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Vulvar Ewing Sarcoma

MedGen UID:
1793842
•Concept ID:
C5557401
•
Neoplastic Process

Definition

Ewing sarcoma arising from the vulva. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVVulvar Ewing Sarcoma

Professional guidelines

PubMed

Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2.
Chokoeva AA, Tchernev G, Cardoso JC, Patterson JW, Dechev I, Valkanov S, Zanardelli M, Lotti T, Wollina U
Int J Immunopathol Pharmacol 2015 Jun;28(2):178-86. Epub 2015 Mar 26 doi: 10.1177/0394632015575977. PMID: 25816393

Recent clinical studies

Etiology

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Primitive Neuroectodermal Tumors of the Female Genital Tract: A Morphologic, Immunohistochemical, and Molecular Study of 19 Cases.
Chiang S, Snuderl M, Kojiro-Sanada S, Quer Pi-Sunyer A, Daya D, Hayashi T, Bosincu L, Ogawa F, Rosenberg AE, Horn LC, Wang L, Iafrate AJ, Oliva E
Am J Surg Pathol 2017 Jun;41(6):761-772. doi: 10.1097/PAS.0000000000000831. PMID: 28296680Free PMC Article
Primary vulvar sarcomas.
Nirenberg A, Ostör AG, Slavin J, Riley CB, Rome RM
Int J Gynecol Pathol 1995 Jan;14(1):55-62. doi: 10.1097/00004347-199501000-00010. PMID: 7883427

Diagnosis

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Primary vulvar Ewing sarcoma/peripheral primitive neuroectodermal tumor with pelvic lymph nodes metastasis: A case report and review of literature.
El Housheimi A, Khalil A, Khalifeh D, Berjawi G, Seoud M, Tabbarah A, Khaled C, Mahfouz R, Abdallah R
J Obstet Gynaecol Res 2020 Oct;46(10):2185-2192. Epub 2020 Aug 5 doi: 10.1111/jog.14399. PMID: 32761741
Primary Ewing Sarcoma Presenting as a Vulvar Mass in an Adolescent: Case Report and Review of Literature.
Tunitsky-Bitton E, Uy-Kroh MJ, Michener C, Tarr ME
J Pediatr Adolesc Gynecol 2015 Dec;28(6):e179-83. Epub 2015 Apr 14 doi: 10.1016/j.jpag.2015.04.004. PMID: 26211932
Vulvar sarcomas: Short guideline for histopathological recognition and clinical management. Part 2.
Chokoeva AA, Tchernev G, Cardoso JC, Patterson JW, Dechev I, Valkanov S, Zanardelli M, Lotti T, Wollina U
Int J Immunopathol Pharmacol 2015 Jun;28(2):178-86. Epub 2015 Mar 26 doi: 10.1177/0394632015575977. PMID: 25816393
Primary vulvar Ewing sarcoma/primitive neuroectodermal tumor: a report of 2 cases and review of the literature.
Cetiner H, Kir G, Gelmann EP, Ozdemirli M
Int J Gynecol Cancer 2009 Aug;19(6):1131-6. doi: 10.1111/IGC.0b013e3181acae33. PMID: 19820381

Therapy

Primary Ewing sarcoma of vulva, confirmed with molecular cytogenetic analysis: A rare case report with diagnostic and treatment implications.
Rekhi B, Chinnaswamy G, Vora T, Shah S, Rangarajan V
Indian J Pathol Microbiol 2015 Jul-Sep;58(3):341-4. doi: 10.4103/0377-4929.162869. PMID: 26275259
Primary metastasized extraskeletal Ewing sarcoma of the vulva: report of a case and review of the literature.
Kelling K, Noack F, Altgassen C, Kujath P, Bohlmann MK, Hoellen F
Arch Gynecol Obstet 2012 Mar;285(3):785-9. Epub 2011 Jul 30 doi: 10.1007/s00404-011-2011-x. PMID: 21805144
Primary vulvar Ewing's sarcoma/primitive neuroectodermal tumor in a post-menopausal woman: a case report.
Boldorini R, Riboni F, Cristina S, Allegrini S, Valentini S, Muscarà M, Ruspa G
Pathol Res Pract 2010 Jul 15;206(7):476-9. Epub 2009 Aug 4 doi: 10.1016/j.prp.2009.07.006. PMID: 19656640
Primary vulvar and vaginal extraosseous Ewing's sarcoma/peripheral neuroectodermal tumor: diagnostic confirmation with CD99 immunostaining and reverse transcriptase-polymerase chain reaction.
Vang R, Taubenberger JK, Mannion CM, Bijwaard K, Malpica A, Ordonez NG, Tavassoli FA, Silver SA
Int J Gynecol Pathol 2000 Apr;19(2):103-9. doi: 10.1097/00004347-200004000-00002. PMID: 10782405
A 10-year experience of pediatric brachytherapy.
Healey EA, Shamberger RC, Grier HE, Loeffler JS, Tarbell NJ
Int J Radiat Oncol Biol Phys 1995 May 15;32(2):451-5. doi: 10.1016/0360-3016(95)00520-9. PMID: 7772200

Prognosis

Pediatric vulvar malignancies: rare but important to know.
Strickland AL, Fadare O
Semin Diagn Pathol 2021 Jan;38(1):99-109. Epub 2020 Sep 5 doi: 10.1053/j.semdp.2020.09.001. PMID: 32943238
Primary Ewing Sarcoma Presenting as a Vulvar Mass in an Adolescent: Case Report and Review of Literature.
Tunitsky-Bitton E, Uy-Kroh MJ, Michener C, Tarr ME
J Pediatr Adolesc Gynecol 2015 Dec;28(6):e179-83. Epub 2015 Apr 14 doi: 10.1016/j.jpag.2015.04.004. PMID: 26211932
Ewing sarcoma/primitive neuroectodermal tumor (PNET) of the vulva. Case report and review of the literature.
Anastasiades EN, El Abiad SA, Chouairy CJ
J Med Liban 2012 Apr-Jun;60(2):113-6. PMID: 22919869
Primary vulvar Ewing sarcoma/primitive neuroectodermal tumor: a report of one case and review of the literature.
Yang J, Guo Q, Yang Y, Zhang J, Lang J, Shi H
J Pediatr Adolesc Gynecol 2012 Aug;25(4):e93-7. doi: 10.1016/j.jpag.2012.03.005. PMID: 22840944
Primary vulvar sarcomas.
Nirenberg A, Ostör AG, Slavin J, Riley CB, Rome RM
Int J Gynecol Pathol 1995 Jan;14(1):55-62. doi: 10.1097/00004347-199501000-00010. PMID: 7883427

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