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Syringomyelia and Hydromyelia

MedGen UID:
888087
•Concept ID:
C4053961
•
Disease or Syndrome

Definition

Syringomyelia associated with accumulation of cerebrospinal fluid in the spinal cord. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSyringomyelia and Hydromyelia

Professional guidelines

PubMed

Treatment of posttraumatic syringomyelia: evidence from a systematic review.
Kleindienst A, Laut FM, Roeckelein V, Buchfelder M, Dodoo-Schittko F
Acta Neurochir (Wien) 2020 Oct;162(10):2541-2556. Epub 2020 Aug 20 doi: 10.1007/s00701-020-04529-w. PMID: 32820376Free PMC Article
Hydromyelia: clinical presentation and comparison of modalities of treatment.
Schlesinger EB, Antunes JL, Michelsen WJ, Louis KM
Neurosurgery 1981 Oct;9(4):356-65. doi: 10.1227/00006123-198110000-00002. PMID: 7301079

Recent clinical studies

Etiology

Terminal syringomyelia associated with lumbar limited dorsal myeloschisis.
Morioka T, Murakami N, Yanagida H, Yamaguchi T, Noguchi Y, Takahata Y, Tsukamoto A, Suzuki SO
Childs Nerv Syst 2020 Apr;36(4):819-826. Epub 2019 Jul 17 doi: 10.1007/s00381-019-04297-8. PMID: 31317225
Chiari Malformations.
Mancarella C, Delfini R, Landi A
Acta Neurochir Suppl 2019;125:89-95. doi: 10.1007/978-3-319-62515-7_13. PMID: 30610307
Syringomyelia: a practical, clinical concept for classification.
Blegvad C, Grotenhuis JA, Juhler M
Acta Neurochir (Wien) 2014 Nov;156(11):2127-38. Epub 2014 Sep 19 doi: 10.1007/s00701-014-2229-z. PMID: 25236931
MR of terminal myelocystoceles.
Byrd SE, Harvey C, Darling CF
Eur J Radiol 1995 Sep;20(3):215-20. doi: 10.1016/0720-048x(95)00659-e. PMID: 8536754
Chiari I malformations and hydromyelia--complications.
Menezes AH
Pediatr Neurosurg 1991-1992;17(3):146-54. doi: 10.1159/000120586. PMID: 1819330

Diagnosis

Syringomyelia and hydromyelia: Current understanding and neurosurgical management.
Leclerc A, Matveeff L, Emery E
Rev Neurol (Paris) 2021 May;177(5):498-507. Epub 2020 Aug 18 doi: 10.1016/j.neurol.2020.07.004. PMID: 32826067
Chiari Malformations.
Mancarella C, Delfini R, Landi A
Acta Neurochir Suppl 2019;125:89-95. doi: 10.1007/978-3-319-62515-7_13. PMID: 30610307
Hydromyelia associated with spinal lipoma of the conus: case report.
Faggin R, Drigo P, Denaro L, Sartori S, d'Avella D
Spine (Phila Pa 1976) 2010 Sep 15;35(20):E1069-71. doi: 10.1097/BRS.0b013e3181ed0b50. PMID: 20802384
Defining the line between hydromyelia and syringomyelia. A differentiation is possible based on electrophysiological and magnetic resonance imaging studies.
Roser F, Ebner FH, Sixt C, Hagen JM, Tatagiba MS
Acta Neurochir (Wien) 2010 Feb;152(2):213-9; discussion 219. Epub 2009 Jun 16 doi: 10.1007/s00701-009-0427-x. PMID: 19533016
Hydromyelia: a critical review.
Wisoff JH
Childs Nerv Syst 1988 Feb;4(1):1-8. doi: 10.1007/BF00274073. PMID: 3042131

