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Type I truncus arteriosus

MedGen UID:
322536
•Concept ID:
C1834934
•
Congenital Abnormality; Finding
Synonym: Type 1 truncus arteriosus
 
HPO: HP:0004384

Definition

Truncus arteriosus (single great artery leaving the base of the heart, giving rise to the coronary, pulmonary, and systemic arteries) with a short pulmonary trunk arises from the truncus arteriosus, giving rise to both pulmonary arteries. [from HPO]

Professional guidelines

PubMed

Clinical utility of repeat fetal echocardiography in congenital heart disease.
Barris DM, Mikhno M, Kornblit M, Wang K, Duong S, Cohen J, Paul E, Stern K, Ezon D, Geiger M
Ultrasound Obstet Gynecol 2023 Nov;62(5):695-700. Epub 2023 Oct 11 doi: 10.1002/uog.26240. PMID: 37128164
Accuracy and impact of prenatal diagnosis of common arterial trunk.
Laux D, Derridj N, Stirnemann J, Lucron H, Stos B, Levy M, Houyel L, Bonnet D
Ultrasound Obstet Gynecol 2022 Aug;60(2):223-233. Epub 2022 Jun 30 doi: 10.1002/uog.24873. PMID: 35118719Free PMC Article
Accuracy of Fetal Echocardiography in the Differential Diagnosis between Truncus Arteriosus and Pulmonary Atresia with Ventricular Septal Defect.
Gómez O, Soveral I, Bennasar M, Crispi F, Masoller N, Marimon E, Bartrons J, Gratacós E, Martinez JM
Fetal Diagn Ther 2016;39(2):90-9. Epub 2015 Jun 25 doi: 10.1159/000433430. PMID: 26113195

Recent clinical studies

Etiology

Diagnosis of the double aortic arch and its differentiation from the conotruncal malformations.
Lee ML
Yonsei Med J 2007 Oct 31;48(5):818-26. doi: 10.3349/ymj.2007.48.5.818. PMID: 17963340Free PMC Article

Diagnosis

Modified Barbero-Marcial repair for type I truncus arteriosus in a 2.7-kg neonate.
Trager LE, Marey G, Said SM
Multimed Man Cardiothorac Surg 2022 Jan 31;2022 doi: 10.1510/mmcts.2022.002. PMID: 35224899
First Trimester Prenatal Diagnosis of a Conotruncal Anomaly Using Spatiotemporal Image Correlation Imaging Confirmed by Conventional Autopsy.
Karmegaraj B, Udhayakumar V, Selvan G
Fetal Pediatr Pathol 2022 Apr;41(2):346-350. Epub 2020 Aug 20 doi: 10.1080/15513815.2020.1806419. PMID: 32815432
Diagnosis of the double aortic arch and its differentiation from the conotruncal malformations.
Lee ML
Yonsei Med J 2007 Oct 31;48(5):818-26. doi: 10.3349/ymj.2007.48.5.818. PMID: 17963340Free PMC Article
Truncus arteriosus repair after palliative bilateral pulmonary artery banding.
Takabayashi S, Shimpo H, Yokoyama K, Kajimoto M
Gen Thorac Cardiovasc Surg 2007 Jan;55(1):35-7. doi: 10.1007/s11748-006-0065-7. PMID: 17444172
Double mitral valve orifice.
Di Segni E, Lew S, Shapira H, Kaplinsky E
Pediatr Cardiol 1986;6(4):215-7. doi: 10.1007/BF02311002. PMID: 3703694

Therapy

Excessive bleeding on extracorporeal membrane oxygenation after surgical repair of type I truncus arteriosus: A case report.
Berger A, Wollenek G, Hermon M, Burda G
Artif Organs 1999 Nov;23(11):1033-5. doi: 10.1046/j.1525-1594.1999.06460.x. PMID: 10564312
Endocarditis with aneurysm involving an aortic homograft used to correct a truncus arteriosus: medical-surgical salvage.
Engle MA, Lang SJ, Edelson P
Br Heart J 1992 May;67(5):409-11. doi: 10.1136/hrt.67.5.409. PMID: 1389722Free PMC Article
Coronary artery injury by a valved external conduit.
Harris JP, Stewart S, Anderson V, Mitchell ML, Manning JA
Ann Thorac Surg 1981 Mar;31(3):271-3. doi: 10.1016/s0003-4975(10)60941-1. PMID: 7212824

Prognosis

A rare variant of type I truncus arteriosus: truncus arteriosus with anterior origin of a main pulmonary artery.
Çelik SF, Karakurt C, Elkıran Ö, Öztürk M, Görmeli AC
Echocardiography 2015 May;32(5):880-2. Epub 2014 Dec 15 doi: 10.1111/echo.12865. PMID: 25496122
Congenital microgastria and primary ciliary dyskinesia in a newborn with DiGeorge syndrome and 22q11.2 deletion.
Filippi L, Serafini L, Fiorini P, Agostini E, Giovannucci Uzielli ML
Eur J Pediatr Surg 2008 Jun;18(3):195-7. doi: 10.1055/s-2008-1038503. PMID: 18493898
Truncus arteriosus repair after palliative bilateral pulmonary artery banding.
Takabayashi S, Shimpo H, Yokoyama K, Kajimoto M
Gen Thorac Cardiovasc Surg 2007 Jan;55(1):35-7. doi: 10.1007/s11748-006-0065-7. PMID: 17444172
Rastelli and Norwood combination for the treatment of type I truncus arteriosus and hypoplastic aortic arch: a case report.
Ugurlucan M, Sayin OA, Surmen B, Sungur Z, Tireli E, Dayioglu E
Heart Surg Forum 2007;10(1):E6-8. doi: 10.1532/HSF98.20061141. PMID: 17162406
Truncus arteriosus communis, an unusual anatomical variant of type I.
Zamora C, Jain SC, Muñoz-Castellanos L, Testelli M
Cathet Cardiovasc Diagn 1980;6(1):81-7. doi: 10.1002/ccd.1810060110. PMID: 7363322

Clinical prediction guides

Congenital microgastria and primary ciliary dyskinesia in a newborn with DiGeorge syndrome and 22q11.2 deletion.
Filippi L, Serafini L, Fiorini P, Agostini E, Giovannucci Uzielli ML
Eur J Pediatr Surg 2008 Jun;18(3):195-7. doi: 10.1055/s-2008-1038503. PMID: 18493898

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