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Microgastria

MedGen UID:
82732
•Concept ID:
C0266150
•
Congenital Abnormality
Synonyms: Congenital gastric hypoplasia; Congenital microgastria; congenital microgastria; Congenital small stomach
SNOMED CT: Microgastria (83714006); Congenital microgastria (83714006); Congenital gastric hypoplasia (83714006); Congenital small stomach (83714006)
 
HPO: HP:0100841
Monarch Initiative: MONDO:0016041
Orphanet: ORPHA199293

Definition

A developmental anomaly with a small tubular or saccular midline stomach. [from HPO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMicrogastria
Follow this link to review classifications for Microgastria in Orphanet.

Professional guidelines

PubMed

Treatment of Congenital Microgastria.
Ruczynski LIA, Botden SMBI, Daniels-Scharbatke HE, Schurink M, de Blaauw I
Eur J Pediatr Surg 2021 Apr;31(2):129-134. Epub 2020 May 18 doi: 10.1055/s-0040-1710027. PMID: 32422678
Prenatal diagnosis of laryngotracheoesophageal clefts.
Samuel M, Burge DM, Griffiths DM
Fetal Diagn Ther 1997 Sep-Oct;12(5):260-5. doi: 10.1159/000264481. PMID: 9430204

Recent clinical studies

Etiology

Follow-up study of three cases of congenital microgastria.
Ugolini S, Oreglio C, Walsh KC, Morabito A
Pediatr Med Chir 2023 Dec 15;45(2) doi: 10.4081/pmc.2023.326. PMID: 38112623
Risk factors of dumping syndrome after fundoplication for gastroesophageal reflux in children.
Yamoto M, Fukumoto K, Takahashi T, Miyake H, Nakaya K, Nomura A, Sekioka A, Yamada Y, Urushihara N
Pediatr Surg Int 2021 Feb;37(2):183-189. Epub 2021 Jan 3 doi: 10.1007/s00383-020-04783-0. PMID: 33388966
Treatment of Congenital Microgastria.
Ruczynski LIA, Botden SMBI, Daniels-Scharbatke HE, Schurink M, de Blaauw I
Eur J Pediatr Surg 2021 Apr;31(2):129-134. Epub 2020 May 18 doi: 10.1055/s-0040-1710027. PMID: 32422678
Surgical Management of Hiatal Hernia in Children with Asplenia Syndrome.
Miyake H, Fukumoto K, Yamoto M, Nouso H, Kaneshiro M, Koyama M, Urushihara N
Eur J Pediatr Surg 2017 Jun;27(3):274-279. Epub 2016 Sep 8 doi: 10.1055/s-0036-1592135. PMID: 27606905
Management of congenital microgastria.
Velasco AL, Holcomb GW 3rd, Templeton JM Jr, Ziegler MM
J Pediatr Surg 1990 Feb;25(2):192-7. doi: 10.1016/0022-3468(90)90401-t. PMID: 2303988

Diagnosis

Gastric dissociation for the treatment of congenital microgastria with paraesophageal hiatal hernia.
Kunisaki SM, Dakhoub A, Jarboe MD, Geiger JD
J Pediatr Surg 2011 Jun;46(6):e1-4. doi: 10.1016/j.jpedsurg.2011.02.048. PMID: 21683183
An eighteen year follow-up after surgery for congenital microgastria--case report and review of literature.
Jones VS, Cohen RC
J Pediatr Surg 2007 Nov;42(11):1957-60. doi: 10.1016/j.jpedsurg.2007.07.054. PMID: 18022457
Holoprosencephaly and limb reduction defects: a consideration of Steinfeld syndrome and related conditions.
Siebert JR, Schoenecker KA, Resta RG, Kapur RP
Am J Med Genet A 2005 May 1;134(4):381-92. doi: 10.1002/ajmg.a.30648. PMID: 15779021
Congenital microgastria: a case report and review of literature.
Kroes EJ, Festen C
Pediatr Surg Int 1998 Jul;13(5-6):416-8. doi: 10.1007/s003830050353. PMID: 9639631
Congenital microgastria.
Hoehner JC, Kimura K, Soper RT
J Pediatr Surg 1994 Dec;29(12):1591-3. doi: 10.1016/0022-3468(94)90228-3. PMID: 7877040

