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Vulvar Ewing Sarcoma

MedGen UID:
1793842
•Concept ID:
C5557401
•
Neoplastic Process

Definition

Ewing sarcoma arising from the vulva. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar Ewing Sarcoma

Professional guidelines

PubMed

Ewing Sarcoma of the Female Genital Tract: Clinicopathologic Analysis of 21 Cases With an Emphasis on the Differential Diagnosis of Gynecologic Round Cell, Spindle, and Epithelioid Neoplasms.
Sharma AE, Wepy CB, Chapel DB, Maccio L, Irshaid L, Al-Ibraheemi A, Dickson BC, Nucci MR, Crum CP, Fletcher CDM, Kolin DL
Am J Surg Pathol 2024 Aug 1;48(8):972-984. Epub 2024 May 2 doi: 10.1097/PAS.0000000000002232. PMID: 38708674
Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2.
Chokoeva AA, Tchernev G, Cardoso JC, Patterson JW, Dechev I, Valkanov S, Zanardelli M, Lotti T, Wollina U
Int J Immunopathol Pharmacol 2015 Jun;28(2):178-86. Epub 2015 Mar 26 doi: 10.1177/0394632015575977. PMID: 25816393

Recent clinical studies

Therapy

Primary metastasized extraskeletal Ewing sarcoma of the vulva: report of a case and review of the literature.
Kelling K, Noack F, Altgassen C, Kujath P, Bohlmann MK, Hoellen F
Arch Gynecol Obstet 2012 Mar;285(3):785-9. Epub 2011 Jul 30 doi: 10.1007/s00404-011-2011-x. PMID: 21805144
Primary vulvar Ewing's sarcoma/primitive neuroectodermal tumor in a post-menopausal woman: a case report.
Boldorini R, Riboni F, Cristina S, Allegrini S, Valentini S, Muscarà M, Ruspa G
Pathol Res Pract 2010 Jul 15;206(7):476-9. Epub 2009 Aug 4 doi: 10.1016/j.prp.2009.07.006. PMID: 19656640
Labial fusion: a rare complication of chronic graft-versus-host disease.
Norian JM, Stratton P
Obstet Gynecol 2008 Aug;112(2 Pt 2):437-9. doi: 10.1097/01.AOG.0000299876.18200.8d. PMID: 18669755Free PMC Article
Primary vulvar and vaginal extraosseous Ewing's sarcoma/peripheral neuroectodermal tumor: diagnostic confirmation with CD99 immunostaining and reverse transcriptase-polymerase chain reaction.
Vang R, Taubenberger JK, Mannion CM, Bijwaard K, Malpica A, Ordonez NG, Tavassoli FA, Silver SA
Int J Gynecol Pathol 2000 Apr;19(2):103-9. doi: 10.1097/00004347-200004000-00002. PMID: 10782405
A 10-year experience of pediatric brachytherapy.
Healey EA, Shamberger RC, Grier HE, Loeffler JS, Tarbell NJ
Int J Radiat Oncol Biol Phys 1995 May 15;32(2):451-5. doi: 10.1016/0360-3016(95)00520-9. PMID: 7772200

Prognosis

Ewing Sarcoma of the Female Genital Tract: Clinicopathologic Analysis of 21 Cases With an Emphasis on the Differential Diagnosis of Gynecologic Round Cell, Spindle, and Epithelioid Neoplasms.
Sharma AE, Wepy CB, Chapel DB, Maccio L, Irshaid L, Al-Ibraheemi A, Dickson BC, Nucci MR, Crum CP, Fletcher CDM, Kolin DL
Am J Surg Pathol 2024 Aug 1;48(8):972-984. Epub 2024 May 2 doi: 10.1097/PAS.0000000000002232. PMID: 38708674
Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Primary Ewing Sarcoma Presenting as a Vulvar Mass in an Adolescent: Case Report and Review of Literature.
Tunitsky-Bitton E, Uy-Kroh MJ, Michener C, Tarr ME
J Pediatr Adolesc Gynecol 2015 Dec;28(6):e179-83. Epub 2015 Apr 14 doi: 10.1016/j.jpag.2015.04.004. PMID: 26211932
Primary vulvar Ewing sarcoma/primitive neuroectodermal tumor: a report of one case and review of the literature.
Yang J, Guo Q, Yang Y, Zhang J, Lang J, Shi H
J Pediatr Adolesc Gynecol 2012 Aug;25(4):e93-7. doi: 10.1016/j.jpag.2012.03.005. PMID: 22840944
Primary vulvar sarcomas.
Nirenberg A, Ostör AG, Slavin J, Riley CB, Rome RM
Int J Gynecol Pathol 1995 Jan;14(1):55-62. doi: 10.1097/00004347-199501000-00010. PMID: 7883427

Clinical prediction guides

Ewing Sarcoma of the Female Genital Tract: Clinicopathologic Analysis of 21 Cases With an Emphasis on the Differential Diagnosis of Gynecologic Round Cell, Spindle, and Epithelioid Neoplasms.
Sharma AE, Wepy CB, Chapel DB, Maccio L, Irshaid L, Al-Ibraheemi A, Dickson BC, Nucci MR, Crum CP, Fletcher CDM, Kolin DL
Am J Surg Pathol 2024 Aug 1;48(8):972-984. Epub 2024 May 2 doi: 10.1097/PAS.0000000000002232. PMID: 38708674

Supplemental Content

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