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Cogan syndrome

MedGen UID:
82871
Concept ID:
C0271270
Disease or Syndrome
Synonym: Cogan's syndrome
SNOMED CT: Cogan's syndrome (405810005); Oculovestibuloauditory syndrome (405810005); Cogan syndrome (405810005)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
Monarch Initiative: MONDO:0015453
Orphanet: ORPHA1467

Definition

A rare inflammatory/autoimmune disorder of unknown origin characterized by interstitial keratitis (IK) and audiovestibular dysfunctions. [from ORDO]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVCogan syndrome

Professional guidelines

PubMed

Durtette C, Hachulla E, Resche-Rigon M, Papo T, Zénone T, Lioger B, Deligny C, Lambert M, Landron C, Pouchot J, Kahn JE, Lavigne C, De Wazieres B, Dhote R, Gondran G, Pertuiset E, Quemeneur T, Hamidou M, Sève P, Le Gallou T, Grasland A, Hatron PY, Fain O, Mekinian A; SNFMI and CRI
Autoimmun Rev 2017 Dec;16(12):1219-1223. Epub 2017 Oct 14 doi: 10.1016/j.autrev.2017.10.005. PMID: 29037902
Kessel A, Vadasz Z, Toubi E
Autoimmun Rev 2014 Apr-May;13(4-5):351-4. Epub 2014 Jan 10 doi: 10.1016/j.autrev.2014.01.002. PMID: 24418297
Unizony S, Stone JH, Stone JR
Curr Opin Rheumatol 2013 Jan;25(1):3-9. doi: 10.1097/BOR.0b013e32835b133a. PMID: 23114585

Recent clinical studies

Etiology

Ferfar Y, Morinet S, Espitia O, Agard C, Vautier M, Comarmond C, Desbois AC, Domont F, Resche-Rigon M, Cacoub P, Biard L, Saadoun D; French Study Group for Large Vessel Vasculitis (GEFA)
J Rheumatol 2021 Oct;48(10):1583-1588. Epub 2021 Jul 1 doi: 10.3899/jrheum.201274. PMID: 34210830
Durtette C, Hachulla E, Resche-Rigon M, Papo T, Zénone T, Lioger B, Deligny C, Lambert M, Landron C, Pouchot J, Kahn JE, Lavigne C, De Wazieres B, Dhote R, Gondran G, Pertuiset E, Quemeneur T, Hamidou M, Sève P, Le Gallou T, Grasland A, Hatron PY, Fain O, Mekinian A; SNFMI and CRI
Autoimmun Rev 2017 Dec;16(12):1219-1223. Epub 2017 Oct 14 doi: 10.1016/j.autrev.2017.10.005. PMID: 29037902
Mora P, Calzetti G, Ghirardini S, Rubino P, Gandolfi S, Orsoni J
Autoimmun Rev 2017 Apr;16(4):385-390. Epub 2017 Feb 14 doi: 10.1016/j.autrev.2017.02.009. PMID: 28232169
Pagnini I, Zannin ME, Vittadello F, Sari M, Simonini G, Cimaz R, Zulian F
J Pediatr 2012 Feb;160(2):303-307.e1. Epub 2011 Sep 13 doi: 10.1016/j.jpeds.2011.07.051. PMID: 21920537
Pasanisi E, Vincenti V, Bacciu A, Guida M, Berghenti T, Barbot A, Orsoni JG, Bacciu S
Otol Neurotol 2003 Jul;24(4):601-4. doi: 10.1097/00129492-200307000-00012. PMID: 12851552

Diagnosis

Ishiyama G
Continuum (Minneap Minn) 2021 Apr 1;27(2):468-490. doi: 10.1212/CON.0000000000000977. PMID: 34351115
Espinoza GM, Wheeler J, Temprano KK, Keller AP
Curr Allergy Asthma Rep 2020 Jun 16;20(9):46. doi: 10.1007/s11882-020-00945-1. PMID: 32548646
Iliescu DA, Timaru CM, Batras M, De Simone A, Stefan C
Rom J Ophthalmol 2015 Jan-Mar;59(1):6-13. PMID: 27373108Free PMC Article
Singer O
Rheum Dis Clin North Am 2015;41(1):75-91, viii. doi: 10.1016/j.rdc.2014.09.007. PMID: 25399941
Toubi E
Isr Med Assoc J 2014 May;16(5):311-2. PMID: 24979838

Therapy

Durtette C, Hachulla E, Resche-Rigon M, Papo T, Zénone T, Lioger B, Deligny C, Lambert M, Landron C, Pouchot J, Kahn JE, Lavigne C, De Wazieres B, Dhote R, Gondran G, Pertuiset E, Quemeneur T, Hamidou M, Sève P, Le Gallou T, Grasland A, Hatron PY, Fain O, Mekinian A; SNFMI and CRI
Autoimmun Rev 2017 Dec;16(12):1219-1223. Epub 2017 Oct 14 doi: 10.1016/j.autrev.2017.10.005. PMID: 29037902
Iliescu DA, Timaru CM, Batras M, De Simone A, Stefan C
Rom J Ophthalmol 2015 Jan-Mar;59(1):6-13. PMID: 27373108Free PMC Article
Espinoza GM, Prost A
Curr Rheumatol Rep 2015 Apr;17(4):24. doi: 10.1007/s11926-015-0499-y. PMID: 25854487
Singer O
Rheum Dis Clin North Am 2015;41(1):75-91, viii. doi: 10.1016/j.rdc.2014.09.007. PMID: 25399941
Orsoni JG, Zavota L, Pellistri I, Piazza F, Cimino L
Cornea 2002 May;21(4):356-9. doi: 10.1097/00003226-200205000-00005. PMID: 11973382

