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Skin Ewing Sarcoma

MedGen UID:
1762969
Concept ID:
C5419752
Neoplastic Process
Synonym: Cutaneous Ewing Sarcoma

Definition

A rare Ewing sarcoma that arises from the skin. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVSkin Ewing Sarcoma

Professional guidelines

PubMed

Machado I, Traves V, Cruz J, Llombart B, Navarro S, Llombart-Bosch A
Semin Diagn Pathol 2013 Feb;30(1):85-94. doi: 10.1053/j.semdp.2012.01.007. PMID: 23327732
Delaplace M, Lhommet C, de Pinieux G, Vergier B, de Muret A, Machet L
Br J Dermatol 2012 Apr;166(4):721-6. Epub 2012 Mar 5 doi: 10.1111/j.1365-2133.2011.10743.x. PMID: 22098102
Machado I, Llombart B, Calabuig-Fariñas S, Llombart-Bosch A
J Cutan Pathol 2011 Aug;38(8):636-43. Epub 2011 Jun 7 doi: 10.1111/j.1600-0560.2011.01705.x. PMID: 21649689

Recent clinical studies

Etiology

Brahmi M, Gaspar N, Gantzer J, Toulmonde M, Boudou-Rouquette P, Bompas E, Firmin N, Valentin T, Cancel M, Duffaud F, Bertucci F, Perrin C, Dufresne A, Marec-Bérard P, Jean-Denis M, Ray-Coquard I, Le Loarer F, Pierron G, Tirode F, Blay JY, Watson S
Cancer Med 2023 Apr;12(7):7801-7807. Epub 2022 Dec 20 doi: 10.1002/cam4.5539. PMID: 36537582Free PMC Article
Villanueva G, Sampor C, Moreno F, Alderete D, Moresco A, Pinto N, Szijan I, Schaiquevich P, Felice MS, Rose A, Zubizarreta P, Sgroi M, Fandiño A, Chantada G
Pediatr Blood Cancer 2022 Aug;69(8):e29710. Epub 2022 Apr 21 doi: 10.1002/pbc.29710. PMID: 35451226
Friedman DN, Chastain K, Chou JF, Moskowitz CS, Adsuar R, Wexler LH, Chou AJ, DeRosa A, Candela J, Magnan H, Pun S, Kahan T, Wolden SL, Meyers PA, Oeffinger KC
Pediatr Blood Cancer 2017 Nov;64(11) Epub 2017 Apr 18 doi: 10.1002/pbc.26562. PMID: 28417551
Di Giannatale A, Frezza AM, Le Deley MC, Marec-Bérard P, Benson C, Blay JY, Bui B, Judson I, Oberlin O, Whelan J, Gaspar N
Pediatr Blood Cancer 2015 Sep;62(9):1555-61. Epub 2015 Apr 20 doi: 10.1002/pbc.25535. PMID: 25894676
Terrier-Lacombe MJ, Guillou L, Chibon F, Gallagher G, Benhattar J, Terrier P, Ranchère D, Coindre JM
Mod Pathol 2009 Jan;22(1):87-94. Epub 2008 Sep 26 doi: 10.1038/modpathol.2008.156. PMID: 18820660

Diagnosis

Cammareri C, Beltzung F, Michal M, Vanhersecke L, Coindre JM, Velasco V, Le Loarer F, Vergier B, Perret R
Virchows Arch 2023 Aug;483(2):145-156. Epub 2023 Jul 21 doi: 10.1007/s00428-023-03606-6. PMID: 37477762
Aiba H, Kojima Y, Shimoi T, Sudo K, Yazaki S, Imai T, Yoshida A, Iwata S, Kobayashi E, Kawai A, Arakawa A, Ogawa C, Kimura H, Yonemori K
Jpn J Clin Oncol 2023 Jun 29;53(7):604-610. doi: 10.1093/jjco/hyad031. PMID: 37093679
Brahmi M, Gaspar N, Gantzer J, Toulmonde M, Boudou-Rouquette P, Bompas E, Firmin N, Valentin T, Cancel M, Duffaud F, Bertucci F, Perrin C, Dufresne A, Marec-Bérard P, Jean-Denis M, Ray-Coquard I, Le Loarer F, Pierron G, Tirode F, Blay JY, Watson S
Cancer Med 2023 Apr;12(7):7801-7807. Epub 2022 Dec 20 doi: 10.1002/cam4.5539. PMID: 36537582Free PMC Article
Miettinen M, Felisiak-Golabek A, Luiña Contreras A, Glod J, Kaplan RN, Killian JK, Lasota J
Hum Pathol 2019 Apr;86:57-65. Epub 2019 Jan 8 doi: 10.1016/j.humpath.2018.12.006. PMID: 30633925Free PMC Article
Delaplace M, Lhommet C, de Pinieux G, Vergier B, de Muret A, Machet L
Br J Dermatol 2012 Apr;166(4):721-6. Epub 2012 Mar 5 doi: 10.1111/j.1365-2133.2011.10743.x. PMID: 22098102

