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Malignant jugulotympanic paraganglioma

MedGen UID:
87584
Concept ID:
C0347856
Neoplastic Process
Synonyms: cancer of jugular body; jugular body cancer; Malignant Glomus Jugulare Neoplasm; malignant glomus jugulare neoplasm; Malignant Glomus Jugulare Tumor; malignant glomus jugulare tumor; malignant glomus jugulare tumour; malignant jugular body neoplasm; Malignant Jugulotympanic Paraganglioma; malignant jugulotympanic paraganglioma; Malignant Neoplasm of Glomus Jugulare; malignant neoplasm of glomus jugulare; malignant neoplasm of jugular body; Malignant Neoplasm of the Glomus Jugulare; malignant neoplasm of the glomus jugulare; Malignant Tumor of Glomus Jugulare; malignant tumor of glomus jugulare; malignant tumor of the glomus jugulare; malignant tumour of glomus jugulare; malignant tumour of the glomus jugulare; Metastatic Jugulotympanic Paraganglioma; Primary malignant neoplasm of glomus jugulare
SNOMED CT: Primary malignant neoplasm of glomus jugulare (93814004)
 
Monarch Initiative: MONDO:0006291

Definition

A jugulotympanic paraganglioma that metastasizes to other anatomic sites. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVMalignant jugulotympanic paraganglioma

Professional guidelines

PubMed

Moore MG, Netterville JL, Mendenhall WM, Isaacson B, Nussenbaum B
Otolaryngol Head Neck Surg 2016 Apr;154(4):597-605. Epub 2016 Feb 9 doi: 10.1177/0194599815627667. PMID: 26861230
Suárez C, Rodrigo JP, Bödeker CC, Llorente JL, Silver CE, Jansen JC, Takes RP, Strojan P, Pellitteri PK, Rinaldo A, Mendenhall WM, Ferlito A
Head Neck 2013 Aug;35(8):1195-204. Epub 2012 Mar 16 doi: 10.1002/hed.22976. PMID: 22422597
Sismanis A
Curr Opin Otolaryngol Head Neck Surg 2011 Oct;19(5):348-57. doi: 10.1097/MOO.0b013e3283493fd8. PMID: 22552697

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