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EBV-Related Leiomyosarcoma

MedGen UID:
1700409
Concept ID:
C5206511
Neoplastic Process
Synonyms: EBV-Associated Leiomyosarcoma; Epstein-Barr Virus-Associated Leiomyosarcoma; Epstein-Barr Virus-Related Leiomyosarcoma

Definition

Leiomyosarcoma that is caused by Epstein-Barr virus infection. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVEBV-Related Leiomyosarcoma

Recent clinical studies

Etiology

Jonigk D, Laenger F, Maegel L, Izykowski N, Rische J, Tiede C, Klein C, Maecker-Kolhoff B, Kreipe H, Hussein K
Am J Transplant 2012 Jul;12(7):1908-17. Epub 2012 Mar 15 doi: 10.1111/j.1600-6143.2012.04011.x. PMID: 22420456
Hsu JL, Glaser SL
Crit Rev Oncol Hematol 2000 Apr;34(1):27-53. doi: 10.1016/s1040-8428(00)00046-9. PMID: 10781747

Diagnosis

Chaves NJ, Kotsimbos TC, Warren MA, McLean CA, Spelman DW, Williams TJ, Snell GI, Westall GP
J Heart Lung Transplant 2007 Jul;26(7):753-5. doi: 10.1016/j.healun.2007.05.007. PMID: 17613410
McClain KL, Leach CT, Jenson HB, Joshi VV, Pollock BH, Parmley RT, DiCarlo FJ, Chadwick EG, Murphy SB
N Engl J Med 1995 Jan 5;332(1):12-8. doi: 10.1056/NEJM199501053320103. PMID: 7990860

Therapy

Jonigk D, Laenger F, Maegel L, Izykowski N, Rische J, Tiede C, Klein C, Maecker-Kolhoff B, Kreipe H, Hussein K
Am J Transplant 2012 Jul;12(7):1908-17. Epub 2012 Mar 15 doi: 10.1111/j.1600-6143.2012.04011.x. PMID: 22420456
Chaves NJ, Kotsimbos TC, Warren MA, McLean CA, Spelman DW, Williams TJ, Snell GI, Westall GP
J Heart Lung Transplant 2007 Jul;26(7):753-5. doi: 10.1016/j.healun.2007.05.007. PMID: 17613410

Prognosis

Jonigk D, Laenger F, Maegel L, Izykowski N, Rische J, Tiede C, Klein C, Maecker-Kolhoff B, Kreipe H, Hussein K
Am J Transplant 2012 Jul;12(7):1908-17. Epub 2012 Mar 15 doi: 10.1111/j.1600-6143.2012.04011.x. PMID: 22420456
Hsu JL, Glaser SL
Crit Rev Oncol Hematol 2000 Apr;34(1):27-53. doi: 10.1016/s1040-8428(00)00046-9. PMID: 10781747

Supplemental Content

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