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Rhabdoid meningioma

MedGen UID:
120445
•Concept ID:
C0259786
•
Neoplastic Process
Synonyms: Meningioma, rhabdoid; meningioma, rhabdoid; meningioma, rhabdoid (morphologic abnormality); papillary meningioma; papillary meningioma (morphologic abnormality); Rhabdoid Meningioma; rhabdoid meningioma
SNOMED CT: Meningioma, rhabdoid (399469000); Rhabdoid meningioma (399469000)
 
Monarch Initiative: MONDO:0003262

Definition

A WHO grade III meningioma characterized by the predominant presence of rhabdoid cells forming sheets. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRhabdoid meningioma

Professional guidelines

PubMed

The Role of Immunotherapy in the Treatment of Rare Central Nervous System Tumors.
Rodriguez A, Kamiya-Matsuoka C, Majd NK
Curr Oncol 2023 May 25;30(6):5279-5298. doi: 10.3390/curroncol30060401. PMID: 37366884Free PMC Article
Update from the 2011 International Schwannomatosis Workshop: From genetics to diagnostic criteria.
Plotkin SR, Blakeley JO, Evans DG, Hanemann CO, Hulsebos TJ, Hunter-Schaedle K, Kalpana GV, Korf B, Messiaen L, Papi L, Ratner N, Sherman LS, Smith MJ, Stemmer-Rachamimov AO, Vitte J, Giovannini M
Am J Med Genet A 2013 Mar;161A(3):405-16. Epub 2013 Feb 7 doi: 10.1002/ajmg.a.35760. PMID: 23401320Free PMC Article

Recent clinical studies

Etiology

Malignant intraventricular meningioma: literature review and case report.
Maiuri F, Mariniello G, Barbato M, Corvino S, Guadagno E, Chiariotti L, Del Basso De Caro M
Neurosurg Rev 2022 Feb;45(1):151-166. Epub 2021 Jun 23 doi: 10.1007/s10143-021-01585-3. PMID: 34159472
Rhabdoid meningiomas: Clinicopathological analysis of a rare variant of meningioma.
Birua GJS, Sadashiva N, Konar S, Rao S, Shukla D, Krishna U, Saini J, Santosh V
Clin Neurol Neurosurg 2021 Aug;207:106778. Epub 2021 Jun 24 doi: 10.1016/j.clineuro.2021.106778. PMID: 34214868
Pathology of meningiomas.
Solomon DA, Pekmezci M
Handb Clin Neurol 2020;169:87-99. doi: 10.1016/B978-0-12-804280-9.00005-6. PMID: 32553300
Prognostic factors and long-term outcomes of primary intracranial rhabdoid meningioma: A systematic review.
Zhang YY, Zhang L, Liu YZ, Zhang R, Zhang GH
Clin Neurol Neurosurg 2020 Sep;196:105971. Epub 2020 Jun 1 doi: 10.1016/j.clineuro.2020.105971. PMID: 32516684
Clinicopathologic analysis of rhabdoid meningioma.
Wu YT, Lin JW, Wang HC, Lee TC, Ho JT, Lin YJ
J Clin Neurosci 2010 Oct;17(10):1271-5. Epub 2010 May 26 doi: 10.1016/j.jocn.2009.12.014. PMID: 20537897

Diagnosis

Clinical, Histopathologic and Genetic Features of Rhabdoid Meningiomas.
Garrido Ruiz PA, González-Tablas M, Pasco Peña A, Zelaya Huerta MV, Ortiz J, Otero Á, Corchete LA, Ludeña MD, Caballero Martínez MC, Córdoba Iturriagagoitia A, Fernández IC, González-Carreró Fojón J, Hernández Laín A, Orfao A, Tabernero MD
Int J Mol Sci 2023 Jan 6;24(2) doi: 10.3390/ijms24021116. PMID: 36674634Free PMC Article
Meningioma with rhabdoid features: Pathologic findings in dogs.
Tabaran AF, Armien AG, Pluhar GE, O'Sullivan MG
Vet Pathol 2022 Sep;59(5):759-767. Epub 2022 Jun 8 doi: 10.1177/03009858221100436. PMID: 35674149
Malignant intraventricular meningioma: literature review and case report.
Maiuri F, Mariniello G, Barbato M, Corvino S, Guadagno E, Chiariotti L, Del Basso De Caro M
Neurosurg Rev 2022 Feb;45(1):151-166. Epub 2021 Jun 23 doi: 10.1007/s10143-021-01585-3. PMID: 34159472
Prognostic factors and long-term outcomes of primary intracranial rhabdoid meningioma: A systematic review.
Zhang YY, Zhang L, Liu YZ, Zhang R, Zhang GH
Clin Neurol Neurosurg 2020 Sep;196:105971. Epub 2020 Jun 1 doi: 10.1016/j.clineuro.2020.105971. PMID: 32516684
The WHO classification of tumors of the nervous system.
Kleihues P, Louis DN, Scheithauer BW, Rorke LB, Reifenberger G, Burger PC, Cavenee WK
J Neuropathol Exp Neurol 2002 Mar;61(3):215-25; discussion 226-9. doi: 10.1093/jnen/61.3.215. PMID: 11895036