Prognosis

Boumghit Y, Boucher S, Godey B, Michel G, Bakhos D
Eur Ann Otorhinolaryngol Head Neck Dis 2023 Sep;140(5):235-238. Epub 2023 Jul 19 doi: 10.1016/j.anorl.2023.06.005. PMID: 37479606
Gauthier AS, Noureddine S, Delbosc B
J Fr Ophtalmol 2019 Jun;42(6):e229-e237. Epub 2019 May 15 doi: 10.1016/j.jfo.2019.04.001. PMID: 31103357
Durtette C, Hachulla E, Resche-Rigon M, Papo T, Zénone T, Lioger B, Deligny C, Lambert M, Landron C, Pouchot J, Kahn JE, Lavigne C, De Wazieres B, Dhote R, Gondran G, Pertuiset E, Quemeneur T, Hamidou M, Sève P, Le Gallou T, Grasland A, Hatron PY, Fain O, Mekinian A; SNFMI and CRI
Autoimmun Rev 2017 Dec;16(12):1219-1223. Epub 2017 Oct 14 doi: 10.1016/j.autrev.2017.10.005. PMID: 29037902
Vodopivec I, Lobo AM, Prasad S
Semin Neurol 2014 Sep;34(4):444-57. Epub 2014 Nov 4 doi: 10.1055/s-0034-1390393. PMID: 25369440
Kessel A, Vadasz Z, Toubi E
Autoimmun Rev 2014 Apr-May;13(4-5):351-4. Epub 2014 Jan 10 doi: 10.1016/j.autrev.2014.01.002. PMID: 24418297

Clinical prediction guides

Ferfar Y, Morinet S, Espitia O, Agard C, Vautier M, Comarmond C, Desbois AC, Domont F, Resche-Rigon M, Cacoub P, Biard L, Saadoun D; French Study Group for Large Vessel Vasculitis (GEFA)
J Rheumatol 2021 Oct;48(10):1583-1588. Epub 2021 Jul 1 doi: 10.3899/jrheum.201274. PMID: 34210830
Alyasin S, Esmaeilzadeh H, Ebrahimi N, Nabavizadeh SH, Nemati H
Arch Iran Med 2019 Dec 1;22(12):682-686. PMID: 31823618
Shamriz O, Tal Y, Gross M
J Immunol Res 2018;2018:1498640. Epub 2018 Apr 23 doi: 10.1155/2018/1498640. PMID: 29850616Free PMC Article
Durtette C, Hachulla E, Resche-Rigon M, Papo T, Zénone T, Lioger B, Deligny C, Lambert M, Landron C, Pouchot J, Kahn JE, Lavigne C, De Wazieres B, Dhote R, Gondran G, Pertuiset E, Quemeneur T, Hamidou M, Sève P, Le Gallou T, Grasland A, Hatron PY, Fain O, Mekinian A; SNFMI and CRI
Autoimmun Rev 2017 Dec;16(12):1219-1223. Epub 2017 Oct 14 doi: 10.1016/j.autrev.2017.10.005. PMID: 29037902
Pasanisi E, Vincenti V, Bacciu A, Guida M, Berghenti T, Barbot A, Orsoni JG, Bacciu S
Otol Neurotol 2003 Jul;24(4):601-4. doi: 10.1097/00129492-200307000-00012. PMID: 12851552

Recent systematic reviews

Kasap Cuceoglu M, Basaran O, Batu ED, Kaya Akca U, Atalay E, Sener S, Balik Z, Bayindir Y, Aliyev E, Gocmen R, Kadayifcilar S, Akyol U, Bilginer Y, Ozen S
Int J Rheum Dis 2023 Mar;26(3):544-550. Epub 2022 Dec 11 doi: 10.1111/1756-185X.14531. PMID: 36502531
Mora P, Calzetti G, Ghirardini S, Rubino P, Gandolfi S, Orsoni J
Autoimmun Rev 2017 Apr;16(4):385-390. Epub 2017 Feb 14 doi: 10.1016/j.autrev.2017.02.009. PMID: 28232169
Iliescu DA, Timaru CM, Batras M, De Simone A, Stefan C
Rom J Ophthalmol 2015 Jan-Mar;59(1):6-13. PMID: 27373108Free PMC Article
Greco A, Gallo A, Fusconi M, Magliulo G, Turchetta R, Marinelli C, Macri GF, De Virgilio A, de Vincentiis M
Autoimmun Rev 2013 Jan;12(3):396-400. Epub 2012 Jul 28 doi: 10.1016/j.autrev.2012.07.012. PMID: 22846458

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