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Abnormal coronary sinus morphology

MedGen UID:
488866
•Concept ID:
C0344680
•
Congenital Abnormality
Synonyms: Abnormality of the coronary sinus; Coronary sinus abnormality; CS - Coronary sinus abnormality
SNOMED CT: Coronary sinus abnormality (253323000); CS - Coronary sinus abnormality (253323000)
 
HPO: HP:0011642

Definition

An abnormality of the coronary sinus, which is formed by the union of the great cardiac vein and the left marginal vein and terminates in the right atrium. The coronary sinus functions to o collect deoxygenated blood from the myocardium of the heart and drain it into the right atrium. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAbnormal coronary sinus morphology

Professional guidelines

PubMed

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Coronary sinus diverticulum: Importance, function, and treatment.
Razeghian-Jahromi I, Natale A, Nikoo MH
Pacing Clin Electrophysiol 2020 Dec;43(12):1582-1587. Epub 2020 Sep 4 doi: 10.1111/pace.14026. PMID: 32815147
Primary-care management of patients with congenital anomalies of the coronary arteries.
Boris JR, Brothers JA
Cardiol Young 2015 Dec;25(8):1540-5. doi: 10.1017/S1047951115002127. PMID: 26675602

Recent clinical studies

Etiology

Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Coronary Artery Anomalies: When You Need to Worry.
Kochar A, Kiefer T
Curr Cardiol Rep 2017 May;19(5):39. doi: 10.1007/s11886-017-0854-x. PMID: 28374180
Clinical Features and Surgical Outcomes of Coronary Sinus Orifice Atresia.
Tadokoro N, Hoashi T, Kagisaki K, Shimada M, Kurosaki K, Shiraishi I, Ichikawa H
Pediatr Cardiol 2016 Feb;37(2):387-91. Epub 2015 Oct 26 doi: 10.1007/s00246-015-1288-0. PMID: 26499514
Coronary arterial development: a review of normal and congenitally anomalous patterns.
Lluri G, Aboulhosn J
Clin Cardiol 2014 Feb;37(2):126-30. Epub 2014 Jan 7 doi: 10.1002/clc.22237. PMID: 24399787Free PMC Article
Sudden cardiac death.
Virmani R, Burke AP, Farb A
Cardiovasc Pathol 2001 Sep-Oct;10(5):211-8. doi: 10.1016/s1054-8807(01)00091-6. PMID: 11673058

Diagnosis

Bicuspid aortic valve and anomalous right coronary artery from the opposite coronary sinus.
Giusti G, Villano M, Pozzi M
Cardiol Young 2022 Jun;32(6):1004-1006. Epub 2021 Oct 20 doi: 10.1017/S1047951121004273. PMID: 34666856
Coronary sinus diverticulum: Importance, function, and treatment.
Razeghian-Jahromi I, Natale A, Nikoo MH
Pacing Clin Electrophysiol 2020 Dec;43(12):1582-1587. Epub 2020 Sep 4 doi: 10.1111/pace.14026. PMID: 32815147
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Congenital coronary sinus stenosis.
Song G, Qiao W, Ren W, Chen Y, Zhou K
Echocardiography 2017 Jan;34(1):131-135. Epub 2016 Nov 2 doi: 10.1111/echo.13411. PMID: 27804165
Unroofing the diagnosis.
Cannavale G, Higgins CB, Ordovas KG
Int J Cardiovasc Imaging 2010 Dec;26(8):841-2. Epub 2010 Jul 8 doi: 10.1007/s10554-010-9667-3. PMID: 20614189

Therapy

Management and Anesthetic Considerations for Patients With Anomalous Aortic Origin of a Coronary Artery.
Kloesel B, Richtsfeld M, Konia M, Bass JL
Semin Cardiothorac Vasc Anesth 2018 Dec;22(4):383-394. Epub 2018 Aug 10 doi: 10.1177/1089253218793888. PMID: 30095030
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Assessing the coronary circulation in hypertension.
Strauer BE, Schwartzkopff B, Kelm M
J Hypertens 1998 Sep;16(9):1221-33. doi: 10.1097/00004872-199816090-00001. PMID: 9746107
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572
The toxic oil syndrome.
James TN
Clin Cardiol 1994 Sep;17(9):463-70. doi: 10.1002/clc.4960170902. PMID: 8001309

Prognosis

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Left superior vena cava: cross-sectional imaging overview.
Batouty NM, Sobh DM, Gadelhak B, Sobh HM, Mahmoud W, Tawfik AM
Radiol Med 2020 Mar;125(3):237-246. Epub 2019 Dec 10 doi: 10.1007/s11547-019-01114-9. PMID: 31823296
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572

Clinical prediction guides

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Anomalies of the Coronary Sinus and Its Tributaries: Evaluation on Multidetector Computed Tomography Angiography.
Sinha M, Pandey NN, Sharma A
J Thorac Imaging 2020 Mar;35(2):W60-W67. doi: 10.1097/RTI.0000000000000456. PMID: 31688460
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572

Recent systematic reviews

Surgical correction of anomalous origin of the right coronary artery from the left sinus of Valsalva: How, where, and when.
Belluschi I, Blasio A, Pozzoli A, Vicentini L, Alfieri O
Multimed Man Cardiothorac Surg 2019 Mar 5;2019 doi: 10.1510/mmcts.2019.005. PMID: 30990579

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