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Vulvar Epithelioid Sarcoma

MedGen UID:
1793839
•Concept ID:
C5557398
•
Neoplastic Process

Definition

An epithelioid sarcoma that arises from the vulva. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar Epithelioid Sarcoma

Professional guidelines

PubMed

Clinical Features and Treatment of Dermatofibrosarcoma Protuberans Affecting the Vulva: A Literature Review.
Nguyen AH, Detty SQ, Gonzaga MI, Huerter C
Dermatol Surg 2017 Jun;43(6):771-774. doi: 10.1097/DSS.0000000000001113. PMID: 28323651
Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 1.
Chokoeva AA, Tchernev G, Cardoso JC, Patterson JW, Dechev I, Valkanov S, Zanardelli M, Lotti T, Wollina U
Int J Immunopathol Pharmacol 2015 Jun;28(2):168-77. Epub 2015 Mar 26 doi: 10.1177/0394632015576029. PMID: 25816394
Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2.
Chokoeva AA, Tchernev G, Cardoso JC, Patterson JW, Dechev I, Valkanov S, Zanardelli M, Lotti T, Wollina U
Int J Immunopathol Pharmacol 2015 Jun;28(2):178-86. Epub 2015 Mar 26 doi: 10.1177/0394632015575977. PMID: 25816393

Recent clinical studies

Etiology

Fine needle aspiration cytology of primary epithelioid sarcoma of the vulva. A case report.
Hernández-Ortiz MJ, Valenzuela-Ruiz P, Gonzalez-Estecha A, Santana-Acosta A, Ruiz-Villaespesa A
Acta Cytol 1995 Jan-Feb;39(1):100-3. PMID: 7846995

Diagnosis

Proximal-type vulvar epithelioid sarcoma masquerading as cellulitis in a young female.
Miura T, Kikuchi N, Yamada H, Hakozaki M, Tajino T, Ohtsuka M, Yamamoto T
Australas J Dermatol 2023 May;64(2):295-297. Epub 2023 Mar 9 doi: 10.1111/ajd.14020. PMID: 36892905
Vulvar epithelioid sarcoma: A case report with literature review.
Noh JJ, Jeon JE, Jung H, Kim HS, Lee YY, Choi CH, Lee JW
Taiwan J Obstet Gynecol 2021 Jan;60(1):132-135. doi: 10.1016/j.tjog.2020.11.020. PMID: 33494986
Epithelioid sarcoma of vulva: a case report and review of the literature.
Altundag K, Dikbas O, Oyan B, Usubutun A, Turker A
Med Oncol 2004;21(4):367-72. doi: 10.1385/MO:21:4:367. PMID: 15579921
Vulvar epithelioid sarcoma in pregnancy.
Moore RG, Steinhoff MM, Granai CO, DeMars LR
Gynecol Oncol 2002 Apr;85(1):218-22. doi: 10.1006/gyno.2002.6610. PMID: 11925150
Epithelioid sarcoma of the Bartholin's gland primarily diagnosed as vulvar carcinoma.
Konefka T, Senkus E, Emerich J, Dudziak M
Gynecol Oncol 1994 Sep;54(3):393-5. doi: 10.1006/gyno.1994.1231. PMID: 8088621

Prognosis

Vulvar epithelioid sarcoma: A case report with literature review.
Noh JJ, Jeon JE, Jung H, Kim HS, Lee YY, Choi CH, Lee JW
Taiwan J Obstet Gynecol 2021 Jan;60(1):132-135. doi: 10.1016/j.tjog.2020.11.020. PMID: 33494986
Epithelioid sarcoma of vulva: a case report and review of the literature.
Altundag K, Dikbas O, Oyan B, Usubutun A, Turker A
Med Oncol 2004;21(4):367-72. doi: 10.1385/MO:21:4:367. PMID: 15579921
Fine needle aspiration cytology of primary epithelioid sarcoma of the vulva. A case report.
Hernández-Ortiz MJ, Valenzuela-Ruiz P, Gonzalez-Estecha A, Santana-Acosta A, Ruiz-Villaespesa A
Acta Cytol 1995 Jan-Feb;39(1):100-3. PMID: 7846995
Epithelioid sarcoma of the Bartholin's gland primarily diagnosed as vulvar carcinoma.
Konefka T, Senkus E, Emerich J, Dudziak M
Gynecol Oncol 1994 Sep;54(3):393-5. doi: 10.1006/gyno.1994.1231. PMID: 8088621
Epithelioid sarcoma of the vulva. Evidence suggesting a more aggressive behavior than extra-genital epithelioid sarcoma.
Ulbright TM, Brokaw SA, Stehman FB, Roth LM
Cancer 1983 Oct 15;52(8):1462-9. doi: 10.1002/1097-0142(19831015)52:8<1462::aid-cncr2820520821>3.0.co;2-y. PMID: 6352000

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