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Refractory Monomorphic Epitheliotropic Intestinal T-cell Lymphoma

MedGen UID:
1677472
•Concept ID:
C4763798
•
Neoplastic Process

Definition

Monomorphic epitheliotropic intestinal T-cell lymphoma that is resistant to treatment. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVRefractory Monomorphic Epitheliotropic Intestinal T-cell Lymphoma

Recent clinical studies

Etiology

T- and NK-cell lymphoproliferative disorders of the gastrointestinal tract: review and update.
van Vliet C, Spagnolo DV
Pathology 2020 Jan;52(1):128-141. Epub 2019 Nov 11 doi: 10.1016/j.pathol.2019.10.001. PMID: 31727264

Diagnosis

T- and NK-cell lymphoproliferative disorders of the gastrointestinal tract: review and update.
van Vliet C, Spagnolo DV
Pathology 2020 Jan;52(1):128-141. Epub 2019 Nov 11 doi: 10.1016/j.pathol.2019.10.001. PMID: 31727264
Two cases of monomorphic epitheliotropic intestinal T-cell lymphoma associated with coeliac disease.
Lenti MV, Biagi F, Lucioni M, Di Sabatino A, Paulli M, Corazza GR
Scand J Gastroenterol 2019 Aug;54(8):965-968. Epub 2019 Jul 30 doi: 10.1080/00365521.2019.1647455. PMID: 31361171
NKp46 is a diagnostic biomarker and may be a therapeutic target in gastrointestinal T-cell lymphoproliferative diseases: a CELAC study.
Cheminant M, Bruneau J, Malamut G, Sibon D, Guegan N, van Gils T, Cording S, Trinquand A, Verkarre V, Lhermitte L, Brousse N, Jannot AS, Khater S, Frenzel L, Delarue R, Suarez F, Marçais A, Mulder CJ, Macintyre E, Asnafi V, Pouyet L, Bonnafous C, Lhospice F, Molina TJ, Meresse B, Cellier C, Cerf-Bensussan N, Hermine O; CELAC network°
Gut 2019 Aug;68(8):1396-1405. Epub 2018 Nov 17 doi: 10.1136/gutjnl-2018-317371. PMID: 30448772

Therapy

PEG-Asparaginase Single-Agent Rescue in an Advanced Case of Monomorphic Epitheliotropic Intestinal T Cell Lymphoma.
Barbieri E, Pozzi S, Gelmini R, Roncati L, Maccaferri M, Potenza L, Marasca R, Luppi M, Leonardi G
J Gastrointest Cancer 2023 Mar;54(1):304-308. Epub 2022 Mar 1 doi: 10.1007/s12029-022-00808-0. PMID: 35230648
Enteropathy-Associated T-Cell Lymphoma.
Ondrejka S, Jagadeesh D
Curr Hematol Malig Rep 2016 Dec;11(6):504-513. doi: 10.1007/s11899-016-0357-7. PMID: 27900603

Prognosis

PEG-Asparaginase Single-Agent Rescue in an Advanced Case of Monomorphic Epitheliotropic Intestinal T Cell Lymphoma.
Barbieri E, Pozzi S, Gelmini R, Roncati L, Maccaferri M, Potenza L, Marasca R, Luppi M, Leonardi G
J Gastrointest Cancer 2023 Mar;54(1):304-308. Epub 2022 Mar 1 doi: 10.1007/s12029-022-00808-0. PMID: 35230648
T- and NK-cell lymphoproliferative disorders of the gastrointestinal tract: review and update.
van Vliet C, Spagnolo DV
Pathology 2020 Jan;52(1):128-141. Epub 2019 Nov 11 doi: 10.1016/j.pathol.2019.10.001. PMID: 31727264
NKp46 is a diagnostic biomarker and may be a therapeutic target in gastrointestinal T-cell lymphoproliferative diseases: a CELAC study.
Cheminant M, Bruneau J, Malamut G, Sibon D, Guegan N, van Gils T, Cording S, Trinquand A, Verkarre V, Lhermitte L, Brousse N, Jannot AS, Khater S, Frenzel L, Delarue R, Suarez F, Marçais A, Mulder CJ, Macintyre E, Asnafi V, Pouyet L, Bonnafous C, Lhospice F, Molina TJ, Meresse B, Cellier C, Cerf-Bensussan N, Hermine O; CELAC network°
Gut 2019 Aug;68(8):1396-1405. Epub 2018 Nov 17 doi: 10.1136/gutjnl-2018-317371. PMID: 30448772
Enteropathy-Associated T-Cell Lymphoma.
Ondrejka S, Jagadeesh D
Curr Hematol Malig Rep 2016 Dec;11(6):504-513. doi: 10.1007/s11899-016-0357-7. PMID: 27900603

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