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Aorto-left ventricular tunnel

MedGen UID:
576719
Concept ID:
C0345054
Congenital Abnormality
Synonyms: Aortic Left Ventricular Tunnel; Aortic-Left Ventricular Tunnel; Aortic-Left Ventricular Tunnels; Aortico Left Ventricular Tunnel; Aortico-Left Ventricular Tunnel; Aortico-Left Ventricular Tunnels; Aorto Left Ventricular Tunnel; Aorto-Left Ventricular Tunnel; Aorto-Left Ventricular Tunnels; Ventricular Tunnel, Aortic-Left; Ventricular Tunnels, Aortic-Left
SNOMED CT: Aortic left ventricular tunnel (26201005); Aorta to left ventricle tunnel (26201005)
 
HPO: HP:0031932
Monarch Initiative: MONDO:0020411
Orphanet: ORPHA99071

Definition

Aorto-left ventricular tunnel (ALVT) is a congenital extracardiac channel connecting the ascending aorta above the sino-tubular junction to either left or right ventricular cavity. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVAorto-left ventricular tunnel
Follow this link to review classifications for Aorto-left ventricular tunnel in Orphanet.

Professional guidelines

PubMed

Weber EC, Recker F, Herberg U, Oberhoffer R, Kurkevych A, Axt-Fliedner R, Geipel A, Gembruch U, Berg C, Gottschalk I
Ultraschall Med 2023 Aug;44(4):e184-e190. Epub 2022 May 5 doi: 10.1055/a-1823-0821. PMID: 35512837
Wong AR, Amelia A, Mohd Zain MR, Sayuti KA
Med J Malaysia 2022 Jan;77(1):101-103. PMID: 35087005
Somerville J, English T, Ross DN
Br Heart J 1974 Apr;36(4):321-8. doi: 10.1136/hrt.36.4.321. PMID: 4276400Free PMC Article

Recent clinical studies

Etiology

Weber EC, Recker F, Herberg U, Oberhoffer R, Kurkevych A, Axt-Fliedner R, Geipel A, Gembruch U, Berg C, Gottschalk I
Ultraschall Med 2023 Aug;44(4):e184-e190. Epub 2022 May 5 doi: 10.1055/a-1823-0821. PMID: 35512837
van Nisselrooij AEL, Moon-Grady AJ, Wacker-Gussmann A, Tomek V, Malčić I, Grzyb A, Pavlova A, Kazamia K, Thakur V, Sinkovskaya E, Ten Harkel ADJ, Haak MC
Prenat Diagn 2022 Feb;42(2):267-277. Epub 2022 Jan 22 doi: 10.1002/pd.6090. PMID: 35018638Free PMC Article
Liang Y, Wang J, Li D, Wan L, Gao Y, Liu R, Li S, Wang H, Pang K
Eur J Cardiothorac Surg 2021 Jun 14;59(6):1312-1319. doi: 10.1093/ejcts/ezab110. PMID: 33759999
Diraneyya OM, Alhabshan F, Alghamdi A, Moafa H, Alnasef M, Kabbani MS
Cardiol Young 2021 Jan;31(1):47-51. Epub 2020 Oct 19 doi: 10.1017/S1047951120003273. PMID: 33070806
Xia H, Jiang Y, Xu Y, Tang J, Gao Y
Echocardiography 2015 Aug;32(8):1270-6. Epub 2015 Jan 2 doi: 10.1111/echo.12870. PMID: 25556394

