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Localized Synovial Sarcoma

MedGen UID:
208947
Concept ID:
C0855071
Neoplastic Process
Synonyms: Non-Metastatic Synovial Sarcoma; Synovial Sarcoma Nonmetastatic

Definition

Synovial sarcoma that is confined to a specific site without evidence of spread to other anatomic sites. [from NCI]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLocalized Synovial Sarcoma

Professional guidelines

PubMed

Singh A, Thorpe S, Keegan T, Maguire F, Malogolowkin M, Abrahão R, Spunt S, Carr-Asher J, Alvarez E
J Adolesc Young Adult Oncol 2023 Oct;12(5):634-643. Epub 2023 Apr 27 doi: 10.1089/jayao.2022.0143. PMID: 37104039Free PMC Article
Hagiwara Y, Iwata S, Ogura K, Kawai A, Susa M, Morioka H, Hiruma T, Tsuda Y, Kawano H, Yonemoto T, Ishii T, Okazaki K
J Orthop Sci 2023 Jan;28(1):261-266. Epub 2021 Oct 27 doi: 10.1016/j.jos.2021.09.012. PMID: 34756517
Shi W, Indelicato DJ, Morris CG, Scarborough MT, Gibbs CP, Zlotecki RA
Am J Clin Oncol 2013 Feb;36(1):83-8. doi: 10.1097/COC.0b013e31823fe450. PMID: 22270107

Recent clinical studies

Etiology

Singh A, Thorpe S, Keegan T, Maguire F, Malogolowkin M, Abrahão R, Spunt S, Carr-Asher J, Alvarez E
J Adolesc Young Adult Oncol 2023 Oct;12(5):634-643. Epub 2023 Apr 27 doi: 10.1089/jayao.2022.0143. PMID: 37104039Free PMC Article
Hagiwara Y, Iwata S, Ogura K, Kawai A, Susa M, Morioka H, Hiruma T, Tsuda Y, Kawano H, Yonemoto T, Ishii T, Okazaki K
J Orthop Sci 2023 Jan;28(1):261-266. Epub 2021 Oct 27 doi: 10.1016/j.jos.2021.09.012. PMID: 34756517
Outani H, Nakamura T, Murata H, Stevenson J, Parry M, Gregory J, Tillman R, Jeys L, Abudu A
J Surg Oncol 2019 Jun;119(7):850-855. Epub 2019 Feb 20 doi: 10.1002/jso.25417. PMID: 30786036
Scheer M, Greulich M, Loff S, Vokuhl C, Feuchtgruber S, von Kalle T, Münter M, Stegmaier S, Sparber-Sauer M, Kazanowska B, Niggli F, Fuchs J, Bielack SS, Klingebiel T, Koscielniak E; and the other members of the Cooperative Weichteilsarkom Studiengruppe (CWS) Group
J Surg Oncol 2019 Jan;119(1):109-119. Epub 2018 Nov 13 doi: 10.1002/jso.25284. PMID: 30421433
Deshmukh R, Mankin HJ, Singer S
Clin Orthop Relat Res 2004 Feb;(419):155-61. PMID: 15021147

Diagnosis

Singh A, Thorpe S, Keegan T, Maguire F, Malogolowkin M, Abrahão R, Spunt S, Carr-Asher J, Alvarez E
J Adolesc Young Adult Oncol 2023 Oct;12(5):634-643. Epub 2023 Apr 27 doi: 10.1089/jayao.2022.0143. PMID: 37104039Free PMC Article
Hagiwara Y, Iwata S, Ogura K, Kawai A, Susa M, Morioka H, Hiruma T, Tsuda Y, Kawano H, Yonemoto T, Ishii T, Okazaki K
J Orthop Sci 2023 Jan;28(1):261-266. Epub 2021 Oct 27 doi: 10.1016/j.jos.2021.09.012. PMID: 34756517
Scheer M, Dantonello T, Hallmen E, Vokuhl C, Leuschner I, Sparber-Sauer M, Kazanowska B, Niggli F, Ladenstein R, Bielack SS, Klingebiel T, Koscielniak E
Pediatr Blood Cancer 2016 Jul;63(7):1198-206. Epub 2016 Mar 22 doi: 10.1002/pbc.25973. PMID: 27003095
Wisanuyotin T, Radapat K, Sirichativapee W, Paholpak P, Kosuwon W, Sumnanoont C, Jeeravipoolvarn P
Asia Pac J Clin Oncol 2013 Mar;9(1):80-5. Epub 2012 Jul 4 doi: 10.1111/j.1743-7563.2012.01563.x. PMID: 22898085
Deshmukh R, Mankin HJ, Singer S
Clin Orthop Relat Res 2004 Feb;(419):155-61. PMID: 15021147

