Etiology
Montani D,
Girerd B,
Jaïs X,
Laveneziana P,
Lau EMT,
Bouchachi A,
Hascoët S,
Günther S,
Godinas L,
Parent F,
Guignabert C,
Beurnier A,
Chemla D,
Hervé P,
Eyries M,
Soubrier F,
Simonneau G,
Sitbon O,
Savale L,
Humbert M
Eur Respir J
2021 Jul;58(1)
Epub 2021 Jul 22
doi: 10.1183/13993003.04229-2020.
PMID: 33380512Free PMC Article
Girerd B,
Weatherald J,
Montani D,
Humbert M
Eur Respir Rev
2017 Sep 30;26(145)
Epub 2017 Sep 6
doi: 10.1183/16000617.0037-2017.
PMID: 28877973Free PMC Article
Girerd B,
Lau E,
Montani D,
Humbert M
Curr Opin Pulm Med
2017 Sep;23(5):386-391.
doi: 10.1097/MCP.0000000000000414.
PMID: 28661905
Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
doi: 10.1016/j.jacc.2013.10.032.
PMID: 24355641
Austin ED,
Loyd JE
Semin Respir Crit Care Med
2013 Oct;34(5):568-80.
Epub 2013 Sep 13
doi: 10.1055/s-0033-1355443.
PMID: 24037626Free PMC Article
Diagnosis
Vorselaars VMM,
Hosman AE,
Westermann CJJ,
Snijder RJ,
Mager JJ,
Goumans MJ,
Post MC
Int J Mol Sci
2018 Oct 17;19(10)
doi: 10.3390/ijms19103203.
PMID: 30336550Free PMC Article
Girerd B,
Weatherald J,
Montani D,
Humbert M
Eur Respir Rev
2017 Sep 30;26(145)
Epub 2017 Sep 6
doi: 10.1183/16000617.0037-2017.
PMID: 28877973Free PMC Article
Girerd B,
Lau E,
Montani D,
Humbert M
Curr Opin Pulm Med
2017 Sep;23(5):386-391.
doi: 10.1097/MCP.0000000000000414.
PMID: 28661905
Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
doi: 10.1016/j.jacc.2013.10.032.
PMID: 24355641
Soubrier F,
Chung WK,
Machado R,
Grünig E,
Aldred M,
Geraci M,
Loyd JE,
Elliott CG,
Trembath RC,
Newman JH,
Humbert M
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D13-21.
doi: 10.1016/j.jacc.2013.10.035.
PMID: 24355637
Therapy
Howard LSGE,
He J,
Watson GMJ,
Huang L,
Wharton J,
Luo Q,
Kiely DG,
Condliffe R,
Pepke-Zaba J,
Morrell NW,
Sheares KK,
Ulrich A,
Quan R,
Zhao Z,
Jing X,
An C,
Liu Z,
Xiong C,
Robbins PA,
Dawes T,
de Marvao A,
Rhodes CJ,
Richter MJ,
Gall H,
Ghofrani HA,
Zhao L,
Huson L,
Wilkins MR
Ann Am Thorac Soc
2021 Jun;18(6):981-988.
doi: 10.1513/AnnalsATS.202009-1131OC.
PMID: 33735594Free PMC Article
Rhodes CJ,
Otero-Núñez P,
Wharton J,
Swietlik EM,
Kariotis S,
Harbaum L,
Dunning MJ,
Elinoff JM,
Errington N,
Thompson AAR,
Iremonger J,
Coghlan JG,
Corris PA,
Howard LS,
Kiely DG,
Church C,
Pepke-Zaba J,
Toshner M,
Wort SJ,
Desai AA,
Humbert M,
Nichols WC,
Southgate L,
Trégouët DA,
Trembath RC,
Prokopenko I,
Gräf S,
Morrell NW,
Wang D,
Lawrie A,
Wilkins MR
Am J Respir Crit Care Med
2020 Aug 15;202(4):586-594.
doi: 10.1164/rccm.202003-0510OC.
