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Refractory Visual Pathway Glioma

MedGen UID:
1667706
•Concept ID:
C4744487
•
Neoplastic Process

Definition

Visual pathway glioma that is resistant to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Visual Pathway Glioma

Professional guidelines

PubMed

Novel "T-Dimension" Therapies for Pediatric Optic Pathway Glioma: A Timely, Targeted, and Tailored Treatment Trend.
Giotta Lucifero A, Elbabaa SK, Baldoncini M, Bruno N, Savasta S, Marseglia GL, Luzzi S
Pediatr Neurosurg 2022;57(3):161-174. Epub 2022 May 4 doi: 10.1159/000524873. PMID: 35588700
Risk factors for treatment-refractory and relapsed optic pathway glioma in children with neurofibromatosis type 1.
Kotch C, Avery R, Getz KD, Bouffet E, de Blank P, Listernick R, Gutmann DH, Bornhorst M, Campen C, Liu GT, Aplenc R, Li Y, Fisher MJ
Neuro Oncol 2022 Aug 1;24(8):1377-1386. doi: 10.1093/neuonc/noac013. PMID: 35018469Free PMC Article

Recent clinical studies

Etiology

Brain Tumors in Adolescents and Young Adults: A Review.
Rousseau J, Bennett J, Lim-Fat MJ
Semin Neurol 2023 Dec;43(6):909-928. Epub 2023 Nov 10 doi: 10.1055/s-0043-1776775. PMID: 37949116
Paediatric Strategy Forum for medicinal product development in mitogen-activated protein kinase pathway inhibitors: ACCELERATE in collaboration with the European Medicines Agency with participation of the Food and Drug Administration.
Pearson AD, Allen C, Fangusaro J, Hutter C, Witt O, Weiner S, Reaman G, Russo M, Bandopadhayay P, Ahsan S, Barone A, Barry E, de Rojas T, Fisher M, Fox E, Bender JG, Gore L, Hargrave D, Hawkins D, Kreider B, Langseth AJ, Lesa G, Ligas F, Marotti M, Marshall LV, Nasri K, Norga K, Nysom K, Pappo A, Rossato G, Scobie N, Smith M, Stieglitz E, Weigel B, Weinstein A, Viana R, Karres D, Vassal G
Eur J Cancer 2022 Dec;177:120-142. Epub 2022 Oct 14 doi: 10.1016/j.ejca.2022.09.036. PMID: 36335782
Risk factors for treatment-refractory and relapsed optic pathway glioma in children with neurofibromatosis type 1.
Kotch C, Avery R, Getz KD, Bouffet E, de Blank P, Listernick R, Gutmann DH, Bornhorst M, Campen C, Liu GT, Aplenc R, Li Y, Fisher MJ
Neuro Oncol 2022 Aug 1;24(8):1377-1386. doi: 10.1093/neuonc/noac013. PMID: 35018469Free PMC Article

Diagnosis

Brain Tumors in Adolescents and Young Adults: A Review.
Rousseau J, Bennett J, Lim-Fat MJ
Semin Neurol 2023 Dec;43(6):909-928. Epub 2023 Nov 10 doi: 10.1055/s-0043-1776775. PMID: 37949116
Marked functional recovery and imaging response of refractory optic pathway glioma to BRAFV600E inhibitor therapy: a report of two cases.
Upadhyaya SA, Robinson GW, Harreld JH, Klimo PD Jr, Hoehn ME, Orr BA, Qaddoumi IA
Childs Nerv Syst 2018 Apr;34(4):605-610. Epub 2018 Feb 1 doi: 10.1007/s00381-018-3739-4. PMID: 29392423Free PMC Article

Therapy

Paediatric Strategy Forum for medicinal product development in mitogen-activated protein kinase pathway inhibitors: ACCELERATE in collaboration with the European Medicines Agency with participation of the Food and Drug Administration.
Pearson AD, Allen C, Fangusaro J, Hutter C, Witt O, Weiner S, Reaman G, Russo M, Bandopadhayay P, Ahsan S, Barone A, Barry E, de Rojas T, Fisher M, Fox E, Bender JG, Gore L, Hargrave D, Hawkins D, Kreider B, Langseth AJ, Lesa G, Ligas F, Marotti M, Marshall LV, Nasri K, Norga K, Nysom K, Pappo A, Rossato G, Scobie N, Smith M, Stieglitz E, Weigel B, Weinstein A, Viana R, Karres D, Vassal G
Eur J Cancer 2022 Dec;177:120-142. Epub 2022 Oct 14 doi: 10.1016/j.ejca.2022.09.036. PMID: 36335782
Novel "T-Dimension" Therapies for Pediatric Optic Pathway Glioma: A Timely, Targeted, and Tailored Treatment Trend.
Giotta Lucifero A, Elbabaa SK, Baldoncini M, Bruno N, Savasta S, Marseglia GL, Luzzi S
Pediatr Neurosurg 2022;57(3):161-174. Epub 2022 May 4 doi: 10.1159/000524873. PMID: 35588700
Marked functional recovery and imaging response of refractory optic pathway glioma to BRAFV600E inhibitor therapy: a report of two cases.
Upadhyaya SA, Robinson GW, Harreld JH, Klimo PD Jr, Hoehn ME, Orr BA, Qaddoumi IA
Childs Nerv Syst 2018 Apr;34(4):605-610. Epub 2018 Feb 1 doi: 10.1007/s00381-018-3739-4. PMID: 29392423Free PMC Article

Prognosis

Novel "T-Dimension" Therapies for Pediatric Optic Pathway Glioma: A Timely, Targeted, and Tailored Treatment Trend.
Giotta Lucifero A, Elbabaa SK, Baldoncini M, Bruno N, Savasta S, Marseglia GL, Luzzi S
Pediatr Neurosurg 2022;57(3):161-174. Epub 2022 May 4 doi: 10.1159/000524873. PMID: 35588700

Clinical prediction guides

Brain Tumors in Adolescents and Young Adults: A Review.
Rousseau J, Bennett J, Lim-Fat MJ
Semin Neurol 2023 Dec;43(6):909-928. Epub 2023 Nov 10 doi: 10.1055/s-0043-1776775. PMID: 37949116

Recent systematic reviews

Novel "T-Dimension" Therapies for Pediatric Optic Pathway Glioma: A Timely, Targeted, and Tailored Treatment Trend.
Giotta Lucifero A, Elbabaa SK, Baldoncini M, Bruno N, Savasta S, Marseglia GL, Luzzi S
Pediatr Neurosurg 2022;57(3):161-174. Epub 2022 May 4 doi: 10.1159/000524873. PMID: 35588700

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