Therapy

Hagiwara Y, Iwata S, Ogura K, Kawai A, Susa M, Morioka H, Hiruma T, Tsuda Y, Kawano H, Yonemoto T, Ishii T, Okazaki K
J Orthop Sci 2023 Jan;28(1):261-266. Epub 2021 Oct 27 doi: 10.1016/j.jos.2021.09.012. PMID: 34756517
Minami Y, Matsumoto S, Ae K, Tanizawa T, Hayakawa K, Funauchi Y, Saito M, Tsuda Y
Anticancer Res 2020 Feb;40(2):1029-1034. doi: 10.21873/anticanres.14038. PMID: 32014949
Scheer M, Dantonello T, Hallmen E, Vokuhl C, Leuschner I, Sparber-Sauer M, Kazanowska B, Niggli F, Ladenstein R, Bielack SS, Klingebiel T, Koscielniak E
Pediatr Blood Cancer 2016 Jul;63(7):1198-206. Epub 2016 Mar 22 doi: 10.1002/pbc.25973. PMID: 27003095
Yaser S, Salah S, Al-Shatti M, Abu-Sheikha A, Shehadeh A, Sultan I, Salem A, Sughayer M, Al-Loh S, Al-Mousa A
Med Oncol 2014 Jun;31(6):958. Epub 2014 Apr 26 doi: 10.1007/s12032-014-0958-8. PMID: 24770952
Mullen JR, Zagars GK
Radiother Oncol 1994 Oct;33(1):23-30. doi: 10.1016/0167-8140(94)90082-5. PMID: 7878206

Prognosis

Hagiwara Y, Iwata S, Ogura K, Kawai A, Susa M, Morioka H, Hiruma T, Tsuda Y, Kawano H, Yonemoto T, Ishii T, Okazaki K
J Orthop Sci 2023 Jan;28(1):261-266. Epub 2021 Oct 27 doi: 10.1016/j.jos.2021.09.012. PMID: 34756517
Outani H, Nakamura T, Murata H, Stevenson J, Parry M, Gregory J, Tillman R, Jeys L, Abudu A
J Surg Oncol 2019 Jun;119(7):850-855. Epub 2019 Feb 20 doi: 10.1002/jso.25417. PMID: 30786036
Scheer M, Greulich M, Loff S, Vokuhl C, Feuchtgruber S, von Kalle T, Münter M, Stegmaier S, Sparber-Sauer M, Kazanowska B, Niggli F, Fuchs J, Bielack SS, Klingebiel T, Koscielniak E; and the other members of the Cooperative Weichteilsarkom Studiengruppe (CWS) Group
J Surg Oncol 2019 Jan;119(1):109-119. Epub 2018 Nov 13 doi: 10.1002/jso.25284. PMID: 30421433
El Beaino M, Araujo DM, Gopalakrishnan V, Lazar AJ, Lin PP
J Surg Oncol 2016 Sep;114(4):490-4. Epub 2016 May 24 doi: 10.1002/jso.24306. PMID: 27220538
Deshmukh R, Mankin HJ, Singer S
Clin Orthop Relat Res 2004 Feb;(419):155-61. PMID: 15021147

Clinical prediction guides

Palmerini E, Benassi MS, Quattrini I, Pazzaglia L, Donati D, Benini S, Gamberi G, Gambarotti M, Picci P, Ferrari S
Orphanet J Rare Dis 2015 Jan 23;10:6. doi: 10.1186/s13023-014-0222-5. PMID: 25613038Free PMC Article
Yaser S, Salah S, Al-Shatti M, Abu-Sheikha A, Shehadeh A, Sultan I, Salem A, Sughayer M, Al-Loh S, Al-Mousa A
Med Oncol 2014 Jun;31(6):958. Epub 2014 Apr 26 doi: 10.1007/s12032-014-0958-8. PMID: 24770952
Guadagnolo BA, Zagars GK, Ballo MT, Patel SR, Lewis VO, Pisters PW, Benjamin RS, Pollock RE
Int J Radiat Oncol Biol Phys 2007 Nov 15;69(4):1173-80. Epub 2007 Aug 6 doi: 10.1016/j.ijrobp.2007.04.056. PMID: 17689031
Deshmukh R, Mankin HJ, Singer S
Clin Orthop Relat Res 2004 Feb;(419):155-61. PMID: 15021147
Singer S, Baldini EH, Demetri GD, Fletcher JA, Corson JM
J Clin Oncol 1996 Apr;14(4):1201-8. doi: 10.1200/JCO.1996.14.4.1201. PMID: 8648375

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