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Angiomatosis

MedGen UID:
1931
•Concept ID:
C0002992
•
Disease or Syndrome
Synonym: Angiomatoses
SNOMED CT: Angiomatosis (14350002); Angiomatosis (205562004)
 
Monarch Initiative: MONDO:0024461

Definition

A benign diffuse vascular proliferation usually occurring in young adults. It is characterized by the formation of capillary-sized and cavernous vascular spaces. Patients present with diffuse persistent swelling. [from NCI]

Professional guidelines

PubMed

Pathophysiology and management of glaucoma associated with phakomatoses.
Thavikulwat AT, Edward DP, AlDarrab A, Vajaranant TS
J Neurosci Res 2019 Jan;97(1):57-69. Epub 2018 Apr 1 doi: 10.1002/jnr.24241. PMID: 29607552
Pathophysiology, diagnosis, and management of glaucoma associated with Sturge-Weber syndrome.
Javaid U, Ali MH, Jamal S, Butt NH
Int Ophthalmol 2018 Feb;38(1):409-416. Epub 2017 Jan 7 doi: 10.1007/s10792-016-0412-3. PMID: 28064423
Pathogenicity and treatment of Bartonella infections.
Angelakis E, Raoult D
Int J Antimicrob Agents 2014 Jul;44(1):16-25. Epub 2014 May 9 doi: 10.1016/j.ijantimicag.2014.04.006. PMID: 24933445

Recent clinical studies

Etiology

Capillary malformations.
Hammill AM, Boscolo E
J Clin Invest 2024 Apr 15;134(8) doi: 10.1172/JCI172842. PMID: 38618955Free PMC Article
Chronic hand infections.
Al-Qattan MM, Helmi AA
J Hand Surg Am 2014 Aug;39(8):1636-45. doi: 10.1016/j.jhsa.2014.04.003. PMID: 25070033
Bartonellosis.
Maguiña C, Guerra H, Ventosilla P
Clin Dermatol 2009 May-Jun;27(3):271-80. doi: 10.1016/j.clindermatol.2008.10.006. PMID: 19362689
Infections in the homeless.
Raoult D, Foucault C, Brouqui P
Lancet Infect Dis 2001 Sep;1(2):77-84. doi: 10.1016/S1473-3099(01)00062-7. PMID: 11871479
Bacillary angiomatosis.
Batsakis JG, Ro JY, Frauenhoffer EE
Ann Otol Rhinol Laryngol 1995 Aug;104(8):668-72. doi: 10.1177/000348949510400815. PMID: 7543738

Diagnosis

Diffuse dermal angiomatosis.
Touloei K, Tongdee E, Smirnov B, Nousari C
Cutis 2019 Mar;103(3):181-184. PMID: 31039226
Lymph node stromal and vascular proliferations.
Xu ML, O'Malley D
Semin Diagn Pathol 2018 Jan;35(1):67-75. Epub 2017 Nov 15 doi: 10.1053/j.semdp.2017.11.004. PMID: 29173940
Angiomatous skeletal lesions.
Choi JJ, Murphey MD
Semin Musculoskelet Radiol 2000;4(1):103-12. doi: 10.1055/s-2000-6858. PMID: 11061695
Bacillary angiomatosis.
Batsakis JG, Ro JY, Frauenhoffer EE
Ann Otol Rhinol Laryngol 1995 Aug;104(8):668-72. doi: 10.1177/000348949510400815. PMID: 7543738
Bacillary angiomatosis.
Berger TG, Koehler JE
AIDS Clin Rev 1993-1994:43-60. PMID: 8217903

Therapy

Sturge-Weber Syndrome: A Review.
Higueros E, Roe E, Granell E, Baselga E
Actas Dermosifiliogr 2017 Jun;108(5):407-417. Epub 2017 Jan 23 doi: 10.1016/j.ad.2016.09.022. PMID: 28126187
Pathogenicity and treatment of Bartonella infections.
Angelakis E, Raoult D
Int J Antimicrob Agents 2014 Jul;44(1):16-25. Epub 2014 May 9 doi: 10.1016/j.ijantimicag.2014.04.006. PMID: 24933445
Treatment of cat-scratch disease.
Conrad DA
Curr Opin Pediatr 2001 Feb;13(1):56-9. doi: 10.1097/00008480-200102000-00010. PMID: 11176245
Bartonella-associated infections.
Spach DH, Koehler JE
Infect Dis Clin North Am 1998 Mar;12(1):137-55. doi: 10.1016/s0891-5520(05)70414-1. PMID: 9494835
Retinal arterial macroaneurysms.
Rabb MF, Gagliano DA, Teske MP
Surv Ophthalmol 1988 Sep-Oct;33(2):73-96. doi: 10.1016/0039-6257(88)90160-9. PMID: 3055391