Therapy

Risk factors of dumping syndrome after fundoplication for gastroesophageal reflux in children.
Yamoto M, Fukumoto K, Takahashi T, Miyake H, Nakaya K, Nomura A, Sekioka A, Yamada Y, Urushihara N
Pediatr Surg Int 2021 Feb;37(2):183-189. Epub 2021 Jan 3 doi: 10.1007/s00383-020-04783-0. PMID: 33388966
Dumping syndrome after esophageal atresia repair without antireflux surgery.
Michaud L, Sfeir R, Couttenier F, Turck D, Gottrand F
J Pediatr Surg 2010 Apr;45(4):E13-5. doi: 10.1016/j.jpedsurg.2010.01.016. PMID: 20385264
Management and long-term follow-up of patients with types III and IV laryngotracheoesophageal clefts.
Kawaguchi AL, Donahoe PK, Ryan DP
J Pediatr Surg 2005 Jan;40(1):158-64; discussion 164-5. doi: 10.1016/j.jpedsurg.2004.09.041. PMID: 15868578
Congenital microgastria: treatment with transient jejunal feedings.
Murray KF, Lillehei CW, Duggan C
J Pediatr Gastroenterol Nutr 1999 Mar;28(3):343-5. doi: 10.1097/00005176-199903000-00028. PMID: 10067744
Retrograde percutaneous gastrostomy and gastrojejunostomy in 505 children: a 4 1/2-year experience.
Chait PG, Weinberg J, Connolly BL, Pencharz P, Richards H, Clift JE, Savoie S, Harrison D
Radiology 1996 Dec;201(3):691-5. doi: 10.1148/radiology.201.3.8939217. PMID: 8939217

Prognosis

Follow-up study of three cases of congenital microgastria.
Ugolini S, Oreglio C, Walsh KC, Morabito A
Pediatr Med Chir 2023 Dec 15;45(2) doi: 10.4081/pmc.2023.326. PMID: 38112623
Surgical Management of Hiatal Hernia in Children with Asplenia Syndrome.
Miyake H, Fukumoto K, Yamoto M, Nouso H, Kaneshiro M, Koyama M, Urushihara N
Eur J Pediatr Surg 2017 Jun;27(3):274-279. Epub 2016 Sep 8 doi: 10.1055/s-0036-1592135. PMID: 27606905
Congenital microgastria: a case report and review of literature.
Kroes EJ, Festen C
Pediatr Surg Int 1998 Jul;13(5-6):416-8. doi: 10.1007/s003830050353. PMID: 9639631
Congenital microgastria.
Hoehner JC, Kimura K, Soper RT
J Pediatr Surg 1994 Dec;29(12):1591-3. doi: 10.1016/0022-3468(94)90228-3. PMID: 7877040
Management of congenital microgastria.
Velasco AL, Holcomb GW 3rd, Templeton JM Jr, Ziegler MM
J Pediatr Surg 1990 Feb;25(2):192-7. doi: 10.1016/0022-3468(90)90401-t. PMID: 2303988

Clinical prediction guides

Value of Biochemical Amniotic Fluid Analysis and Fetal Magnetic Resonance Imaging in the Prenatal Diagnosis of Congenital Microgastria.
Lepee A, Massardier J, Atallah A, Massoud M, Pettazzoni M, Huissoud C, Dubois R, Guibaud L, Cabet S
Fetal Diagn Ther 2024;51(5):486-492. Epub 2024 Jun 24 doi: 10.1159/000539888. PMID: 38934150
Congenital microgastria and primary ciliary dyskinesia in a newborn with DiGeorge syndrome and 22q11.2 deletion.
Filippi L, Serafini L, Fiorini P, Agostini E, Giovannucci Uzielli ML
Eur J Pediatr Surg 2008 Jun;18(3):195-7. doi: 10.1055/s-2008-1038503. PMID: 18493898
Laryngotracheoesophageal cleft (type IV): management and repair of lesions beyond the carina.
Ryan DP, Muehrcke DD, Doody DP, Kim SH, Donahoe PK
J Pediatr Surg 1991 Aug;26(8):962-9; discussion 969-70. doi: 10.1016/0022-3468(91)90844-j. PMID: 1919990
Congenital microgastria. A follow-up observation over six years.
Hochberger O, Swoboda W
Pediatr Radiol 1974;2(3):207-8. doi: 10.1007/BF00972735. PMID: 4153736

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