Therapy

Aiba H, Kojima Y, Shimoi T, Sudo K, Yazaki S, Imai T, Yoshida A, Iwata S, Kobayashi E, Kawai A, Arakawa A, Ogawa C, Kimura H, Yonemori K
Jpn J Clin Oncol 2023 Jun 29;53(7):604-610. doi: 10.1093/jjco/hyad031. PMID: 37093679
Laskar S, Sinha S, Chatterjee A, Khanna N, Manjali JJ, Puri A, Gulia A, Nayak P, Vora T, Chinnaswamy G, Prasad M, Bajpai J, Juvekar S, Desai S, Janu A, Rangarajan V, Purandare N, Shah S, Rekhi B, Jambhekar N, Muckaden MA, Kurkure P
Int J Radiat Oncol Biol Phys 2022 Aug 1;113(5):996-1002. Epub 2022 May 11 doi: 10.1016/j.ijrobp.2022.04.024. PMID: 35568246
Gaito S, Abravan A, Richardson J, Lowe M, Indelicato DJ, Burnet N, Smith E
Clin Oncol (R Coll Radiol) 2021 Aug;33(8):507-516. Epub 2021 Apr 2 doi: 10.1016/j.clon.2021.03.009. PMID: 33820695
Friedman DN, Chastain K, Chou JF, Moskowitz CS, Adsuar R, Wexler LH, Chou AJ, DeRosa A, Candela J, Magnan H, Pun S, Kahan T, Wolden SL, Meyers PA, Oeffinger KC
Pediatr Blood Cancer 2017 Nov;64(11) Epub 2017 Apr 18 doi: 10.1002/pbc.26562. PMID: 28417551
Di Giannatale A, Frezza AM, Le Deley MC, Marec-Bérard P, Benson C, Blay JY, Bui B, Judson I, Oberlin O, Whelan J, Gaspar N
Pediatr Blood Cancer 2015 Sep;62(9):1555-61. Epub 2015 Apr 20 doi: 10.1002/pbc.25535. PMID: 25894676

Prognosis

Aiba H, Kojima Y, Shimoi T, Sudo K, Yazaki S, Imai T, Yoshida A, Iwata S, Kobayashi E, Kawai A, Arakawa A, Ogawa C, Kimura H, Yonemori K
Jpn J Clin Oncol 2023 Jun 29;53(7):604-610. doi: 10.1093/jjco/hyad031. PMID: 37093679
Miettinen M, Felisiak-Golabek A, Luiña Contreras A, Glod J, Kaplan RN, Killian JK, Lasota J
Hum Pathol 2019 Apr;86:57-65. Epub 2019 Jan 8 doi: 10.1016/j.humpath.2018.12.006. PMID: 30633925Free PMC Article
Friedman DN, Chastain K, Chou JF, Moskowitz CS, Adsuar R, Wexler LH, Chou AJ, DeRosa A, Candela J, Magnan H, Pun S, Kahan T, Wolden SL, Meyers PA, Oeffinger KC
Pediatr Blood Cancer 2017 Nov;64(11) Epub 2017 Apr 18 doi: 10.1002/pbc.26562. PMID: 28417551
Simons SA, Bridge JA, Leon ME
Semin Diagn Pathol 2016 Mar;33(2):91-103. Epub 2015 Sep 10 doi: 10.1053/j.semdp.2015.09.010. PMID: 26585346
Delaplace M, Lhommet C, de Pinieux G, Vergier B, de Muret A, Machet L
Br J Dermatol 2012 Apr;166(4):721-6. Epub 2012 Mar 5 doi: 10.1111/j.1365-2133.2011.10743.x. PMID: 22098102

Clinical prediction guides

Laskar S, Sinha S, Chatterjee A, Khanna N, Manjali JJ, Puri A, Gulia A, Nayak P, Vora T, Chinnaswamy G, Prasad M, Bajpai J, Juvekar S, Desai S, Janu A, Rangarajan V, Purandare N, Shah S, Rekhi B, Jambhekar N, Muckaden MA, Kurkure P
Int J Radiat Oncol Biol Phys 2022 Aug 1;113(5):996-1002. Epub 2022 May 11 doi: 10.1016/j.ijrobp.2022.04.024. PMID: 35568246
Gaito S, Abravan A, Richardson J, Lowe M, Indelicato DJ, Burnet N, Smith E
Clin Oncol (R Coll Radiol) 2021 Aug;33(8):507-516. Epub 2021 Apr 2 doi: 10.1016/j.clon.2021.03.009. PMID: 33820695
Brčić I, Brodowicz T, Cerroni L, Kashofer K, Serbanescu GL, Kasseroler MT, Amann G, Scheipl S, Szkandera J, Leithner A, Liegl-Atzwanger B
Pathology 2020 Feb;52(2):236-242. Epub 2019 Dec 20 doi: 10.1016/j.pathol.2019.09.015. PMID: 31870501
Manzanares A, Restrepo-Perdomo CA, Botteri G, Castillo-Ecija H, Pascual-Pasto G, Cano F, Garcia-Alvarez L, Monterrubio C, Ruiz B, Vazquez-Carrera M, Suñol M, Mora J, Tornero JA, Sosnik A, Carcaboso AM
Adv Healthc Mater 2018 Aug;7(15):e1800255. Epub 2018 Jun 11 doi: 10.1002/adhm.201800255. PMID: 29892999
Simons SA, Bridge JA, Leon ME
Semin Diagn Pathol 2016 Mar;33(2):91-103. Epub 2015 Sep 10 doi: 10.1053/j.semdp.2015.09.010. PMID: 26585346

Recent systematic reviews

Delaplace M, Lhommet C, de Pinieux G, Vergier B, de Muret A, Machet L
Br J Dermatol 2012 Apr;166(4):721-6. Epub 2012 Mar 5 doi: 10.1111/j.1365-2133.2011.10743.x. PMID: 22098102

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