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Acinar Cystic Transformation of the Pancreas

MedGen UID:
459447
Concept ID:
C2987221
Neoplastic Process
Synonyms: Pancreatic Acinar Cell Cystadenoma; Pancreatic Acinar Cystic Transformation

Definition

A non-neoplastic cystic lesion of the pancreas lined by benign-appearing acinar and ductal epithelium. (WHO 2019) [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAcinar Cystic Transformation of the Pancreas

Recent clinical studies

Etiology

Aguilera Munoz L, Boros C, Bonvalet F, Ronot M, Rebours V
Pancreas 2023 Mar 1;52(3):e210-e212. doi: 10.1097/MPA.0000000000002233. PMID: 37716003
Zhang X, Zhu H, Yang X, Adsay VN, Jain D
Pathol Res Pract 2017 Aug;213(8):997-1001. Epub 2017 Apr 1 doi: 10.1016/j.prp.2017.03.013. PMID: 28599853
Wang G, Ji L, Qu FZ, Li L, Cao CL, Li ZB, Zhu H, Sun B
Pancreatology 2016 Jul-Aug;16(4):625-31. Epub 2016 Apr 7 doi: 10.1016/j.pan.2016.03.020. PMID: 27086062
Tanaka M, Shibahara J, Fukushima N, Shinozaki A, Umeda M, Ishikawa S, Kokudo N, Fukayama M
J Histochem Cytochem 2011 Oct;59(10):942-52. Epub 2011 Aug 10 doi: 10.1369/0022155411420569. PMID: 21832145Free PMC Article

Diagnosis

Mattiolo P, Wang H, Basturk O, Brosens LAA, Hong SM, Adsay V, Scarpa A, Luchini C
J Clin Pathol 2023 Nov;76(11):740-746. Epub 2023 Aug 29 doi: 10.1136/jcp-2023-209103. PMID: 37643836
Tatsumi M, Anazawa T, Masano Y, Yoh T, Nishino H, Yamane K, Nagai K, Uchida Y, Yoshizawa A, Hatano E
Clin J Gastroenterol 2023 Dec;16(6):919-924. Epub 2023 Jul 31 doi: 10.1007/s12328-023-01838-2. PMID: 37523124
Büyük M, Gündüz M, Berker N, Serin K, Çetin S, Özdemir H, Acunaş B, Güllüoğlu M
Int J Surg Pathol 2022 Sep;30(6):697-705. Epub 2022 Mar 3 doi: 10.1177/10668969221080070. PMID: 35238229
Rift CV, Hasselby JP, Hansen CP, Federspiel B
Pathol Res Pract 2020 Jun;216(6):152928. Epub 2020 Mar 17 doi: 10.1016/j.prp.2020.152928. PMID: 32204924
Leung PS
Adv Exp Med Biol 2010;690:29-51. doi: 10.1007/978-90-481-9060-7_3. PMID: 20700836Free PMC Article

Therapy

Hohwieler M, Illing A, Hermann PC, Mayer T, Stockmann M, Perkhofer L, Eiseler T, Antony JS, Müller M, Renz S, Kuo CC, Lin Q, Sendler M, Breunig M, Kleiderman SM, Lechel A, Zenker M, Leichsenring M, Rosendahl J, Zenke M, Sainz B Jr, Mayerle J, Costa IG, Seufferlein T, Kormann M, Wagner M, Liebau S, Kleger A
Gut 2017 Mar;66(3):473-486. Epub 2016 Sep 15 doi: 10.1136/gutjnl-2016-312423. PMID: 27633923Free PMC Article
Singhi AD, Norwood S, Liu TC, Sharma R, Wolfgang CL, Schulick RD, Zeh HJ, Hruban RH
Am J Surg Pathol 2013 Sep;37(9):1329-35. doi: 10.1097/PAS.0b013e3182a1ad72. PMID: 24076773

Prognosis

Chung WC, Challagundla L, Zhou Y, Li M, Atfi A, Xu K
Life Sci Alliance 2021 Feb;4(2) Epub 2020 Dec 2 doi: 10.26508/lsa.201900503. PMID: 33268505Free PMC Article
Yamaguchi J, Yokoyama Y, Kokuryo T, Ebata T, Nagino M
Surg Today 2018 Jan;48(1):9-17. Epub 2017 Mar 4 doi: 10.1007/s00595-017-1501-2. PMID: 28260136
Wang G, Ji L, Qu FZ, Li L, Cao CL, Li ZB, Zhu H, Sun B
Pancreatology 2016 Jul-Aug;16(4):625-31. Epub 2016 Apr 7 doi: 10.1016/j.pan.2016.03.020. PMID: 27086062
Kai K, Nakamura J, Ide T, Masuda M, Kitahara K, Miyoshi A, Noshiro H, Tokunaga O
Pathol Int 2012 Jul;62(7):485-90. Epub 2012 Mar 27 doi: 10.1111/j.1440-1827.2012.02814.x. PMID: 22726068
Klöppel G
Semin Diagn Pathol 2000 Feb;17(1):7-15. PMID: 10721803

Clinical prediction guides

Büyük M, Gündüz M, Berker N, Serin K, Çetin S, Özdemir H, Acunaş B, Güllüoğlu M
Int J Surg Pathol 2022 Sep;30(6):697-705. Epub 2022 Mar 3 doi: 10.1177/10668969221080070. PMID: 35238229
Lee JH, Jung SJ, Park YH, Park SJ, Choi JS
Korean J Gastroenterol 2021 Aug 25;78(2):138-143. doi: 10.4166/kjg.2021.044. PMID: 34446637
Rift CV, Hasselby JP, Hansen CP, Federspiel B
Pathol Res Pract 2020 Jun;216(6):152928. Epub 2020 Mar 17 doi: 10.1016/j.prp.2020.152928. PMID: 32204924
Singhi AD, Norwood S, Liu TC, Sharma R, Wolfgang CL, Schulick RD, Zeh HJ, Hruban RH
Am J Surg Pathol 2013 Sep;37(9):1329-35. doi: 10.1097/PAS.0b013e3182a1ad72. PMID: 24076773
Tanaka M, Shibahara J, Fukushima N, Shinozaki A, Umeda M, Ishikawa S, Kokudo N, Fukayama M
J Histochem Cytochem 2011 Oct;59(10):942-52. Epub 2011 Aug 10 doi: 10.1369/0022155411420569. PMID: 21832145Free PMC Article

Recent systematic reviews

Mattiolo P, Wang H, Basturk O, Brosens LAA, Hong SM, Adsay V, Scarpa A, Luchini C
J Clin Pathol 2023 Nov;76(11):740-746. Epub 2023 Aug 29 doi: 10.1136/jcp-2023-209103. PMID: 37643836

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