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Abnormal coronary sinus morphology

MedGen UID:
488866
•Concept ID:
C0344680
•
Congenital Abnormality
Synonyms: Abnormality of the coronary sinus; Coronary sinus abnormality; CS - Coronary sinus abnormality
SNOMED CT: Coronary sinus abnormality (253323000); CS - Coronary sinus abnormality (253323000)
 
HPO: HP:0011642

Definition

An abnormality of the coronary sinus, which is formed by the union of the great cardiac vein and the left marginal vein and terminates in the right atrium. The coronary sinus functions to o collect deoxygenated blood from the myocardium of the heart and drain it into the right atrium. [from HPO]

Professional guidelines

PubMed

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Coronary sinus diverticulum: Importance, function, and treatment.
Razeghian-Jahromi I, Natale A, Nikoo MH
Pacing Clin Electrophysiol 2020 Dec;43(12):1582-1587. Epub 2020 Sep 4 doi: 10.1111/pace.14026. PMID: 32815147
Primary-care management of patients with congenital anomalies of the coronary arteries.
Boris JR, Brothers JA
Cardiol Young 2015 Dec;25(8):1540-5. doi: 10.1017/S1047951115002127. PMID: 26675602

Recent clinical studies

Etiology

Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Introduction to anomalous aortic origin of a coronary artery.
Brothers JA
Congenit Heart Dis 2017 Sep;12(5):600-602. Epub 2017 Jun 27 doi: 10.1111/chd.12497. PMID: 28653465
Persistent Left Superior Vena Cava in Fetuses: An Autopsy Series.
Ramakrishnan D, Chidambarathanu S, Murli L, Micheal J, Jagadeesh S, Suresh I, Seshadri S
Fetal Pediatr Pathol 2017 Aug;36(4):304-310. Epub 2017 Jun 1 doi: 10.1080/15513815.2017.1324546. PMID: 28569558
Coronary Artery Anomalies: When You Need to Worry.
Kochar A, Kiefer T
Curr Cardiol Rep 2017 May;19(5):39. doi: 10.1007/s11886-017-0854-x. PMID: 28374180
Sudden cardiac death.
Virmani R, Burke AP, Farb A
Cardiovasc Pathol 2001 Sep-Oct;10(5):211-8. doi: 10.1016/s1054-8807(01)00091-6. PMID: 11673058

Diagnosis

The Sinus Venosus Veno-Venous Bridge: Not a septal defect.
Maddali MM, Anderson RH, Al Maskari SN, Al Kindi F, Al Kindi HN
Sultan Qaboos Univ Med J 2023 Dec;23(Spec Iss):5-9. Epub 2023 Nov 30 doi: 10.18295/squmj.12.2023.075. PMID: 38161764Free PMC Article
Bicuspid aortic valve and anomalous right coronary artery from the opposite coronary sinus.
Giusti G, Villano M, Pozzi M
Cardiol Young 2022 Jun;32(6):1004-1006. Epub 2021 Oct 20 doi: 10.1017/S1047951121004273. PMID: 34666856
Coronary sinus diverticulum: Importance, function, and treatment.
Razeghian-Jahromi I, Natale A, Nikoo MH
Pacing Clin Electrophysiol 2020 Dec;43(12):1582-1587. Epub 2020 Sep 4 doi: 10.1111/pace.14026. PMID: 32815147
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Persistent Left Superior Vena Cava in Fetuses: An Autopsy Series.
Ramakrishnan D, Chidambarathanu S, Murli L, Micheal J, Jagadeesh S, Suresh I, Seshadri S
Fetal Pediatr Pathol 2017 Aug;36(4):304-310. Epub 2017 Jun 1 doi: 10.1080/15513815.2017.1324546. PMID: 28569558

