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Refractory Hepatoblastoma

MedGen UID:
1645468
Concept ID:
C4684867
Neoplastic Process

Definition

Hepatoblastoma that does not respond to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Hepatoblastoma

Professional guidelines

PubMed

Espinoza AF, Patel RH, Patel KR, Badachhape AA, Whitlock R, Srivastava RK, Govindu SR, Duong A, Kona A, Kureti P, Armbruster B, Kats D, Srinivasan RR, Dobrolecki LE, Yu X, Najaf Panah MJ, Zorman B, Sarabia SF, Urbicain M, Major A, Bissig KD, Keller C, Lewis MT, Heczey A, Sumazin P, López-Terrada DH, Woodfield SE, Vasudevan SA
J Hepatol 2024 Apr;80(4):610-621. Epub 2024 Jan 17 doi: 10.1016/j.jhep.2024.01.003. PMID: 38242326
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

Recent clinical studies

Etiology

Espinoza AF, Patel RH, Patel KR, Badachhape AA, Whitlock R, Srivastava RK, Govindu SR, Duong A, Kona A, Kureti P, Armbruster B, Kats D, Srinivasan RR, Dobrolecki LE, Yu X, Najaf Panah MJ, Zorman B, Sarabia SF, Urbicain M, Major A, Bissig KD, Keller C, Lewis MT, Heczey A, Sumazin P, López-Terrada DH, Woodfield SE, Vasudevan SA
J Hepatol 2024 Apr;80(4):610-621. Epub 2024 Jan 17 doi: 10.1016/j.jhep.2024.01.003. PMID: 38242326
Levy CF, Oo KZ, Fireman F, Pierre L, Bania MA, Sadanandan S, Yamashiro DJ, Glade Bender JL
Pediatr Blood Cancer 2009 May;52(5):669-71. doi: 10.1002/pbc.21866. PMID: 19101996
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

Diagnosis

Filenko BM *, Starchenko II, Royko NV, Vynnyk NI, Dyachenko LV
Exp Oncol 2020 Sep;42(3):245-247. doi: 10.32471/exp-oncology.2312-8852.vol-42-no-3.14855. PMID: 32996745
Goto H, Kitagawa N, Sekiguchi H, Miyagi Y, Keino D, Sugiyama M, Sarashina T, Miyagawa N, Yokosuka T, Hamanoue S, Iwasaki F, Shiomi M, Goto S, Tanaka Y
J Pediatr Hematol Oncol 2017 Jul;39(5):395-401. doi: 10.1097/MPH.0000000000000865. PMID: 28562516
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

Therapy

Espinoza AF, Patel RH, Patel KR, Badachhape AA, Whitlock R, Srivastava RK, Govindu SR, Duong A, Kona A, Kureti P, Armbruster B, Kats D, Srinivasan RR, Dobrolecki LE, Yu X, Najaf Panah MJ, Zorman B, Sarabia SF, Urbicain M, Major A, Bissig KD, Keller C, Lewis MT, Heczey A, Sumazin P, López-Terrada DH, Woodfield SE, Vasudevan SA
J Hepatol 2024 Apr;80(4):610-621. Epub 2024 Jan 17 doi: 10.1016/j.jhep.2024.01.003. PMID: 38242326
Filenko BM *, Starchenko II, Royko NV, Vynnyk NI, Dyachenko LV
Exp Oncol 2020 Sep;42(3):245-247. doi: 10.32471/exp-oncology.2312-8852.vol-42-no-3.14855. PMID: 32996745
Goto H, Kitagawa N, Sekiguchi H, Miyagi Y, Keino D, Sugiyama M, Sarashina T, Miyagawa N, Yokosuka T, Hamanoue S, Iwasaki F, Shiomi M, Goto S, Tanaka Y
J Pediatr Hematol Oncol 2017 Jul;39(5):395-401. doi: 10.1097/MPH.0000000000000865. PMID: 28562516
George SL, Broster S, Chisholm JC, Brock P
J Pediatr Hematol Oncol 2012 Oct;34(7):e295-7. doi: 10.1097/MPH.0b013e3182441588. PMID: 22469940
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

Prognosis

Filenko BM *, Starchenko II, Royko NV, Vynnyk NI, Dyachenko LV
Exp Oncol 2020 Sep;42(3):245-247. doi: 10.32471/exp-oncology.2312-8852.vol-42-no-3.14855. PMID: 32996745
George SL, Broster S, Chisholm JC, Brock P
J Pediatr Hematol Oncol 2012 Oct;34(7):e295-7. doi: 10.1097/MPH.0b013e3182441588. PMID: 22469940
Miyamura T, Yoshida R, Yagi T, Matsukawa H, Chayama K, Ishida T, Washio K, Morishita N, Oda M, Morishima T
Pediatr Transplant 2011 Aug;15(5):E87-91. Epub 2010 Jan 11 doi: 10.1111/j.1399-3046.2009.01262.x. PMID: 20070564
Levy CF, Oo KZ, Fireman F, Pierre L, Bania MA, Sadanandan S, Yamashiro DJ, Glade Bender JL
Pediatr Blood Cancer 2009 May;52(5):669-71. doi: 10.1002/pbc.21866. PMID: 19101996
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

Clinical prediction guides

Filenko BM *, Starchenko II, Royko NV, Vynnyk NI, Dyachenko LV
Exp Oncol 2020 Sep;42(3):245-247. doi: 10.32471/exp-oncology.2312-8852.vol-42-no-3.14855. PMID: 32996745
Goto H, Kitagawa N, Sekiguchi H, Miyagi Y, Keino D, Sugiyama M, Sarashina T, Miyagawa N, Yokosuka T, Hamanoue S, Iwasaki F, Shiomi M, Goto S, Tanaka Y
J Pediatr Hematol Oncol 2017 Jul;39(5):395-401. doi: 10.1097/MPH.0000000000000865. PMID: 28562516
Matsunaga T, Sasaki F, Ohira M, Hashizume K, Hayashi A, Hayashi Y, Mugishima H, Ohnuma N; Japanese Study Group for Pediatric Liver Tumor
Pediatr Surg Int 2003 May;19(3):142-6. Epub 2003 May 24 doi: 10.1007/s00383-002-0906-0. PMID: 12768314

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