Therapy

The Management of Idiopathic and Refractory Syringomyelia.
Gallo P, Kaliaperumal C
Adv Tech Stand Neurosurg 2022;45:317-338. doi: 10.1007/978-3-030-99166-1_10. PMID: 35976455
Treatment of posttraumatic syringomyelia: evidence from a systematic review.
Kleindienst A, Laut FM, Roeckelein V, Buchfelder M, Dodoo-Schittko F
Acta Neurochir (Wien) 2020 Oct;162(10):2541-2556. Epub 2020 Aug 20 doi: 10.1007/s00701-020-04529-w. PMID: 32820376Free PMC Article
Acute central canal dilatation after minimally invasive lateral cervical decompression through the Frykholm approach.
Foelsch C, Peterlein CD, Fuchs-Winkelmann S, Lakemeier S
J Spinal Disord Tech 2011 May;24(3):208-11. doi: 10.1097/BSD.0b013e3181e16217. PMID: 21519303
US of the spinal cord in newborns: spectrum of normal findings, variants, congenital anomalies, and acquired diseases.
Unsinn KM, Geley T, Freund MC, Gassner I
Radiographics 2000 Jul-Aug;20(4):923-38. doi: 10.1148/radiographics.20.4.g00jl06923. PMID: 10903684
Iodoventriculography in hydromyelia.
Tjaden RJ, Ethier R, Vezina JL, Melançon D
J Can Assoc Radiol 1969 Dec;20(4):265-8. PMID: 4312232

Prognosis

Terminal syringomyelia associated with lumbar limited dorsal myeloschisis.
Morioka T, Murakami N, Yanagida H, Yamaguchi T, Noguchi Y, Takahata Y, Tsukamoto A, Suzuki SO
Childs Nerv Syst 2020 Apr;36(4):819-826. Epub 2019 Jul 17 doi: 10.1007/s00381-019-04297-8. PMID: 31317225
Clinical Relevance of Preoperative MRI in Adolescent Idiopathic Scoliosis: Is Hydromyelia a Predictive Factor of Intraoperative Electrophysiological Monitoring Alterations?
Scaramuzzo L, Giudici F, Archetti M, Minoia L, Zagra A, Bongetta D
Clin Spine Surg 2019 May;32(4):E183-E187. doi: 10.1097/BSD.0000000000000820. PMID: 30913042
MR of terminal myelocystoceles.
Byrd SE, Harvey C, Darling CF
Eur J Radiol 1995 Sep;20(3):215-20. doi: 10.1016/0720-048x(95)00659-e. PMID: 8536754
Chiari I malformations and hydromyelia--complications.
Menezes AH
Pediatr Neurosurg 1991-1992;17(3):146-54. doi: 10.1159/000120586. PMID: 1819330
Hydromyelia: a critical review.
Wisoff JH
Childs Nerv Syst 1988 Feb;4(1):1-8. doi: 10.1007/BF00274073. PMID: 3042131

Clinical prediction guides

Treatment of posttraumatic syringomyelia: evidence from a systematic review.
Kleindienst A, Laut FM, Roeckelein V, Buchfelder M, Dodoo-Schittko F
Acta Neurochir (Wien) 2020 Oct;162(10):2541-2556. Epub 2020 Aug 20 doi: 10.1007/s00701-020-04529-w. PMID: 32820376Free PMC Article
Clinical Relevance of Preoperative MRI in Adolescent Idiopathic Scoliosis: Is Hydromyelia a Predictive Factor of Intraoperative Electrophysiological Monitoring Alterations?
Scaramuzzo L, Giudici F, Archetti M, Minoia L, Zagra A, Bongetta D
Clin Spine Surg 2019 May;32(4):E183-E187. doi: 10.1097/BSD.0000000000000820. PMID: 30913042
A new concept in the electrophysiological evaluation of syringomyelia.
Roser F, Ebner FH, Liebsch M, Dietz K, Tatagiba M
J Neurosurg Spine 2008 Jun;8(6):517-23. doi: 10.3171/SPI/2008/8/6/517. PMID: 18518671
Delayed resolution of Chiari I-associated hydromyelia after posterior fossa decompression: case report and review of the literature.
Doughty KE, Tubbs RS, Webb D, Oakes WJ
Neurosurgery 2004 Sep;55(3):711. doi: 10.1227/01.neu.0000134548.16165.9. PMID: 16933383
Treatment of hydromyelia in spina bifida.
Caldarelli M, Di Rocco C, La Marca F
Surg Neurol 1998 Nov;50(5):411-20. doi: 10.1016/s0090-3019(97)00457-6. PMID: 9842864

Recent systematic reviews

Treatment of posttraumatic syringomyelia: evidence from a systematic review.
Kleindienst A, Laut FM, Roeckelein V, Buchfelder M, Dodoo-Schittko F
Acta Neurochir (Wien) 2020 Oct;162(10):2541-2556. Epub 2020 Aug 20 doi: 10.1007/s00701-020-04529-w. PMID: 32820376Free PMC Article

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