Prognosis

Unusual Gigantiform Angiomatosis of Jawbone.
Kumar N, Anehosur V, Desai A, Agrawal S, Prabhu A, Hallikeri K
J Craniofac Surg 2022 May 1;33(3):e230-e233. Epub 2021 Jul 14 doi: 10.1097/SCS.0000000000007967. PMID: 34261965
Sturge-Weber Syndrome: A Review.
Higueros E, Roe E, Granell E, Baselga E
Actas Dermosifiliogr 2017 Jun;108(5):407-417. Epub 2017 Jan 23 doi: 10.1016/j.ad.2016.09.022. PMID: 28126187
Sturge-Weber syndrome: a review.
Thomas-Sohl KA, Vaslow DF, Maria BL
Pediatr Neurol 2004 May;30(5):303-10. doi: 10.1016/j.pediatrneurol.2003.12.015. PMID: 15165630
Bartonella (Rochalimaea) quintana infections.
Maurin M, Raoult D
Clin Microbiol Rev 1996 Jul;9(3):273-92. doi: 10.1128/CMR.9.3.273. PMID: 8809460Free PMC Article
Nodal angiomatosis.
Fayemi AO, Toker C
Arch Pathol 1975 Mar;99(3):170-2. PMID: 1120027

Clinical prediction guides

Unusual Gigantiform Angiomatosis of Jawbone.
Kumar N, Anehosur V, Desai A, Agrawal S, Prabhu A, Hallikeri K
J Craniofac Surg 2022 May 1;33(3):e230-e233. Epub 2021 Jul 14 doi: 10.1097/SCS.0000000000007967. PMID: 34261965
Cat Scratch Disease and Bartonellaceae: The Known, the Unknown and the Curious.
Zangwill KM
Pediatr Infect Dis J 2021 May 1;40(5S):S11-S15. doi: 10.1097/INF.0000000000002776. PMID: 34042905
Clinical impact of persistent Bartonella bacteremia in humans and animals.
Chomel BB, Kasten RW, Sykes JE, Boulouis HJ, Breitschwerdt EB
Ann N Y Acad Sci 2003 Jun;990:267-78. doi: 10.1111/j.1749-6632.2003.tb07376.x. PMID: 12860639
Treatment of cat-scratch disease.
Conrad DA
Curr Opin Pediatr 2001 Feb;13(1):56-9. doi: 10.1097/00008480-200102000-00010. PMID: 11176245
Bartonella (Rochalimaea) quintana infections.
Maurin M, Raoult D
Clin Microbiol Rev 1996 Jul;9(3):273-92. doi: 10.1128/CMR.9.3.273. PMID: 8809460Free PMC Article

Recent systematic reviews

A systematic review on antibiotic therapy of cutaneous bacillary angiomatosis not related to major immunocompromising conditions: from pathogenesis to treatment.
Rotundo S, Tassone MT, Marascio N, Morrone HL, Gigliotti S, Quirino A, Russo A, Matera G, Trecarichi EM, Torti C
BMC Infect Dis 2024 Apr 8;24(1):380. doi: 10.1186/s12879-024-09253-9. PMID: 38589795Free PMC Article
Meningioangiomatosis: Multimodal Analysis and Insights From a Systematic Review.
Roux A, Zanello M, Mancusi RL, Still MEH, Nascimento FA, Tauziede-Espariat A, Huberfeld G, Zah-Bi G, Dezamis E, Meder JF, Bourgeois M, Parraga E, Chretien F, Varlet P, Oppenheim C, Lechapt-Zalcman E, Pallud J
Neurology 2021 Feb 9;96(6):274-286. Epub 2020 Dec 22 doi: 10.1212/WNL.0000000000011372. PMID: 33361266
Systematic review of mortality associated with neonatal primary staged closure of giant omphalocele.
Barrios Sanjuanelo A, Abelló Munarriz C, Cardona-Arias JA
J Pediatr Surg 2021 Apr;56(4):678-685. Epub 2020 Aug 29 doi: 10.1016/j.jpedsurg.2020.08.019. PMID: 32981659
Pathophysiology, diagnosis, and management of glaucoma associated with Sturge-Weber syndrome.
Javaid U, Ali MH, Jamal S, Butt NH
Int Ophthalmol 2018 Feb;38(1):409-416. Epub 2017 Jan 7 doi: 10.1007/s10792-016-0412-3. PMID: 28064423
Treatment outcomes of human bartonellosis: a systematic review and meta-analysis.
Prutsky G, Domecq JP, Mori L, Bebko S, Matzumura M, Sabouni A, Shahrour A, Erwin PJ, Boyce TG, Montori VM, Malaga G, Murad MH
Int J Infect Dis 2013 Oct;17(10):e811-9. Epub 2013 Apr 18 doi: 10.1016/j.ijid.2013.02.016. PMID: 23602630

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