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Hypothalamic-Chiasmatic Pilomyxoid Astrocytoma

MedGen UID:
1663605
•Concept ID:
C4744523
•
Neoplastic Process

Definition

A pilomyxoid astrocytoma occurring in the hypothalamic-chiasmatic region. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVHypothalamic-Chiasmatic Pilomyxoid Astrocytoma

Professional guidelines

PubMed

Successful treatment with a low-dose cisplatin--etoposide regimen for patients with diencephalic syndrome.
Sardi I, Bresci C, Schiavello E, Biassoni V, Fratoni V, Cardellicchio S, Genitori L, Aricò M, Massimino M
J Neurooncol 2012 Sep;109(2):375-83. Epub 2012 Jun 21 doi: 10.1007/s11060-012-0903-7. PMID: 22717669

Recent clinical studies

Etiology

A rare case of cerebellar pilomyxoid astrocytoma associated with neurofibromatosis-1 in a young female; case report highlighting immunohistochemical features.
Sinai Khandeparkar SG, Gosavi SS, Gogate BP, Talathi N
Indian J Pathol Microbiol 2021 Apr-Jun;64(2):354-357. doi: 10.4103/IJPM.IJPM_209_20. PMID: 33851634
Intermediate pilomyxoid astrocytoma and diencephalic syndrome: imaging findings.
Nakamura OK, Pinho Mda C, Odone Filho V, Rosemberg S
Einstein (Sao Paulo) 2012 Apr-Jun;10(2):236-8. doi: 10.1590/s1679-45082012000200020. PMID: 23052462
Pilomyxoid astrocytoma of the cerebellum.
Ajani OA, Al Sulaiti G, Al Bozom I
J Neurosurg Pediatr 2011 May;7(5):539-42. doi: 10.3171/2011.2.PEDS10314. PMID: 21529196
Pilomyxoid astrocytoma of the cervical spinal cord in a child with rapid progression into glioblastoma: case report and literature review.
Paraskevopoulos D, Patsalas I, Karkavelas G, Foroglou N, Magras I, Selviaridis P
Childs Nerv Syst 2011 Feb;27(2):313-21. Epub 2010 May 12 doi: 10.1007/s00381-010-1171-5. PMID: 20461521
Pilocytic and pilomyxoid hypothalamic/chiasmatic astrocytomas.
Komotar RJ, Burger PC, Carson BS, Brem H, Olivi A, Goldthwaite PT, Tihan T
Neurosurgery 2004 Jan;54(1):72-9; discussion 79-80. doi: 10.1227/01.neu.0000097266.89676.25. PMID: 14683543

Diagnosis

A rare case of cerebellar pilomyxoid astrocytoma associated with neurofibromatosis-1 in a young female; case report highlighting immunohistochemical features.
Sinai Khandeparkar SG, Gosavi SS, Gogate BP, Talathi N
Indian J Pathol Microbiol 2021 Apr-Jun;64(2):354-357. doi: 10.4103/IJPM.IJPM_209_20. PMID: 33851634
Pediatric cerebellar pilomyxoid-spectrum astrocytomas.
Forbes JA, Mobley BC, O'Lynnger TM, Cooper CM, Ghiassi M, Hanif R, Pearson MM
J Neurosurg Pediatr 2011 Jul;8(1):90-6. doi: 10.3171/2011.4.PEDS1115. PMID: 21721894Free PMC Article
Pilomyxoid astrocytoma of the cerebellum.
Ajani OA, Al Sulaiti G, Al Bozom I
J Neurosurg Pediatr 2011 May;7(5):539-42. doi: 10.3171/2011.2.PEDS10314. PMID: 21529196
Pilomyxoid astrocytoma with involvement of the sella turcica in an adolescent.
Alimohamadi M, Bidabadi MS, Ayan Z, Ketabchi E, Amirjamshidi A
J Clin Neurosci 2009 Dec;16(12):1648-9. Epub 2009 Sep 17 doi: 10.1016/j.jocn.2009.01.035. PMID: 19766001
Pilocytic and pilomyxoid hypothalamic/chiasmatic astrocytomas.
Komotar RJ, Burger PC, Carson BS, Brem H, Olivi A, Goldthwaite PT, Tihan T
Neurosurgery 2004 Jan;54(1):72-9; discussion 79-80. doi: 10.1227/01.neu.0000097266.89676.25. PMID: 14683543

