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Medulloepithelioma

MedGen UID:
1702218
Concept ID:
C5231013
Neoplastic Process
Synonyms: Medulloepithelioma of central nervous system; Medulloepithelioma of the central nervous system
SNOMED CT: Medulloepithelioma of central nervous system (818967003)
Modes of inheritance:
Not genetically inherited
MedGen UID:
988794
Concept ID:
CN307044
Finding
Source: Orphanet
clinical entity without genetic inheritance.
 
HPO: HP:0030071
Monarch Initiative: MONDO:0003144
Orphanet: ORPHA251883

Definition

A primitive neuroectodermal tumor that originates from the cells of the embryonic medullary canal. [from HPO]

Term Hierarchy

Professional guidelines

PubMed

Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Sin-Chan P, Li BK, Ho B, Fonseca A, Huang A
Curr Oncol Rep 2018 Jul 11;20(9):69. doi: 10.1007/s11912-018-0717-7. PMID: 29995179
Poon DS, Reich E, Smith VM, Kingston J, Reddy MA, Hungerford JL, Sagoo MS
Ophthalmology 2015 Sep;122(9):1949-51. Epub 2015 Apr 8 doi: 10.1016/j.ophtha.2015.03.002. PMID: 25863421

Recent clinical studies

Etiology

Hořínová V, Drábová K, Nosková H, Bajčiová V, Šoukalová J, Černá L, Hůrková V, Slabý O, Štěrba J
Klin Onkol 2019 Summer;32(Supplementum2):123-127. doi: 10.14735/amko2019S123. PMID: 31409088
Tadepalli SH, Shields CL, Shields JA, Honavar SG
Indian J Ophthalmol 2019 Jun;67(6):755-762. doi: 10.4103/ijo.IJO_845_19. PMID: 31124483Free PMC Article
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Essuman VA, Tagoe NN, Ndanu TA, Ntim-Amponsah CT
Ghana Med J 2014 Dec;48(4):204-7. doi: 10.4314/gmj.v48i4.6. PMID: 25709135Free PMC Article
Müller K, Zwiener I, Welker H, Maass E, Bongartz R, Berthold F, Pietsch T, Warmuth-Metz M, von Bueren A, Rutkowski S
Strahlenther Onkol 2011 Nov;187(11):757-62. Epub 2011 Oct 28 doi: 10.1007/s00066-011-2256-0. PMID: 22037651

Diagnosis

Barchitta M, De Francesco S, Menicacci C, Girolamo MM, Salvoldi F, Hadjistilianou D
Eur J Ophthalmol 2022 Nov;32(6):NP73-NP77. Epub 2021 May 31 doi: 10.1177/11206721211019579. PMID: 34053319
Schultz KAP, Williams GM, Kamihara J, Stewart DR, Harris AK, Bauer AJ, Turner J, Shah R, Schneider K, Schneider KW, Carr AG, Harney LA, Baldinger S, Frazier AL, Orbach D, Schneider DT, Malkin D, Dehner LP, Messinger YH, Hill DA
Clin Cancer Res 2018 May 15;24(10):2251-2261. Epub 2018 Jan 17 doi: 10.1158/1078-0432.CCR-17-3089. PMID: 29343557Free PMC Article
Brennan RC, Wilson MW, Kaste S, Helton KJ, McCarville MB
Pediatr Radiol 2012 Jun;42(6):738-49. Epub 2012 Mar 31 doi: 10.1007/s00247-012-2374-6. PMID: 22466750Free PMC Article
Saunders T, Margo CE
Arch Pathol Lab Med 2012 Feb;136(2):212-6. doi: 10.5858/arpa.2010-0669-RS. PMID: 22288972
Morovic A, Damjanov I
Histol Histopathol 2008 Jun;23(6):765-71. doi: 10.14670/HH-23.765. PMID: 18366014

Therapy

Thottian AG, Benson R, Kashyap S, Haresh KP, Gupta S, Sharma D, Rath GK
Orbit 2016 Dec;35(6):313-316. Epub 2016 Aug 12 doi: 10.1080/01676830.2016.1193536. PMID: 27715363
Poon DS, Reich E, Smith VM, Kingston J, Reddy MA, Hungerford JL, Sagoo MS
Ophthalmology 2015 Sep;122(9):1949-51. Epub 2015 Apr 8 doi: 10.1016/j.ophtha.2015.03.002. PMID: 25863421
Moftakhar P, Fan X, Hurvitz CH, Black KL, Danielpour M
J Neurosurg Pediatr 2008 Nov;2(5):339-45. doi: 10.3171/PED.2008.2.11.349. PMID: 18976104
Lumbroso L, Desjardins L, Coue O, Ducourneau Y, Pechereau A
Arch Ophthalmol 2001 Mar;119(3):449-50. PMID: 11231783
Sayed BA, Sahgal KN, Desai VK
Br J Ophthalmol 1962 Jan;46(1):58-60. doi: 10.1136/bjo.46.1.58. PMID: 18170756Free PMC Article

Prognosis

González IA, Stewart DR, Schultz KAP, Field AP, Hill DA, Dehner LP
Mod Pathol 2022 Jan;35(1):4-22. Epub 2021 Oct 1 doi: 10.1038/s41379-021-00905-8. PMID: 34599283Free PMC Article
Stagner AM, Jakobiec FA
Semin Ophthalmol 2016;31(1-2):188-96. doi: 10.3109/08820538.2015.1115257. PMID: 26959146
Saunders T, Margo CE
Arch Pathol Lab Med 2012 Feb;136(2):212-6. doi: 10.5858/arpa.2010-0669-RS. PMID: 22288972
Morovic A, Damjanov I
Histol Histopathol 2008 Jun;23(6):765-71. doi: 10.14670/HH-23.765. PMID: 18366014
Pang LM, Roebuck DJ, Ng HK, Chan YL
Pediatr Radiol 2001 Aug;31(8):594-6. doi: 10.1007/s002470100495. PMID: 11550774

Clinical prediction guides

Mudhar HS, Milman T, Eagle RC Jr, Sanderson T, Pheasey L, Paine S, Salvi S, Rennie IG, Rundle P, Shields CL, Shields JA
Ophthalmology 2021 May;128(5):765-778. Epub 2020 Sep 29 doi: 10.1016/j.ophtha.2020.09.033. PMID: 33002562
Guillerman RP, Foulkes WD, Priest JR
Pediatr Radiol 2019 Oct;49(11):1488-1505. Epub 2019 Oct 16 doi: 10.1007/s00247-019-04429-x. PMID: 31620849
Hořínová V, Drábová K, Nosková H, Bajčiová V, Šoukalová J, Černá L, Hůrková V, Slabý O, Štěrba J
Klin Onkol 2019 Summer;32(Supplementum2):123-127. doi: 10.14735/amko2019S123. PMID: 31409088
Shields JA, Eagle RC Jr, Ferguson K, Shields CL
Retina 2015 May;35(5):957-65. doi: 10.1097/IAE.0000000000000445. PMID: 25545484
Figarella-Branger D, Gambarelli D, Perez-Castillo M, Gentet JC, Grisoli F, Pellissier JF
Neuropathol Appl Neurobiol 1992 Aug;18(4):408-14. doi: 10.1111/j.1365-2990.1992.tb00802.x. PMID: 1528392

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