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Papillary ependymoma

MedGen UID:
90810
Concept ID:
C0334578
Neoplastic Process
Synonyms: Ependymoma, Papillary; Ependymomas, Papillary; Papillary Ependymoma; Papillary Ependymomas
SNOMED CT: Papillary ependymoma (128839002)
 
Monarch Initiative: MONDO:0003475

Definition

A rare variant of ependymoma characterized by well formed papillae. Tumor cell processes abutting capillaries are usually GFAP-positive. Differential diagnoses include choroid plexus papilloma, papillary meningioma and metastatic papillary carcinoma. (Adapted from WHO) [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVPapillary ependymoma

Professional guidelines

PubMed

Du J, Wang J, Cui Y, Zhang C, Li G, Fang J, Yue S, Xu L
Neuropathology 2015 Oct;35(5):410-20. Epub 2015 May 6 doi: 10.1111/neup.12200. PMID: 25944396

Recent clinical studies

Etiology

Neumann JE, Spohn M, Obrecht D, Mynarek M, Thomas C, Hasselblatt M, Dorostkar MM, Wefers AK, Frank S, Monoranu CM, Koch A, Witt H, Kool M, Pajtler KW, Rutkowski S, Glatzel M, Schüller U
Acta Neuropathol 2020 Feb;139(2):305-318. Epub 2019 Nov 2 doi: 10.1007/s00401-019-02090-0. PMID: 31679042
Lee Y, Kim SI, Kim SK, Kim IO, Park SH
Brain Tumor Pathol 2016 Apr;33(2):147-50. Epub 2015 Dec 15 doi: 10.1007/s10014-015-0242-4. PMID: 26670168
Grajkowska W, Matyja E, Pronicki M, Daszkiewicz P, Roszkowski M, Perek D, Drogosiewicz M
Folia Neuropathol 2009;47(4):354-61. PMID: 20054788
Suri VS, Tatke M, Singh D, Sharma A
Indian J Cancer 2004 Apr-Jun;41(2):66-71. PMID: 15318011
Park SH, Park HR, Chi JG
J Korean Med Sci 1996 Oct;11(5):415-21. doi: 10.3346/jkms.1996.11.5.415. PMID: 8934397Free PMC Article

Diagnosis

Neumann JE, Spohn M, Obrecht D, Mynarek M, Thomas C, Hasselblatt M, Dorostkar MM, Wefers AK, Frank S, Monoranu CM, Koch A, Witt H, Kool M, Pajtler KW, Rutkowski S, Glatzel M, Schüller U
Acta Neuropathol 2020 Feb;139(2):305-318. Epub 2019 Nov 2 doi: 10.1007/s00401-019-02090-0. PMID: 31679042
Du J, Wang J, Cui Y, Zhang C, Li G, Fang J, Yue S, Xu L
Neuropathology 2015 Oct;35(5):410-20. Epub 2015 May 6 doi: 10.1111/neup.12200. PMID: 25944396
Fèvre Montange M, Vasiljevic A, Champier J, Jouvet A
Neurochirurgie 2015 Apr-Jun;61(2-3):138-42. Epub 2014 Feb 18 doi: 10.1016/j.neuchi.2013.04.011. PMID: 24556386
Schuldt M, Retamero JA, Bergeron C, Nogales FF
Histopathology 2014 Dec;65(6):923-5. Epub 2014 Oct 30 doi: 10.1111/his.12462. PMID: 24845054
Suri VS, Tatke M, Singh D, Sharma A
Indian J Cancer 2004 Apr-Jun;41(2):66-71. PMID: 15318011

Therapy

Jinhu Y, Jianping D, Jun M, Hui S, Yepeng F
J Neurooncol 2007 May;83(1):47-52. Epub 2007 Mar 27 doi: 10.1007/s11060-006-9300-4. PMID: 17387433

Prognosis

Tang H, Wu T, Zhao F, Zhang J, Yang Z, Li P, Wang X, Wang B, Wang Z, Liu P
Br J Neurosurg 2023 Oct;37(5):1277-1280. Epub 2020 Dec 10 doi: 10.1080/02688697.2020.1853044. PMID: 33300386
Neumann JE, Spohn M, Obrecht D, Mynarek M, Thomas C, Hasselblatt M, Dorostkar MM, Wefers AK, Frank S, Monoranu CM, Koch A, Witt H, Kool M, Pajtler KW, Rutkowski S, Glatzel M, Schüller U
Acta Neuropathol 2020 Feb;139(2):305-318. Epub 2019 Nov 2 doi: 10.1007/s00401-019-02090-0. PMID: 31679042
Lee Y, Kim SI, Kim SK, Kim IO, Park SH
Brain Tumor Pathol 2016 Apr;33(2):147-50. Epub 2015 Dec 15 doi: 10.1007/s10014-015-0242-4. PMID: 26670168
Dulai MS, Caccamo DV, Briley AL, Edwards MS, Fisher PG, Lehman NL
J Neurosurg Pediatr 2010 May;5(5):511-7. doi: 10.3171/2009.12.PEDS09130. PMID: 20433266
Suri VS, Tatke M, Singh D, Sharma A
Indian J Cancer 2004 Apr-Jun;41(2):66-71. PMID: 15318011

Clinical prediction guides

Tang H, Wu T, Zhao F, Zhang J, Yang Z, Li P, Wang X, Wang B, Wang Z, Liu P
Br J Neurosurg 2023 Oct;37(5):1277-1280. Epub 2020 Dec 10 doi: 10.1080/02688697.2020.1853044. PMID: 33300386
Lee Y, Kim SI, Kim SK, Kim IO, Park SH
Brain Tumor Pathol 2016 Apr;33(2):147-50. Epub 2015 Dec 15 doi: 10.1007/s10014-015-0242-4. PMID: 26670168
Matyja E, Grajkowska W, Nauman P, Bonicki W
Folia Neuropathol 2011;49(3):181-90. PMID: 22101951
Yano H, Ohe N, Nakayama N, Shinoda J, Iwama T
Brain Tumor Pathol 2009;26(2):83-8. Epub 2009 Oct 27 doi: 10.1007/s10014-009-0246-z. PMID: 19856220
Buchino JJ, Mason KG
Acta Cytol 1992 Jan-Feb;36(1):95-7. PMID: 1312286

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