PMID: 32352834Free PMC Article
Ogawa A,
Satoh T,
Tamura Y,
Fukuda K,
Matsubara H
Am J Cardiol
2017 May 1;119(9):1479-1484.
Epub 2017 Feb 9
doi: 10.1016/j.amjcard.2017.01.015.
PMID: 28267959
Dardi F,
Manes A,
Palazzini M,
Bachetti C,
Mazzanti G,
Rinaldi A,
Albini A,
Gotti E,
Monti E,
Bacchi Reggiani ML,
Galiè N
Eur Respir J
2015 Aug;46(2):414-21.
Epub 2015 May 28
doi: 10.1183/09031936.00209914.
PMID: 26022952
Matsubara H,
Ogawa A
J Cardiol
2014 Oct;64(4):243-9.
Epub 2014 Jul 28
doi: 10.1016/j.jjcc.2014.06.009.
PMID: 25082294
Prognosis
Suzuki S,
Asano R,
Aoki T,
Nakayama S,
Ueda J,
Tsuji A,
Noguchi T,
Ogo T
Open Heart
2022 Jun;9(1)
doi: 10.1136/openhrt-2022-002054.
PMID: 35675988Free PMC Article
Girerd B,
Weatherald J,
Montani D,
Humbert M
Eur Respir Rev
2017 Sep 30;26(145)
Epub 2017 Sep 6
doi: 10.1183/16000617.0037-2017.
PMID: 28877973Free PMC Article
Girerd B,
Lau E,
Montani D,
Humbert M
Curr Opin Pulm Med
2017 Sep;23(5):386-391.
doi: 10.1097/MCP.0000000000000414.
PMID: 28661905
Matsubara H,
Ogawa A
J Cardiol
2014 Oct;64(4):243-9.
Epub 2014 Jul 28
doi: 10.1016/j.jjcc.2014.06.009.
PMID: 25082294
Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
doi: 10.1016/j.jacc.2013.10.032.
PMID: 24355641
Clinical prediction guides
Suzuki S,
Asano R,
Aoki T,
Nakayama S,
Ueda J,
Tsuji A,
Noguchi T,
Ogo T
Open Heart
2022 Jun;9(1)
doi: 10.1136/openhrt-2022-002054.
PMID: 35675988Free PMC Article
Wang MT,
Charng MJ,
Chi PL,
Cheng CC,
Hung CC,
Huang WC
Glob Heart
2021;16(1):70.
Epub 2021 Oct 18
doi: 10.5334/gh.1002.
PMID: 34900561Free PMC Article
Rhodes CJ,
Otero-Núñez P,
Wharton J,
Swietlik EM,
Kariotis S,
Harbaum L,
Dunning MJ,
Elinoff JM,
Errington N,
Thompson AAR,
Iremonger J,
Coghlan JG,
Corris PA,
Howard LS,
Kiely DG,
Church C,
Pepke-Zaba J,
Toshner M,
Wort SJ,
Desai AA,
Humbert M,
Nichols WC,
Southgate L,
Trégouët DA,
Trembath RC,
Prokopenko I,
Gräf S,
Morrell NW,
Wang D,
Lawrie A,
Wilkins MR
Am J Respir Crit Care Med
2020 Aug 15;202(4):586-594.
doi: 10.1164/rccm.202003-0510OC.
PMID: 32352834Free PMC Article
Girerd B,
Weatherald J,
Montani D,
Humbert M
Eur Respir Rev
2017 Sep 30;26(145)
Epub 2017 Sep 6
doi: 10.1183/16000617.0037-2017.
PMID: 28877973Free PMC Article
Hoeper MM,
Bogaard HJ,
Condliffe R,
Frantz R,
Khanna D,
Kurzyna M,
Langleben D,
Manes A,
Satoh T,
Torres F,
Wilkins MR,
Badesch DB
J Am Coll Cardiol
2013 Dec 24;62(25 Suppl):D42-50.
doi: 10.1016/j.jacc.2013.10.032.
PMID: 24355641