Bladder PEComa

MedGen UID:: 1697229
•Concept ID:: C5204615
•: Neoplastic Process

Synonym:

Bladder Perivascular Epithelioid Cell Tumor

Definition

A benign or malignant perivascular epithelioid cell tumor arising from the bladder. [from NCI]

Term Hierarchy

GTR
MeSH

CClinical test, RResearch test, OOMIM, GGeneReviews, VClinVar

CROGVBladder PEComa

Disorder by Site
- Disorder of the genitourinary system
  - Urinary system disorder
    - Urinary bladder disorder
      - Bladder neoplasm
        Bladder Soft Tissue Neoplasm
        Bladder PEComa
        Bladder Benign PEComa
        Bladder Malignant PEComa

Recent clinical studies

Etiology

Bladder perivascular epithelioid cell tumor: a novel rare neoplasm.

Kyrou D, Staios D, Papatsoris AG
Urol Int 2012;88(4):480-2. Epub 2011 Nov 15 doi: 10.1159/000332199. PMID: 22094379

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Diagnosis

Transurethral en bloc resection of a bladder perivascular epithelioid cell tumor (PEComa): a case report.

Zeng SP, Sun YF, Ye JB, Zeng K, Li XB
BMC Urol 2023 Mar 2;23(1):28. doi: 10.1186/s12894-023-01198-6. PMID: 36864398 Free PMC Article

Bladder perivascular epithelioid cell tumour and tuberous sclerosis complex: a rare association.

Tee JL, Chambers J, Strutton G
BMJ Case Rep 2021 May 26;14(5) doi: 10.1136/bcr-2021-241635. PMID: 34039545 Free PMC Article

Perivascular Epithelioid Cell Tumor of Urinary Bladder.

Wu YL, Lang L, Ma Q, Wu F, Zhang Y, Chen W, Yan XC, Duan GJ
Am J Clin Pathol 2021 Jun 17;156(1):56-71. doi: 10.1093/ajcp/aqaa204. PMID: 33336255

Perivascular Epithelioid Cell Tumor of the Urinary Bladder: A Systematic Review.

Hamza A, Guo CC
Int J Surg Pathol 2020 Jun;28(4):393-400. Epub 2019 Dec 22 doi: 10.1177/1066896919895810. PMID: 31865807

Bladder perivascular epithelioid cell tumor (PEComa): a case report and literature review.

Sarti A, Rubilotta E, Balzarro M, Cerruto MA, Brunelli M, Artibani W
Urologia 2015 Apr-Jun;82(2):120-3. Epub 2014 Jan 28 doi: 10.5301/urologia.5000045. PMID: 24557821

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Prognosis

Bladder perivascular epithelioid cell tumour and tuberous sclerosis complex: a rare association.

Tee JL, Chambers J, Strutton G
BMJ Case Rep 2021 May 26;14(5) doi: 10.1136/bcr-2021-241635. PMID: 34039545 Free PMC Article

Perivascular Epithelioid Cell Tumor of Urinary Bladder.

Wu YL, Lang L, Ma Q, Wu F, Zhang Y, Chen W, Yan XC, Duan GJ
Am J Clin Pathol 2021 Jun 17;156(1):56-71. doi: 10.1093/ajcp/aqaa204. PMID: 33336255

Perivascular Epithelioid Cell Tumor of the Urinary Bladder: A Systematic Review.

Hamza A, Guo CC
Int J Surg Pathol 2020 Jun;28(4):393-400. Epub 2019 Dec 22 doi: 10.1177/1066896919895810. PMID: 31865807

TFE3-Expressing Epithelioid Rich Perivascular Epithelioid Cell Neoplasm (PEComa) of the Bladder with Unusual Benign Course.

Chen XF, Yeong J, Chang KTE, Lim AST, Kuick CH, Lim TH, Sudhanshi J, Selvarajan S, Gan VHL, Khor LY
Ann Clin Lab Sci 2018 Jan;48(1):110-115. PMID: 29531006

Malignant perivascular epithelioid cell neoplasm (PEComa) of the urinary bladder with TFE3 gene rearrangement: clinicopathologic, immunohistochemical, and molecular features.

Williamson SR, Bunde PJ, Montironi R, Lopez-Beltran A, Zhang S, Wang M, Maclennan GT, Cheng L
Am J Surg Pathol 2013 Oct;37(10):1619-26. doi: 10.1097/PAS.0b013e318293729d. PMID: 23797724

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