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Coated aorta

MedGen UID:
1389349
•Concept ID:
C4476810
•
Disease or Syndrome
HPO: HP:0025494

Definition

Regular circumferential periaortic fibrosis involving the whole aorta and leading to a coated aorta appearance on computed tomography scans [from HPO]

Professional guidelines

PubMed

ADAM17: A novel treatment target for aneurysms.
Bai H, Zhang L, Sun P, Wu H, Li M, Gu Y, Zhang C, Lou C, Li J
Biomed Pharmacother 2022 Apr;148:112712. Epub 2022 Feb 11 doi: 10.1016/j.biopha.2022.112712. PMID: 35158143
Management of the infected aortic endograft.
Laohapensang K, Arworn S, Orrapin S, Reanpang T, Orrapin S
Semin Vasc Surg 2017 Jun-Sep;30(2-3):91-94. Epub 2017 Nov 14 doi: 10.1053/j.semvascsurg.2017.11.001. PMID: 29248126
Current management of infected aortic grafts in patients with connective tissue disorders.
Glebova NO, Black JH 3rd
Semin Vasc Surg 2017 Jun-Sep;30(2-3):75-79. Epub 2017 Oct 24 doi: 10.1053/j.semvascsurg.2017.10.003. PMID: 29248123

Recent clinical studies

Etiology

Erdheim-Chester disease.
Haroche J, Cohen-Aubart F, Amoura Z
Blood 2020 Apr 16;135(16):1311-1318. doi: 10.1182/blood.2019002766. PMID: 32107533
Erdheim-Chester disease.
Campochiaro C, Tomelleri A, Cavalli G, Berti A, Dagna L
Eur J Intern Med 2015 May;26(4):223-9. Epub 2015 Apr 10 doi: 10.1016/j.ejim.2015.03.004. PMID: 25865950

Diagnosis

Erdheim-Chester disease.
Haroche J, Cohen-Aubart F, Amoura Z
Blood 2020 Apr 16;135(16):1311-1318. doi: 10.1182/blood.2019002766. PMID: 32107533
Exophthalmos and coated aorta in Erdheim-Chester disease.
Liu SZ, Zhou X, Song A, Wang YP, Liu Y
Rheumatology (Oxford) 2020 Sep 1;59(9):2651-2652. doi: 10.1093/rheumatology/keaa022. PMID: 32025736
Erdheim-Chester disease.
Campochiaro C, Tomelleri A, Cavalli G, Berti A, Dagna L
Eur J Intern Med 2015 May;26(4):223-9. Epub 2015 Apr 10 doi: 10.1016/j.ejim.2015.03.004. PMID: 25865950
Cardiovascular manifestations of Erdheim-Chester disease.
Berti A, Ferrarini M, Ferrero E, Dagna L
Clin Exp Rheumatol 2015 Mar-Apr;33(2 Suppl 89):S-155-63. Epub 2015 Feb 18 PMID: 25738753
Imaging in Erdheim-Chester disease: classic features and new insights.
Moulis G, Sailler L, Bonneville F, Wagner T
Clin Exp Rheumatol 2014 May-Jun;32(3):410-4. Epub 2014 Jan 14 PMID: 24428974

Therapy

Rare presentation of multiple thromboses in Erdheim-Chester disease: a case-based review.
Liu Y, Huang C, Meng X, Fang X, Xie X, Wang C, Wang M
Int J Hematol 2022 Nov;116(5):798-806. Epub 2022 Jun 10 doi: 10.1007/s12185-022-03393-x. PMID: 35687294Free PMC Article
Coated aorta in Erdheim-Chester disease.
Cui R, Chen M, Dai SM
Rheumatology (Oxford) 2021 Feb 1;60(2):986-987. doi: 10.1093/rheumatology/keaa430. PMID: 33527114
Exophthalmos and coated aorta in Erdheim-Chester disease.
Liu SZ, Zhou X, Song A, Wang YP, Liu Y
Rheumatology (Oxford) 2020 Sep 1;59(9):2651-2652. doi: 10.1093/rheumatology/keaa022. PMID: 32025736
Association between Ischemic Stroke and Erdheim-Chester Disease: A Case Report and Review of Literature.
Fargeot G, Stefanizzi S, Depuydt S, Klapczynski F, Ameri A
J Stroke Cerebrovasc Dis 2017 Aug;26(8):e153-e155. Epub 2017 Jun 13 doi: 10.1016/j.jstrokecerebrovasdis.2017.04.029. PMID: 28623120
Erdheim-Chester disease.
Campochiaro C, Tomelleri A, Cavalli G, Berti A, Dagna L
Eur J Intern Med 2015 May;26(4):223-9. Epub 2015 Apr 10 doi: 10.1016/j.ejim.2015.03.004. PMID: 25865950

Prognosis

Erdheim-Chester disease.
Haroche J, Cohen-Aubart F, Amoura Z
Blood 2020 Apr 16;135(16):1311-1318. doi: 10.1182/blood.2019002766. PMID: 32107533
Association between Ischemic Stroke and Erdheim-Chester Disease: A Case Report and Review of Literature.
Fargeot G, Stefanizzi S, Depuydt S, Klapczynski F, Ameri A
J Stroke Cerebrovasc Dis 2017 Aug;26(8):e153-e155. Epub 2017 Jun 13 doi: 10.1016/j.jstrokecerebrovasdis.2017.04.029. PMID: 28623120
Erdheim-Chester disease.
Campochiaro C, Tomelleri A, Cavalli G, Berti A, Dagna L
Eur J Intern Med 2015 May;26(4):223-9. Epub 2015 Apr 10 doi: 10.1016/j.ejim.2015.03.004. PMID: 25865950
Cardiovascular manifestations of Erdheim-Chester disease.
Berti A, Ferrarini M, Ferrero E, Dagna L
Clin Exp Rheumatol 2015 Mar-Apr;33(2 Suppl 89):S-155-63. Epub 2015 Feb 18 PMID: 25738753
Imaging in Erdheim-Chester disease: classic features and new insights.
Moulis G, Sailler L, Bonneville F, Wagner T
Clin Exp Rheumatol 2014 May-Jun;32(3):410-4. Epub 2014 Jan 14 PMID: 24428974

Clinical prediction guides

Erdheim-Chester disease.
Haroche J, Cohen-Aubart F, Amoura Z
Blood 2020 Apr 16;135(16):1311-1318. doi: 10.1182/blood.2019002766. PMID: 32107533
Cardiovascular manifestations of Erdheim-Chester disease.
Berti A, Ferrarini M, Ferrero E, Dagna L
Clin Exp Rheumatol 2015 Mar-Apr;33(2 Suppl 89):S-155-63. Epub 2015 Feb 18 PMID: 25738753

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