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Liver mesenchymal hamartoma

MedGen UID:
232278
•Concept ID:
C1333971
•
Neoplastic Process
Synonyms: Biliary hamartoma; biliary hamartoma; Hepatic cystic hamartoma; hepatic cystic hamartoma; Hepatic Mesenchymal Hamartoma; hepatic mesenchymal hamartoma; Liver Mesenchymal Hamartoma; liver mesenchymal hamartoma; Liver MH; liver MH; Mesenchymal hamartoma of liver; Mesenchymal Hamartoma of Liver; mesenchymal hamartoma of liver; Mesenchymal Hamartoma of the Liver; mesenchymal hamartoma of the liver; MHL; VMC; Von Meyenburg complexes disease
SNOMED CT: Mesenchymal hamartoma of liver (715397000); Hepatic cystic hamartoma (715397000)
 
Monarch Initiative: MONDO:0018308
Orphanet: ORPHA386

Definition

A rare benign liver tumour of childhood that usually presents before the age of 2. The tumour is of mesenchymal origin and has a variable clinical presentation. [from SNOMEDCT_US]

Term Hierarchy

CClinical test,  RResearch test,  OOMIM,  GGeneReviews,  VClinVar  
  • CROGVLiver mesenchymal hamartoma

Professional guidelines

PubMed

Pediatric Hepatic Cystic Lesions: Differential Diagnosis and Multimodality Imaging Approach.
Riedesel EL, Richer EJ, Taylor SD, Tao T, Gagnon MH, Braithwaite KA, Alazraki AL, Khanna G
Radiographics 2022 Sep-Oct;42(5):1514-1531. Epub 2022 Jul 15 doi: 10.1148/rg.220006. PMID: 35839138
Primary mesenchymal liver tumors: radiological spectrum, differential diagnosis, and pathologic correlation.
Harman M, Nart D, Acar T, Elmas N
Abdom Imaging 2015 Jun;40(5):1316-30. doi: 10.1007/s00261-014-0268-9. PMID: 25311993
Pitfalls in the surgical management of undifferentiated sarcoma of the liver and benefits of preoperative chemotherapy.
Merli L, Mussini C, Gabor F, Branchereau S, Martelli H, Pariente D, Guérin F
Eur J Pediatr Surg 2015 Feb;25(1):132-7. Epub 2014 Sep 26 doi: 10.1055/s-0034-1387937. PMID: 25259441

Recent clinical studies

Diagnosis

Mesenchymal Neoplasms of the Liver.
Papke DJ Jr
Surg Pathol Clin 2023 Sep;16(3):609-634. Epub 2023 Jun 11 doi: 10.1016/j.path.2023.04.013. PMID: 37536892

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