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Right aortic arch with retroesophageal left subclavian artery

MedGen UID:
866789
Concept ID:
C4021140
Anatomical Abnormality
Synonyms: Right aortic arch with aberrant left subclavian artery; Right aortic arch with anomalous left subclavian artery
 
HPO: HP:0011598

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRight aortic arch with retroesophageal left subclavian artery

Recent clinical studies

Etiology

Chaudhary B, Kumari S
Surg Radiol Anat 2022 Nov;44(11):1461-1465. Epub 2022 Oct 23 doi: 10.1007/s00276-022-03036-0. PMID: 36273342
Ito T, Itoh A, Kiyoshima D, Ikeda Y
Anat Sci Int 2022 Sep;97(4):423-427. Epub 2022 Mar 22 doi: 10.1007/s12565-022-00658-7. PMID: 35316514
Plotkin A, Ng B, Han SM, Weaver FA, Ham SW, Bowdish ME, Wilcox AG, Magee GA
J Vasc Surg 2020 Nov;72(5):1534-1543. Epub 2020 Mar 29 doi: 10.1016/j.jvs.2020.01.042. PMID: 32238310
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Tyczyński P, Michałowska I, Wolny R, Dobrowolski P, Łazarczyk H, Rybicka J, Hoffman P, Witkowski A
Int J Cardiol 2017 Aug 1;240:183-186. Epub 2017 Apr 25 doi: 10.1016/j.ijcard.2017.04.052. PMID: 28483478

Diagnosis

Chen YW, Chang SL, Wu NC, Shih YJ
Medicine (Baltimore) 2022 Dec 9;101(49):e32272. doi: 10.1097/MD.0000000000032272. PMID: 36626475Free PMC Article
Plotkin A, Ng B, Han SM, Weaver FA, Ham SW, Bowdish ME, Wilcox AG, Magee GA
J Vasc Surg 2020 Nov;72(5):1534-1543. Epub 2020 Mar 29 doi: 10.1016/j.jvs.2020.01.042. PMID: 32238310
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Dong SZ, Zhu M
Sci Rep 2018 Oct 3;8(1):14781. doi: 10.1038/s41598-018-33033-6. PMID: 30283087Free PMC Article
Backer CL, Russell HM, Wurlitzer KC, Rastatter JC, Rigsby CK
Ann Thorac Surg 2012 Nov;94(5):1612-7. Epub 2012 Aug 9 doi: 10.1016/j.athoracsur.2012.05.101. PMID: 22884596

Therapy

Gray SE, Scali ST, Feezor RJ, Beaver TM, Back MR, Upchurch GR Jr, Huber TS, Fatima J
J Vasc Surg 2020 Dec;72(6):1873-1882. Epub 2020 Jul 19 doi: 10.1016/j.jvs.2020.01.075. PMID: 32665182

Prognosis

Chen YW, Chang SL, Wu NC, Shih YJ
Medicine (Baltimore) 2022 Dec 9;101(49):e32272. doi: 10.1097/MD.0000000000032272. PMID: 36626475Free PMC Article
Buffoli B, Verzeletti V, Hirtler L, Rezzani R, Rodella LF
Surg Radiol Anat 2021 Sep;43(9):1491-1495. Epub 2021 Apr 15 doi: 10.1007/s00276-021-02746-1. PMID: 33856505Free PMC Article
Plotkin A, Ng B, Han SM, Weaver FA, Ham SW, Bowdish ME, Wilcox AG, Magee GA
J Vasc Surg 2020 Nov;72(5):1534-1543. Epub 2020 Mar 29 doi: 10.1016/j.jvs.2020.01.042. PMID: 32238310
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Białowas J, Hreczecha J, Grzybiak M
Folia Morphol (Warsz) 2000;59(3):211-6. PMID: 10974792

Clinical prediction guides

Ito T, Itoh A, Kiyoshima D, Ikeda Y
Anat Sci Int 2022 Sep;97(4):423-427. Epub 2022 Mar 22 doi: 10.1007/s12565-022-00658-7. PMID: 35316514
Gray SE, Scali ST, Feezor RJ, Beaver TM, Back MR, Upchurch GR Jr, Huber TS, Fatima J
J Vasc Surg 2020 Dec;72(6):1873-1882. Epub 2020 Jul 19 doi: 10.1016/j.jvs.2020.01.075. PMID: 32665182
Silveira JV, Junqueira FP, Silveira CG, Consolim-Colombo FM
Am J Case Rep 2019 Feb 21;20:228-232. doi: 10.12659/AJCR.912053. PMID: 30787266Free PMC Article
Li S, Wen H, Liang M, Luo D, Qin Y, Liao Y, Ouyang S, Bi J, Tian X, Norwitz ER, Luo G
Cardiovasc Pathol 2019 Mar-Apr;39:38-50. Epub 2018 Dec 6 doi: 10.1016/j.carpath.2018.11.004. PMID: 30623879
Nakatani T, Tanaka S, Mizukami S, Okamoto K, Shiraishi Y, Nakamura T
Ann Anat 1996 Jun;178(3):269-71. doi: 10.1016/S0940-9602(96)80064-1. PMID: 8712376

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