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Hair nevus

MedGen UID:
6707
•Concept ID:
C0018508
•
Neoplastic Process
Synonyms: Hair Nevus; hair nevus; Hairy Nevus; hairy nevus; Nevoid hypertrichosis; Nevoid Hypertrichosis; nevoid hypertrichosis
SNOMED CT: Hair nevus (201161009); Nevoid hypertrichosis (201161009)
 
Monarch Initiative: MONDO:0020980

Definition

A usually benign congenital skin growth that is often pigmented and sometimes develop coarse surface hair. There is a lifetime risk of transformation to malignant melanoma which varies depending on the size of the lesion. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVHair nevus

Professional guidelines

PubMed

Care of Congenital Melanocytic Nevi in Newborns and Infants: Review and Management Recommendations.
Jahnke MN, O'Haver J, Gupta D, Hawryluk EB, Finelt N, Kruse L, Jen M, Horii KA, Frieden IJ, Price H, Coughlin CC
Pediatrics 2021 Dec 1;148(6) doi: 10.1542/peds.2021-051536. PMID: 34845496
Characteristics and management of Asian skin.
Chan IL, Cohen S, da Cunha MG, Maluf LC
Int J Dermatol 2019 Feb;58(2):131-143. Epub 2018 Jul 24 doi: 10.1111/ijd.14153. PMID: 30039861
Laser treatment of periocular skin conditions.
Yates B, Que SK, D'Souza L, Suchecki J, Finch JJ
Clin Dermatol 2015 Mar-Apr;33(2):197-206. doi: 10.1016/j.clindermatol.2014.10.011. PMID: 25704939

Recent clinical studies

Etiology

Alopecia in genetic diseases.
Calvieri S, Rossi A
G Ital Dermatol Venereol 2014 Feb;149(1):1-13. PMID: 24566562
The group of epidermal nevus syndromes Part I. Well defined phenotypes.
Happle R
J Am Acad Dermatol 2010 Jul;63(1):1-22; quiz 23-4. doi: 10.1016/j.jaad.2010.01.017. PMID: 20542174
Giant congenital nevi: a 20-year experience and an algorithm for their management.
Gosain AK, Santoro TD, Larson DL, Gingrass RP
Plast Reconstr Surg 2001 Sep 1;108(3):622-36. doi: 10.1097/00006534-200109010-00004. PMID: 11698832

Diagnosis

Isolated straight hair nevus in a White child.
Rault L, Morice-Picard F, Svahn I, Gontier E, Eyraud A, Taïeb A
Pediatr Dermatol 2019 Mar;36(2):260-261. Epub 2019 Feb 21 doi: 10.1111/pde.13740. PMID: 30791146
Wooly hair nevus, Post's Type 2.
Kamat D, Sendhil Kumaran M
Int J Dermatol 2019 Oct;58(10):1197-1198. Epub 2019 Jan 29 doi: 10.1111/ijd.14380. PMID: 30697702
Phylloid terminal hair nevus: A unique clinical entity.
Kittler NW, Antonov NK, Scripps TB, Anyane-Yeboa K, Garzon MC, Lauren CT
Pediatr Dermatol 2018 Nov;35(6):e404-e405. Epub 2018 Aug 28 doi: 10.1111/pde.13616. PMID: 30152562
Hair follicle nevus.
Komura A, Tani M
Dermatology 1992;185(2):154-5. doi: 10.1159/000247435. PMID: 1421631
Circumscribed pilary dysembryoplasia of the palms.
Camacho F, Cámpora RG
Dermatologica 1991;182(1):63-4. doi: 10.1159/000247741. PMID: 2013359

Therapy

Topical everolimus therapy for epidermal nevi associated with woolly hair nevus in a patient with a mosaic HRAS mutation.
Singh A, Gorell ES, Lucky AW
Pediatr Dermatol 2024 Sep-Oct;41(5):871-873. Epub 2024 Apr 1 doi: 10.1111/pde.15605. PMID: 38558293

Clinical prediction guides

Woolly hair nevus caused by somatic mutation and Costello syndrome caused by germline mutation in HRAS: Consider parental mosaicism in prenatal counseling.
Liang J, Guo Y, Lu Z, Yu H, Wu L, Yao Z
J Dermatol 2022 Jan;49(1):161-164. Epub 2021 Oct 2 doi: 10.1111/1346-8138.16177. PMID: 34601768

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