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Medulloepithelioma

MedGen UID:
1702218
Concept ID:
C5231013
Neoplastic Process
Synonyms: Medulloepithelioma of central nervous system; Medulloepithelioma of the central nervous system
SNOMED CT: Medulloepithelioma of central nervous system (818967003)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
HPO: HP:0030071
Monarch Initiative: MONDO:0003144
Orphanet: ORPHA251883

Definition

A primitive neuroectodermal tumor that originates from the cells of the embryonic medullary canal. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Camp DA, Yadav P, Dalvin LA, Shields CL
Curr Opin Ophthalmol 2019 Mar;30(2):71-81. doi: 10.1097/ICU.0000000000000550. PMID: 30562240
Sin-Chan P, Li BK, Ho B, Fonseca A, Huang A
Curr Oncol Rep 2018 Jul 11;20(9):69. doi: 10.1007/s11912-018-0717-7. PMID: 29995179

Recent clinical studies

Etiology

Nambirajan A, Gurung N, Suri V, Sarkar C, Kumar A, Singh M, Sharma MC
Childs Nerv Syst 2021 Apr;37(4):1067-1075. Epub 2020 Nov 24 doi: 10.1007/s00381-020-04973-0. PMID: 33236184
Mudhar HS, Milman T, Eagle RC Jr, Sanderson T, Pheasey L, Paine S, Salvi S, Rennie IG, Rundle P, Shields CL, Shields JA
Ophthalmology 2021 May;128(5):765-778. Epub 2020 Sep 29 doi: 10.1016/j.ophtha.2020.09.033. PMID: 33002562
Hořínová V, Drábová K, Nosková H, Bajčiová V, Šoukalová J, Černá L, Hůrková V, Slabý O, Štěrba J
Klin Onkol 2019 Summer;32(Supplementum2):123-127. doi: 10.14735/amko2019S123. PMID: 31409088
Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article

Diagnosis

Bailey D, Mau C, Toepke C, Finch E, Rizk E
Childs Nerv Syst 2022 Jul;38(7):1259-1266. Epub 2022 Apr 27 doi: 10.1007/s00381-022-05525-4. PMID: 35474542
Guillerman RP, Foulkes WD, Priest JR
Pediatr Radiol 2019 Oct;49(11):1488-1505. Epub 2019 Oct 16 doi: 10.1007/s00247-019-04429-x. PMID: 31620849
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Saunders T, Margo CE
Arch Pathol Lab Med 2012 Feb;136(2):212-6. doi: 10.5858/arpa.2010-0669-RS. PMID: 22288972
Canning CR, McCartney AC, Hungerford J
Br J Ophthalmol 1988 Oct;72(10):764-7. doi: 10.1136/bjo.72.10.764. PMID: 3056510Free PMC Article

Therapy

Sheriff IHN, Karaa EK, Chowdhury T, Scheimberg I, Duncan C, Reddy MA, Sagoo MS
Eye (Lond) 2023 Apr;37(5):947-952. Epub 2022 Feb 1 doi: 10.1038/s41433-022-01936-4. PMID: 35105935Free PMC Article
Stathopoulos C, Gaillard MC, Schneider J, Munier FL
BMC Ophthalmol 2020 Jun 18;20(1):239. doi: 10.1186/s12886-020-01512-y. PMID: 32552699Free PMC Article
Camp DA, Yadav P, Dalvin LA, Shields CL
Curr Opin Ophthalmol 2019 Mar;30(2):71-81. doi: 10.1097/ICU.0000000000000550. PMID: 30562240
Jain V, Dabir S, Shome D, Dadu T, Natarajan S
Surv Ophthalmol 2009 Mar-Apr;54(2):286-91. doi: 10.1016/j.survophthal.2008.12.008. PMID: 19298905
Sayed BA, Sahgal KN, Desai VK
Br J Ophthalmol 1962 Jan;46(1):58-60. doi: 10.1136/bjo.46.1.58. PMID: 18170756Free PMC Article

Prognosis

González IA, Stewart DR, Schultz KAP, Field AP, Hill DA, Dehner LP
Mod Pathol 2022 Jan;35(1):4-22. Epub 2021 Oct 1 doi: 10.1038/s41379-021-00905-8. PMID: 34599283Free PMC Article
Sin-Chan P, Li BK, Ho B, Fonseca A, Huang A
Curr Oncol Rep 2018 Jul 11;20(9):69. doi: 10.1007/s11912-018-0717-7. PMID: 29995179
Saunders T, Margo CE
Arch Pathol Lab Med 2012 Feb;136(2):212-6. doi: 10.5858/arpa.2010-0669-RS. PMID: 22288972
MacDonald TJ
J Child Neurol 2008 Oct;23(10):1195-204. doi: 10.1177/0883073808321769. PMID: 18952586Free PMC Article
Morovic A, Damjanov I
Histol Histopathol 2008 Jun;23(6):765-71. doi: 10.14670/HH-23.765. PMID: 18366014

Clinical prediction guides

Mudhar HS, Milman T, Eagle RC Jr, Sanderson T, Pheasey L, Paine S, Salvi S, Rennie IG, Rundle P, Shields CL, Shields JA
Ophthalmology 2021 May;128(5):765-778. Epub 2020 Sep 29 doi: 10.1016/j.ophtha.2020.09.033. PMID: 33002562
Guillerman RP, Foulkes WD, Priest JR
Pediatr Radiol 2019 Oct;49(11):1488-1505. Epub 2019 Oct 16 doi: 10.1007/s00247-019-04429-x. PMID: 31620849
Hořínová V, Drábová K, Nosková H, Bajčiová V, Šoukalová J, Černá L, Hůrková V, Slabý O, Štěrba J
Klin Onkol 2019 Summer;32(Supplementum2):123-127. doi: 10.14735/amko2019S123. PMID: 31409088
Huryn LA, Turriff A, Harney LA, Carr AG, Chevez-Barrios P, Gombos DS, Ram R, Hufnagel RB, Hill DA, Zein WM, Schultz KAP, Bishop R, Stewart DR
Ophthalmology 2019 Feb;126(2):296-304. Epub 2018 Oct 17 doi: 10.1016/j.ophtha.2018.09.038. PMID: 30339877Free PMC Article
Shields JA, Eagle RC Jr, Ferguson K, Shields CL
Retina 2015 May;35(5):957-65. doi: 10.1097/IAE.0000000000000445. PMID: 25545484

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