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Ampulla of Vater Gangliocytic Paraganglioma

MedGen UID:
474118
Concept ID:
C3272485
Neoplastic Process
Synonym: Gangliocytic Paraganglioma of the Ampullary Region

Definition

An extra-adrenal paraganglioma that arises from the ampulla of Vater and the periampullary region. It consists of a mixture of neuroendocrine cells, Schwann-like cells, and ganglion cells. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAmpulla of Vater Gangliocytic Paraganglioma

Recent clinical studies

Etiology

Sekine M, Miyatani H, Matsumoto K, Kashima H, Koito Y, Miura T, Takahashi Y, Tsuboi R, Ishii T, Fujiwara J, Uehara T, Urayoshi S, Yuhashi K, Asano T, Sagihara N, Matsumoto S, Mashima H
Intern Med 2018 Sep 15;57(18):2663-2668. Epub 2018 May 18 doi: 10.2169/internalmedicine.0464-17. PMID: 29780117Free PMC Article
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
J Am Coll Surg 2008 Aug;207(2):210-8. Epub 2008 May 5 doi: 10.1016/j.jamcollsurg.2008.01.028. PMID: 18656049
Akoglu S, Uçan ES, Celik G, Sener G, Sevinç C, Kilinç O, Itil O
Clin Exp Metastasis 2005;22(7):587-91. Epub 2006 Feb 11 doi: 10.1007/s10585-005-5787-x. PMID: 16475029
Sakhuja P, Malhotra V, Gondal R, Dutt N, Choudhary A
J Clin Gastroenterol 2001 Aug;33(2):154-6. doi: 10.1097/00004836-200108000-00013. PMID: 11468445
Altavilla G, Chiarelli S, Fassina A
Ultrastruct Pathol 2001 Mar-Apr;25(2):137-45. doi: 10.1080/019131201750222220. PMID: 11407527

Diagnosis

Choi H, Choi JW, Ryu DH, Park S, Kim MJ, Yoo KC, Woo CG
Medicine (Baltimore) 2022 Apr 15;101(15):e29138. doi: 10.1097/MD.0000000000029138. PMID: 35475800Free PMC Article
Sekine M, Miyatani H, Matsumoto K, Kashima H, Koito Y, Miura T, Takahashi Y, Tsuboi R, Ishii T, Fujiwara J, Uehara T, Urayoshi S, Yuhashi K, Asano T, Sagihara N, Matsumoto S, Mashima H
Intern Med 2018 Sep 15;57(18):2663-2668. Epub 2018 May 18 doi: 10.2169/internalmedicine.0464-17. PMID: 29780117Free PMC Article
Kwon J, Lee SE, Kang MJ, Jang JY, Kim SW
World J Surg Oncol 2010 May 24;8:42. doi: 10.1186/1477-7819-8-42. PMID: 20497533Free PMC Article
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
Arch Surg 2009 Jun;144(6):527-31. doi: 10.1001/archsurg.2009.80. PMID: 19528385
Sakhuja P, Malhotra V, Gondal R, Dutt N, Choudhary A
J Clin Gastroenterol 2001 Aug;33(2):154-6. doi: 10.1097/00004836-200108000-00013. PMID: 11468445

Therapy

Toh SK, Davies N, Dolan P, Worthley C, Townsend N, Williams JA
Aust N Z J Surg 1999 Mar;69(3):195-8. doi: 10.1046/j.1440-1622.1999.01521.x. PMID: 10075358

Prognosis

Sánchez Torrijos Y, León Montañés R, Mejías Manzano MÁ
Rev Esp Enferm Dig 2017 Aug;109(8):605-606. doi: 10.17235/reed.2017.4808/2016. PMID: 28715900
Rafiullah, Tanimu S, Onitilo AA
BMJ Case Rep 2014 Jul 2;2014 doi: 10.1136/bcr-2013-202941. PMID: 25100803Free PMC Article
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
Arch Surg 2009 Jun;144(6):527-31. doi: 10.1001/archsurg.2009.80. PMID: 19528385
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
J Am Coll Surg 2008 Aug;207(2):210-8. Epub 2008 May 5 doi: 10.1016/j.jamcollsurg.2008.01.028. PMID: 18656049
Witzigmann H, Loracher C, Geissler F, Wagner T, Tannapfel A, Uhlmann D, Caca K, Hauss J, Hehl JA
Langenbecks Arch Surg 2002 Jan;386(7):525-33. Epub 2001 Nov 6 doi: 10.1007/s00423-001-0260-z. PMID: 11819111

Clinical prediction guides

Sekine M, Miyatani H, Matsumoto K, Kashima H, Koito Y, Miura T, Takahashi Y, Tsuboi R, Ishii T, Fujiwara J, Uehara T, Urayoshi S, Yuhashi K, Asano T, Sagihara N, Matsumoto S, Mashima H
Intern Med 2018 Sep 15;57(18):2663-2668. Epub 2018 May 18 doi: 10.2169/internalmedicine.0464-17. PMID: 29780117Free PMC Article
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
Arch Surg 2009 Jun;144(6):527-31. doi: 10.1001/archsurg.2009.80. PMID: 19528385
Carter JT, Grenert JP, Rubenstein L, Stewart L, Way LW
J Am Coll Surg 2008 Aug;207(2):210-8. Epub 2008 May 5 doi: 10.1016/j.jamcollsurg.2008.01.028. PMID: 18656049
Büchler M, Malfertheiner P, Baczako K, Krautzberger W, Beger HG
Digestion 1985;31(1):54-9. doi: 10.1159/000199178. PMID: 2858422

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