
Monarch Initiative: MONDO:0006438

Definition

An uncommon, benign cartilaginous neoplasm usually occurring in adults. The nodular tumor arises from the synovial membranes of joints. It is characterized by the presence of chondrocytes, nuclear pleomorphism, and hyaline cartilage differentiation. Clinical presentation may include joint pain, swelling, and limited range of motion. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSynovial chondromatosis

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