Therapy

Recurrent rhabdoid meningioma with lymph node, pulmonary and bone metastases: a diagnostic and therapeutic challenge.
Kakkar A, Baghmar S, Garg A, Suri V, Raina V, Sarkar C, Sharma MC
Brain Tumor Pathol 2016 Jul;33(3):228-33. Epub 2016 Feb 13 doi: 10.1007/s10014-016-0250-z. PMID: 26875176
Metastatic rhabdoid meningioma with BRAF V600E mutation and good response to personalized therapy: case report and review of the literature.
Mordechai O, Postovsky S, Vlodavsky E, Eran A, Constantini S, Dotan E, Cagnano E, Weyl-Ben-Arush M
Pediatr Hematol Oncol 2015 Apr;32(3):207-11. Epub 2014 Aug 12 doi: 10.3109/08880018.2014.936058. PMID: 25116269
Hemorrhagic onset of rhabdoid meningioma after initiating treatment for infertility.
Motegi H, Kobayashi H, Terasaka S, Ishii N, Ito M, Shimbo D, Kubota K, Houkin K
Brain Tumor Pathol 2012 Oct;29(4):240-4. Epub 2012 Feb 17 doi: 10.1007/s10014-012-0088-y. PMID: 22350616

Prognosis

Clinical, Histopathologic and Genetic Features of Rhabdoid Meningiomas.
Garrido Ruiz PA, González-Tablas M, Pasco Peña A, Zelaya Huerta MV, Ortiz J, Otero Á, Corchete LA, Ludeña MD, Caballero Martínez MC, Córdoba Iturriagagoitia A, Fernández IC, González-Carreró Fojón J, Hernández Laín A, Orfao A, Tabernero MD
Int J Mol Sci 2023 Jan 6;24(2) doi: 10.3390/ijms24021116. PMID: 36674634Free PMC Article
Malignant intraventricular meningioma: literature review and case report.
Maiuri F, Mariniello G, Barbato M, Corvino S, Guadagno E, Chiariotti L, Del Basso De Caro M
Neurosurg Rev 2022 Feb;45(1):151-166. Epub 2021 Jun 23 doi: 10.1007/s10143-021-01585-3. PMID: 34159472
Rhabdoid meningiomas: Clinicopathological analysis of a rare variant of meningioma.
Birua GJS, Sadashiva N, Konar S, Rao S, Shukla D, Krishna U, Saini J, Santosh V
Clin Neurol Neurosurg 2021 Aug;207:106778. Epub 2021 Jun 24 doi: 10.1016/j.clineuro.2021.106778. PMID: 34214868
Prognostic factors and long-term outcomes of primary intracranial rhabdoid meningioma: A systematic review.
Zhang YY, Zhang L, Liu YZ, Zhang R, Zhang GH
Clin Neurol Neurosurg 2020 Sep;196:105971. Epub 2020 Jun 1 doi: 10.1016/j.clineuro.2020.105971. PMID: 32516684
The WHO classification of tumors of the nervous system.
Kleihues P, Louis DN, Scheithauer BW, Rorke LB, Reifenberger G, Burger PC, Cavenee WK
J Neuropathol Exp Neurol 2002 Mar;61(3):215-25; discussion 226-9. doi: 10.1093/jnen/61.3.215. PMID: 11895036

Clinical prediction guides

Paediatric Rhabdoid Meningioma: Clinical and Therapeutic Features Findings - Case Series of 3 Patients.
Gader G, Slimane A, Sliti F, Badri M, Zammel I
Pediatr Neurosurg 2024;59(1):20-26. Epub 2023 Dec 13 doi: 10.1159/000535715. PMID: 38091966
Clinical, Histopathologic and Genetic Features of Rhabdoid Meningiomas.
Garrido Ruiz PA, González-Tablas M, Pasco Peña A, Zelaya Huerta MV, Ortiz J, Otero Á, Corchete LA, Ludeña MD, Caballero Martínez MC, Córdoba Iturriagagoitia A, Fernández IC, González-Carreró Fojón J, Hernández Laín A, Orfao A, Tabernero MD
Int J Mol Sci 2023 Jan 6;24(2) doi: 10.3390/ijms24021116. PMID: 36674634Free PMC Article
Analysis of the inflammatory tumor microenvironment in meningeal neoplasms.
Berghoff AS, Kresl P, Rajky O, Widhalm G, Ricken G, Hainfellner JA, Marosi C, Birner P, Preusser M
Clin Neuropathol 2020 Nov/Dec;39(6):256-262. doi: 10.5414/NP301156. PMID: 32831157
Primary Pulmonary Meningioma With Rhabdoid Features.
Žulpaitė R, Jagelavičius Ž, Mickys U, Janilionis R
Int J Surg Pathol 2019 Jun;27(4):457-463. Epub 2018 Dec 18 doi: 10.1177/1066896918819257. PMID: 30563401
The WHO classification of tumors of the nervous system.
Kleihues P, Louis DN, Scheithauer BW, Rorke LB, Reifenberger G, Burger PC, Cavenee WK
J Neuropathol Exp Neurol 2002 Mar;61(3):215-25; discussion 226-9. doi: 10.1093/jnen/61.3.215. PMID: 11895036

Recent systematic reviews

Prognostic factors and long-term outcomes of primary intracranial rhabdoid meningioma: A systematic review.
Zhang YY, Zhang L, Liu YZ, Zhang R, Zhang GH
Clin Neurol Neurosurg 2020 Sep;196:105971. Epub 2020 Jun 1 doi: 10.1016/j.clineuro.2020.105971. PMID: 32516684
Clinicopathological analysis of rhabdoid meningiomas: report of 12 cases and a systematic review of the literature.
Zhou Y, Xie Q, Gong Y, Mao Y, Zhong P, Che X, Jiang C, Huang F, Zheng K, Li S, Gu Y, Bao W, Yang B, Wu J, Wang Y, Chen H, Xie L, Zheng M, Tang H, Wang D, Zhu H, Chen X
World Neurosurg 2013 May-Jun;79(5-6):724-32. Epub 2012 Aug 14 doi: 10.1016/j.wneu.2012.08.002. PMID: 22902360

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