Therapy

Sustained response to weekly vinblastine in 2 children with pilomyxoid astrocytoma associated with diencephalic syndrome.
Singh G, Wei XC, Hader W, Chan JA, Bouffet E, Lafay-Cousin L
J Pediatr Hematol Oncol 2013 Mar;35(2):e53-6. doi: 10.1097/MPH.0b013e3182707e67. PMID: 23042016
Successful treatment with a low-dose cisplatin--etoposide regimen for patients with diencephalic syndrome.
Sardi I, Bresci C, Schiavello E, Biassoni V, Fratoni V, Cardellicchio S, Genitori L, Aricò M, Massimino M
J Neurooncol 2012 Sep;109(2):375-83. Epub 2012 Jun 21 doi: 10.1007/s11060-012-0903-7. PMID: 22717669

Prognosis

A rare case of cerebellar pilomyxoid astrocytoma associated with neurofibromatosis-1 in a young female; case report highlighting immunohistochemical features.
Sinai Khandeparkar SG, Gosavi SS, Gogate BP, Talathi N
Indian J Pathol Microbiol 2021 Apr-Jun;64(2):354-357. doi: 10.4103/IJPM.IJPM_209_20. PMID: 33851634
Pediatric cerebellar pilomyxoid-spectrum astrocytomas.
Forbes JA, Mobley BC, O'Lynnger TM, Cooper CM, Ghiassi M, Hanif R, Pearson MM
J Neurosurg Pediatr 2011 Jul;8(1):90-6. doi: 10.3171/2011.4.PEDS1115. PMID: 21721894Free PMC Article
Pilomyxoid astrocytoma of the cerebellum.
Ajani OA, Al Sulaiti G, Al Bozom I
J Neurosurg Pediatr 2011 May;7(5):539-42. doi: 10.3171/2011.2.PEDS10314. PMID: 21529196
Pilomyxoid astrocytoma with involvement of the sella turcica in an adolescent.
Alimohamadi M, Bidabadi MS, Ayan Z, Ketabchi E, Amirjamshidi A
J Clin Neurosci 2009 Dec;16(12):1648-9. Epub 2009 Sep 17 doi: 10.1016/j.jocn.2009.01.035. PMID: 19766001
Pilocytic and pilomyxoid hypothalamic/chiasmatic astrocytomas.
Komotar RJ, Burger PC, Carson BS, Brem H, Olivi A, Goldthwaite PT, Tihan T
Neurosurgery 2004 Jan;54(1):72-9; discussion 79-80. doi: 10.1227/01.neu.0000097266.89676.25. PMID: 14683543

Clinical prediction guides

Successful treatment with a low-dose cisplatin--etoposide regimen for patients with diencephalic syndrome.
Sardi I, Bresci C, Schiavello E, Biassoni V, Fratoni V, Cardellicchio S, Genitori L, Aricò M, Massimino M
J Neurooncol 2012 Sep;109(2):375-83. Epub 2012 Jun 21 doi: 10.1007/s11060-012-0903-7. PMID: 22717669
Occipital pilomyxoid astrocytoma in a 14-year-old girl--case report.
Buccoliero AM, Gheri CF, Maio V, Moncini D, Castiglione F, Garbini F, Sanzo M, Taddei A, Genitori L, Taddei GL
Clin Neuropathol 2008 Nov-Dec;27(6):373-7. doi: 10.5414/npp27373. PMID: 19130733

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