Diagnosis

Weber EC, Recker F, Herberg U, Oberhoffer R, Kurkevych A, Axt-Fliedner R, Geipel A, Gembruch U, Berg C, Gottschalk I
Ultraschall Med 2023 Aug;44(4):e184-e190. Epub 2022 May 5 doi: 10.1055/a-1823-0821. PMID: 35512837
van Nisselrooij AEL, Moon-Grady AJ, Wacker-Gussmann A, Tomek V, Malčić I, Grzyb A, Pavlova A, Kazamia K, Thakur V, Sinkovskaya E, Ten Harkel ADJ, Haak MC
Prenat Diagn 2022 Feb;42(2):267-277. Epub 2022 Jan 22 doi: 10.1002/pd.6090. PMID: 35018638Free PMC Article
Chowdhury UK, Anderson RH, George N, Singh S, Sankhyan LK, Pradeep D, Chauhan A, Sengupta S, Vaswani P
World J Pediatr Congenit Heart Surg 2021 Jan;12(1):103-115. doi: 10.1177/2150135120954809. PMID: 33407031
Diraneyya OM, Alhabshan F, Alghamdi A, Moafa H, Alnasef M, Kabbani MS
Cardiol Young 2021 Jan;31(1):47-51. Epub 2020 Oct 19 doi: 10.1017/S1047951120003273. PMID: 33070806
Ma X, Li J, Zhang Q, Kong X, Yuan G, Wang Z, Zou C
J Cardiothorac Surg 2018 Jun 28;13(1):81. doi: 10.1186/s13019-018-0770-1. PMID: 29954427Free PMC Article

Therapy

Nakamura Y, Miyaji K, Yoshii T, Ootomo Y, Kimura S
Ann Thorac Surg 2016 May;101(5):1988-90. doi: 10.1016/j.athoracsur.2015.06.105. PMID: 27106439
Xia H, Jiang Y, Xu Y, Tang J, Gao Y
Echocardiography 2015 Aug;32(8):1270-6. Epub 2015 Jan 2 doi: 10.1111/echo.12870. PMID: 25556394

Prognosis

Weber EC, Recker F, Herberg U, Oberhoffer R, Kurkevych A, Axt-Fliedner R, Geipel A, Gembruch U, Berg C, Gottschalk I
Ultraschall Med 2023 Aug;44(4):e184-e190. Epub 2022 May 5 doi: 10.1055/a-1823-0821. PMID: 35512837
van Nisselrooij AEL, Moon-Grady AJ, Wacker-Gussmann A, Tomek V, Malčić I, Grzyb A, Pavlova A, Kazamia K, Thakur V, Sinkovskaya E, Ten Harkel ADJ, Haak MC
Prenat Diagn 2022 Feb;42(2):267-277. Epub 2022 Jan 22 doi: 10.1002/pd.6090. PMID: 35018638Free PMC Article
Djukic M, Djordjevic SA, Dähnert I
Cardiol Young 2017 Oct;27(8):1618-1621. Epub 2017 Apr 17 doi: 10.1017/S1047951117000701. PMID: 28414001
Xia H, Jiang Y, Xu Y, Tang J, Gao Y
Echocardiography 2015 Aug;32(8):1270-6. Epub 2015 Jan 2 doi: 10.1111/echo.12870. PMID: 25556394
Cook AC, Fagg NL, Ho SY, Groves AM, Sharland GK, Anderson RH, Allan LD
Br Heart J 1995 Oct;74(4):443-8. doi: 10.1136/hrt.74.4.443. PMID: 7488462Free PMC Article

Clinical prediction guides

Yang C, Yang J, Huang X, Wang J
Cardiovasc Ultrasound 2023 Apr 1;21(1):5. doi: 10.1186/s12947-023-00303-x. PMID: 37004030Free PMC Article
Weber EC, Recker F, Herberg U, Oberhoffer R, Kurkevych A, Axt-Fliedner R, Geipel A, Gembruch U, Berg C, Gottschalk I
Ultraschall Med 2023 Aug;44(4):e184-e190. Epub 2022 May 5 doi: 10.1055/a-1823-0821. PMID: 35512837
van Nisselrooij AEL, Moon-Grady AJ, Wacker-Gussmann A, Tomek V, Malčić I, Grzyb A, Pavlova A, Kazamia K, Thakur V, Sinkovskaya E, Ten Harkel ADJ, Haak MC
Prenat Diagn 2022 Feb;42(2):267-277. Epub 2022 Jan 22 doi: 10.1002/pd.6090. PMID: 35018638Free PMC Article
Cook AC, Fagg NL, Ho SY, Groves AM, Sharland GK, Anderson RH, Allan LD
Br Heart J 1995 Oct;74(4):443-8. doi: 10.1136/hrt.74.4.443. PMID: 7488462Free PMC Article

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