Therapy

Management and Anesthetic Considerations for Patients With Anomalous Aortic Origin of a Coronary Artery.
Kloesel B, Richtsfeld M, Konia M, Bass JL
Semin Cardiothorac Vasc Anesth 2018 Dec;22(4):383-394. Epub 2018 Aug 10 doi: 10.1177/1089253218793888. PMID: 30095030
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Anomalous aortic origin of coronary arteries from the opposite sinus: a critical appraisal of risk.
Peñalver JM, Mosca RS, Weitz D, Phoon CK
BMC Cardiovasc Disord 2012 Oct 1;12:83. doi: 10.1186/1471-2261-12-83. PMID: 23025810Free PMC Article
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572
The toxic oil syndrome.
James TN
Clin Cardiol 1994 Sep;17(9):463-70. doi: 10.1002/clc.4960170902. PMID: 8001309

Prognosis

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Left superior vena cava: cross-sectional imaging overview.
Batouty NM, Sobh DM, Gadelhak B, Sobh HM, Mahmoud W, Tawfik AM
Radiol Med 2020 Mar;125(3):237-246. Epub 2019 Dec 10 doi: 10.1007/s11547-019-01114-9. PMID: 31823296
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572

Clinical prediction guides

International consensus statement on nomenclature and classification of the congenital bicuspid aortic valve and its aortopathy, for clinical, surgical, interventional and research purposes.
Michelena HI, Della Corte A, Evangelista A, Maleszewski JJ, Edwards WD, Roman MJ, Devereux RB, Fernández B, Asch FM, Barker AJ, Sierra-Galan LM, De Kerchove L, Fernandes SM, Fedak PWM, Girdauskas E, Delgado V, Abbara S, Lansac E, Prakash SK, Bissell MM, Popescu BA, Hope MD, Sitges M, Thourani VH, Pibarot P, Chandrasekaran K, Lancellotti P, Borger MA, Forrest JK, Webb J, Milewicz DM, Makkar R, Leon MB, Sanders SP, Markl M, Ferrari VA, Roberts WC, Song JK, Blanke P, White CS, Siu S, Svensson LG, Braverman AC, Bavaria J, Sundt TM, El Khoury G, De Paulis R, Enriquez-Sarano M, Bax JJ, Otto CM, Schäfers HJ
J Thorac Cardiovasc Surg 2021 Sep;162(3):e383-e414. Epub 2021 Jul 22 doi: 10.1016/j.jtcvs.2021.06.019. PMID: 34304896
Anomalies of the Coronary Sinus and Its Tributaries: Evaluation on Multidetector Computed Tomography Angiography.
Sinha M, Pandey NN, Sharma A
J Thorac Imaging 2020 Mar;35(2):W60-W67. doi: 10.1097/RTI.0000000000000456. PMID: 31688460
Coronary venous anatomy and anomalies.
Sirajuddin A, Chen MY, White CS, Arai AE
J Cardiovasc Comput Tomogr 2020 Jan-Feb;14(1):80-86. Epub 2019 Aug 7 doi: 10.1016/j.jcct.2019.08.006. PMID: 31444098
Acquired and congenital coronary artery abnormalities.
Young ML, McLeary M, Chan KC
Cardiol Young 2017 Jan;27(S1):S31-S35. doi: 10.1017/S1047951116002201. PMID: 28084958
Development and validation of an ECG algorithm for identifying accessory pathway ablation site in Wolff-Parkinson-White syndrome.
Arruda MS, McClelland JH, Wang X, Beckman KJ, Widman LE, Gonzalez MD, Nakagawa H, Lazzara R, Jackman WM
J Cardiovasc Electrophysiol 1998 Jan;9(1):2-12. doi: 10.1111/j.1540-8167.1998.tb00861.x. PMID: 9475572

Recent systematic reviews

Surgical correction of anomalous origin of the right coronary artery from the left sinus of Valsalva: How, where, and when.
Belluschi I, Blasio A, Pozzoli A, Vicentini L, Alfieri O
Multimed Man Cardiothorac Surg 2019 Mar 5;2019 doi: 10.1510/mmcts.2019.005. PMID: 30990579

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